Flashcards in Chapter 12 lecture 3 soft tissue tumors Deck (49):
What is multiple endocrine neoplasia characterized by?
-Adrenal gland tumors
What are adrenal gland tumors also known as?
What are thyroid tumors also known as?
Patients with multiple endocrine neoplasia have what type of build?
-Marfanoid build (long thin face)
What is the typically the first sign of multiple endocrine neoplasia?
-Oral mucosal neuromas
What are bilateral neuromas of the commissural mucosa highly characteristic of?
-Multiple endocrine neoplasia
What is a rare pigmented tumor that usually occurs during the 1st year of life?
-Melanotic neuroectodermal tumor of infancy
What does a melanotic neuroectodermal tumor of infancy appear as clinically?
-Black and or blue rapidly expanding mass usually found on the anterior maxilla
How do they diagnose melanotic neuroectodermal tumor of infancy?
-Test for high urinary levels of vanillymandelic acid
What is a granular cell tumor?
-Benign soft tissue neoplasm that shows a predilection for the oral cavity
What is the most common site for a granular cell tumor?
-Tongue with the dorsal surface being the most common
What does a granular cell tumor appear as clinically?
-Yellow or mucosal colored, asymptomatic sessile nodule that is less than than 2 cm.
What can a granular cell tumor cause?
-Pseudoepitheliomatous hyperlasia (also caused by blastomycosis)
What is S-100 positive associated with: granular cell tumor or congenital epulis?
-Granular cell tumor
What can occur almost exclusively on the alveolar ridge of newborns?
What does a congenital epulis appear as clinically?
-Mucosal colored, smooth surfaced, polypoid mass typically less than 2 cm
What arch do you typically see a congenital epulis?
-Maxillary on the ridge
What differentiates a congenital epulis from a granular cell tumor?
-a congenital epulis does not have PEH (pseudoepithelomatous hyperlasia) and is S-100 negative
What gender does a congenital epulis most commonly occur in?
What is the most common tumor of infancy?
What is the most common location for a hemangioma?
-Head and neck
What are the two types of hemangiomas?
What might you do to tell if it is a capillary hemangioma?
-May not blanch clinically and is usually red in color
What might you do to tell if it is a cavernous hemangioma?
-Typically blanches, and is a darker red to purple color
What is a rare, nonhereditary developmental condition caused by the persistence of a vascular plexus around the cephalic portion of the neural tube?
Patients with sturge-weber angiomatosis are born with a dermal capillary vascular malformation known as what?
-Port wine stain
T/F if a pt has port wine stain they have sturge-weber angiomatosis
-Not all people with the stain have sturge weber angiomatosis
T/F Sturge-weber angiomatosis is unilateral and is usually associated with the trigeminal nerve
What is a benign tumor of lymphatic vessels?
What are the types of lymphangioma?
Where are cavernous lymphangiomas more frequently found?
-In the mouth
What are cystic lymphangiomas most often found?
Oral lymphangiomas occur most frequently where?
-Anterior two thirds of the tongue resulting often in macroglossia
What age do most cases of lymphangiomas occur?
-Before 2 yrs of age
What is a benign tumor of smooth muscle?
What is the most common location of Leiomyoma?
What is a benign neoplasm of skeletal muscle?
Who does the adult type of Rhabdomyoma occur in?
In adult Rhabdomyoma where does it most commonly occur?
In fetal Rhabdomyoma who and where does it occur?
-Young male pts
-Predilection for the face
What are six soft tissue sarcomas?
-Malignant fibrous histiocytoma
-Malignant peripheral nerve sheath tumor
What are the four clinical presentations of Kaposi's sarcoma?
-Iatrogenic immunosuppression associated
What ethnicities can get the classic kaposi's sarcoma?
Where is the endemic type of kaposi's sarcoma found?
What is a malignancy of skeletal muscles?
Where are the most common locations of Rhabdomyosarcoma?
-Face and orbit in children
Head and neck metastases in the absence of lung metastases is possible because of what?
What is Batson's plexus?
-Valveless vertebral venous plexus that might allow retrograde spread of tumor cells and bypass the lungs