Hirschsprung Disease Flashcards Preview

Peds Exam 2 > Hirschsprung Disease > Flashcards

Flashcards in Hirschsprung Disease Deck (20):
1

which part of the intestine does hirschsprung disease usually occur

large intestine

2

the absence of what causes this disease

ganglion cells

3

what is the result of no ganglion cells

obstruction
accumulation of intestinal contents
distention of bowel

4

what are signs of this disease in the newborn

no meconium within 24-48 hours
refusal to feed
bilious vomiting
abdominal distention

5

what are signs of this disease in the infant

failure to thrive
constipation
explosive V/D
fever

6

what are signs of this disease in the child

constipation
ribbon-like stools
visible peristalsis
palpable fecal mass LLQ

7

what does an abdominal xray show

dilated loops of bowel

8

what does an unprepped barium enema show

visualize the dilated & narrow segments of the colon

9

what is the definitive test that reveals the absence of ganglion cells

rectal biopsy

10

what are 3 alternatives to surgery

dietary modifications
stool softeners
isotonic irrigations

11

how often would isotonic irrigations need to be done

daily

12

when should enemas be avoided
why

suspect enterocolotis
potential for perforation

13

what are the 2 phases of surgical management

temporary colostomy
close colostomy

14

at which weight can the colostomy be closed

20 lbs

15

what kind of diet is needed pre-op

high calorie
high protein
low fiber

16

what are s/s of bowel perforation

abdominal pain
fever

17

what are 4 post-op complications

chronic constipation
anal stricture
incontinence
enterocolitis

18

which % develop enterocolitis post-op

20-60

19

what results from enterocolitis

ischemia & ulceration of the bowel

20

what are s/s of enterocolitis

bleeding & diarrhea