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PBR 2 and 3 > PAGE 10 > Flashcards

PAGE 10 Flashcards

1
Q

association of ascites and pleural effusion with ovarian fibromas

A

Meig / Meigs syndrome

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2
Q

mucinous tumors metastatic to the ovary from a mucinous gastric ca

A

Krukenberg tumor

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3
Q

remnant of the connection of the vitelline duct/omphalomesenteric duct to the distal ileum

A

Meckel diverticulum

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3
Q

AR; polydactyly with polycystic kidneys, midline CNS malformations (such as occipital encephalocele, Dandy-Walker malformation)

A

Meckel-Gruber syndrome

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4
Q

classic triad: occipital cephalocele, postaxial polydactyly, and dysplastic cystic kidneys; lethal

A

Meckel syndrome

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5
Q

oligohydramnios -> fetal compression: flattened faces, pulmonary hypoplasia, clubfeet, congenital hip dislocation, low-set ears, micrognathia

A

Potter sequence

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6
Q

congenital anomaly in which the scapula is hypoplastic and elevated

A

Sprengel deformity

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6
Q

Sprengel deformity + omovertebral vertebra, fused cervical vertebrae, hemivertebrae, kyphoscoliosis, and rib anomalies

A

Klippel-Feil syndrome

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6
Q

classic triad: short neck, low posterior hairline, and limited ROM due to fusion of cervical vertebrae

A

Klippel-Feil syndrome

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7
Q

capillary-lymphatic-venous malformation; Sturge-Weber syndrome + extensive cutaneous capillary malformations, limb hypertrophy, and vascular and/or
lymphatic malformations

A

Klippel-Trenaunay syndrome

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7
Q

triad of multiple hemangiomas, arteriovenous fistulas, and unilateral limb hypertrophy, due to bony and soft tissue overgrowth

A

Klippel-Trenaunay -Weber syndrome

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8
Q

C5 and C6 injury

A

Erb-Duchenne palsy

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8
Q

aka (massive) subchorionic thrombosis/hematoma; bulging protuberance that appears hypoechoic or cystic and that elevates and distorts the fetal surface of the placenta

A

Breus mole (misnomer–not a mole)

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8
Q

prevesical or retropubic space

A

space of Retzius

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8
Q

ovarian fossa

A

fossa of Waldeyer

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8
Q

part of the cranial end of the paramesonephric duct which may persist as a vesicular appendage to the fallopian tube

A

hydatid of Morgagni

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8
Q

raised protuberance projecting into the cyst cavity of mature cystic teratomas; aka dermoid plug

A

Rokitansky nodule

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8
Q

remnants of the embryologic wolffian duct system

A

Gartner duct cysts

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9
Q

spectrum, part is agenesis of the upper vagina and uterus

A

Mayer-Rokitansky-Kuster-hauser syndrome

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9
Q

aka PCOS

A

Stein-Levanthal syndrome

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9
Q

acute thrombophlebitis of the superficial veins of the breast

A

Mondor disease

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9
Q

primary adrenal insufficiency

A

Addison disease

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9
Q

co-existence of neonatal omphalocele or umbilical hernia in a large infant with organomegaly (liver, kidneys) and large tongue; some are more prone (although rarely) to Wilm’s tumor and liver or adrenal cortical tumors/adrenal cytomegaly

A

Addison disease

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9
Q

classic triad of macrosomia, omphalocele, and macroglossia

A

Beckwith-Wiedemann syndrome

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9
Q

gastric leiomyosarcoma, pulmonary chondroma, and functioning extra-adrenal pheochromocytoma

A

Carney triad (see Neuro)

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10
Q

primary aldosteronism; hypersecretion of aldosterone by adrenal adenoma

A

Conn’s syndrome

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10
Q

bilateral adrenal hyperplasia caused by unregulated ACTH production by a pituitary adenoma

A

Cushing’s disease

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10
Q

excessive serum cortisol (hydrocortisone and corticosterone); HTN, truncal obesity, easy bruisability, hirsutism, oligo/amenorrhea, generalized weakness, muscle atrophy, DM, and abdominal striae

A

Cushing’s syndrome

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11
Q

lipid storage disease, enlarged densely calcified adrenal glands and mild adrenocortical insufficiency; to distinguish from ordinary adrenal hemorrhage, this disease has marked hepatosplenomegaly

A

Wolman’s disease

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11
Q

rare lipidosis; plain films are usually diagnostic

A

Wolman disease

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11
Q

small kidney, predominantly because of cortical loss in the upper pole associated with cortical indentations; thought by some to be a variant of renal hypoplasia; currently thrught to be caused by scarring due to chronic pyelo rather than true congenital lesion

A

Ash-Upmark kidney

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11
Q

absence or hypoplasia of the uterus and absence or aplasia of the vagina

A

Rokitansky-Kuster-Hauser syndrome

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12
Q

form of inherited RCC also characterized by hair follicle hamartomas and frequent pneumotosis from rupture of thin-walled lung cysts; chromophobe tumors or mixed chromophobe tumors and oncocytomas

A

Birt-Hogg-Dube syndrome

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13
Q

aka tuberous sclerosis; syndrome includes epilepsy, mental retardation, and various hamartomas; renal angiomyolipomas and multiple renal cysts, retinal phakomas and cerebral hamartomas; small cutaneous angiofibromas on the face (adenoma sebaceum) / cutaneous, retinal, cardiac, cerebral hamartomas

A

Bourneville disease

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13
Q

male pseudohermaphroditism, glomerulonephritis, Wilms tumor

A

Drash syndrome

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14
Q

multiple renal cysts, multiple and bilateral RCC, adrenal pheochromocytomas, pancreatic cysts (serous cystadenomas), and pancreatic islet cell tumors/adenocarcinomas; retinal angiomas/hemangioblastomas and cerebellar hemangioblastomas; papillary cystadenomas of the epididymis

A

von Hippel-Lindau disease

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14
Q

mass effect against the kidney causing ischemia resulting to excess renin secretion and hypertension

A

Page kidney

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14
Q

hereditary nephritis/nephropathy and nerve deafness; cortical nephrocalcinosis may be seen

A

Alport syndrome

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15
Q

aka prune belly syndrome; rare; classic triad of absent abdominal musculature, undescended testicles, and urinary tract abnormalities

A

Eagle-Barrett syndrome

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15
Q

upper pole infundibulum is scissored between 2 vessels resulting in hydrocalyx and pain or, alternaltively, pressure from 1 crossing vessel resulting in
isolated hydrocalyx

A

Fraley syndrome

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15
Q

ulceration near the bladder dome that cracks and bleeds with bladder distention, which is a typical finding of interstitial cystitis at cystocopy

A

Hunner ulcer

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16
Q

nonneurogenic neurogenic bladder

A

Hinmann syndrome

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16
Q

bladder/paraureteral diverticulum occuring as a result of congenital deficiency in bladder musculature adjacent to the UVJ and commonly associated with VUR located lateral and cephalad to the ureteral orifice

A

Hutch diverticulum

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16
Q

congenital bladder diverticulum that occurs in close relationship to the ureteral orifice typically opening just above and lateral to it

A

Hutch diverticulum

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16
Q

pea-sized accessory sex glands within the urogenital diaphragm on either side of the membranous urethra

A

Cowper glands

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16
Q

connective tissue disorder which produces plaques in the tunica albuginea resulting in penile curvature and deformity

A

Peyronie disease

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17
Q

rapidly progressive polymicrobial necrotizing fasciitis involving the scrotum and perineum

A

Fournier gangrene

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17
Q

X-linked, triad: CC agenesis, chorioretinal lacunae, and infantile spasms; chroid plexus papillomas are also a part of this syndrome

A

Aicardi syndrome

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17
Q

through which pelvic tumors hematogenously spread resulting in subdural spinal lesions; through which prostate ca, just like infection, may preferentially ascend to the lumbar region/lower spine to reach the vertebrae

A

Batson’s venous plexus

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17
Q

ecchymosis over the mastoid process

A

Battle sign

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18
Q

one of the other terms for small vessel ischemic change; multi-infarct dementia

A

Binswanger disease

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19
Q

pulmonary chondromas, gastric stromal neoplasms (leiomyosarcomas), and pheochromocytoma

A

Carney’s syndrome

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19
Q

markedly elevated NAA levels (pathognomonic MR spectra) as a result of deficient aspartoacylase that metabolizes it, causing subsequent myelin destruction

A

Canavan’s / Canavan disease

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19
Q

bulbous tufts of choroid plexus in the CPA cistern extending from the 4th ventricle through its lateral recesses (normal finding)

A

Bochdalek’s flower basket

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20
Q

myxomas of the heart, breast, and skin as well as psammomatous melanotic schwannomas and osteochondromyxomas; associated with primary pigmented nodular adrenal dysplasia

A

Carney complex

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20
Q

rare AD syndrome characterized by lentiginous facial pigmentation / pigmented lesions of the skin and mucosa, cardiac, cutaneous, and other myxomas, and multiple endocrine tumors (such as pituitary adenoma) / endocrine overactivity, and Cushing syndrome; melanotic schwannomas occurs in 10% of cases

A

Carney complex / syndrome

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21
Q

cerebellar hypoplasia with cyst

A

Dandy-Walker complex

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21
Q

aka “bleeding globes”; small pseudoaneurysms due to weakening of the lenticulostriate arteries

A

Charcot-Bouchard aneurysms

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22
Q

rare; transmissible spongioform encephalopathy caused by an infectious proteinaceous particle/prion

A

Creutzfeldt-Jakob disease

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22
Q

characeristic secondary brain stem lesion; midline hematoma in the tegmentum of the rostral pons and midbrain seen in association with descending transtentorial herniation

A

Duret hemorrhage

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22
Q

centripetal perivenular extension radiating outward from the lateral ventricles, seen in MS

A

Dawson fingers

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22
Q

cloverleaf skull due to bicoronal AND bilambdoid synostoses; bulging temporal bones, towering skull, and shallow orbits

A

Kleeblattschadel

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22
Q

aka basal cell nevus syndrome; associated with medulloblastomas + dense tentorial/falcine calcifications

A

Gorlin syndrome

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23
Q

cerebral hemiatrophy typically caused by an in utero or early childhood cerebral insult; lack of ipsilateral brain growth causes the calvaria and diploic space to thicken, whereas the paranasal sinuses and mastoids become enlarged and hyperaerated

A

Dyke-Davidoff-Masson syndrome

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23
Q

other term for septooptic dysplasia

A

de Morsier syndrome

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23
Q

anomalies of the kidneys, eyes, extremities, liver, and bile ducts are common in the JSRD spectrum; hallmark: molar tooth sign

A

Joubert syndrome, JS-related disorders

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23
Q

rare AR disorder in which hydranencephaly is accompanied by glomeruloid vasculopathy of the CNS vessels and neurogenic muscular atrophy

A

Fowler syndrome

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23
Q

rare; seen in uncal herniation as a focal impression on the contralateral cerebral peduncle against the tentorial margin due to displacement of the brain stem, resulting in peduncular hemorrhage or infarction; mass effect on CN III and compression of the contralateral cerebral peduncle cause characteristic blown pupil with ipsilateral hemiparesis

A

Kernohan notch

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23
Q

proton MRS images obtained from the basal ganglia, occipital cortex, and brainstem show elevations in lactate, which are most pronounced in regions where abnormalities are seen with routine T2 MRI

A

Leigh syndrome

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24
Q

olfactory aplasia/hypoplasia + hypogonadotropic hypogonadism; pituitary gland hypoplasia as well as visual and septal anomalies are common

A

Kallman syndrome

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24
Q

intracorneal deposit of copper, which is virtually diagnostic of Wilson disease

A

Kayser-Fleischer ring

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25
Q

prominent basal arachnoid membrane that forms trabeculae that cross the suprasellar cistern and cover the hypothalamus and diaphragm sellae

A

Liliequist membrane

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25
Q

lacunar skull; focal calvarial thinning and scooped out appearance

A

Luckenschadel

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25
Q

mitochondrial enzyme defect

A

Leigh disease

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25
Q

aka dysplastic cerebellar gangliocytoma

A

Lhermitte-Duclos disease

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25
Q

iris hamartomas

A

Lisch nodules

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25
Q

histologically mixed neoplasms (malignant peripheral nerve sheath tumors with rhabdomyoblastic and other heterologous elements) that are very characteristic of NF1

A

malignant Triton tumors

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25
Q

Brant: rare form of demyelination usually involving the medial zone of the corpus callosum seen most frequently in alcoholics, Osborn: rare disorder characterized by osmotic demyelination and later necrosis of the corpus callosum

A

Marchiafava-Bignami disease

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25
Q

location of the trigeminal ganglion; just posterolateral to the cavernous sinus

A

Meckel’s cave

25
Q

persistent embryonic precursor of the vein of Galen

A

median prosencephalic vein of Markowski

25
Q

prominent posterior anastomotic vein that courses inferolaterally over the temporal lobe to drain into the transverse sinus

A

vein of Labbe

25
Q

persistent embryonic precursor of the vein of Galen

A

median prosencephalic vein of Markowski

25
Q

formed by the union of the bilateral internal cerebral veins and basal veins of Rosenthal in the quadrigeminal cistern; unites with the inferior sagittal sinus at the falcotentorial junction to form the straight sinus

A

vein of Galen

25
Q

dominant anastomotic superior cortical vein that receives the superficial middle cerebral vein and courses upward from the sylvian fissure to join the SSS

A

vein of Trolard

25
Q

classic lissencephaly + severe facial deformities; frontal bossing, hypertelorism, upturned nose, small jaw, and prominent upper lip with thin vermilion border

A

Miller-Dieker syndrome

25
Q

paralysis of upward gaze brought about by compression of the superior colliculus; can be seen in germinomas

A

Parinaud syndrome

25
Q

devastating disease of childhood and of unknown etiology, usually involving one hemisphere showing focal cortical swelling which later progresses to dramatic atrophy

A

Rasmussen encephalitis

25
Q

rapid enlargement of a pituitary adenoma following bilateral adrenalectomy, presentation of corticotroph tumors

A

Nelson syndrome

26
Q

transformation of CLL into diffuse large non-Hodgkin lymhoma

A

Richter syndrome

26
Q

antiphospholipid syndrome with widespread livedo reticularis and ischemic cerebrovascular episodes

A

Sneddon syndrome

26
Q

largest of the medial lenticulostriates of the ACA, which supplies the caudate head/anterior internal capsule region

A

recurrent artery of Heubner

26
Q

ischemic necrosis of anterior pituitary due to severe postpartum hemorrhage, which may result to secondary empty sella; rare variant of pituitary apoplexy

A

Sheehan syndrome

26
Q

encephalo-trigeminal angiomatosis

A

Sturge-Weber syndrome

27
Q

other term for focal cortical dysplasia

A

Taylor cortical dysplasia

28
Q

intraocular (most commonly subhyaloid) hemorrhage that is found in 12-13% of patients with aneurysmal SAH

A

Terson syndrome

28
Q

Osborn: triad of congenital muscular dystrophy, brain anomalies (primarily cobblestone cortex), and ocular abnormalities

A

Walker-Warburg syndrome

29
Q

involvement of medulla in PICA infarction; ataxia, facial numbness, Horner syndrome, dysphagia, and dysarthria

A

Wallenburg syndrome

29
Q

Pedia: most severe cerebellar hypoplasia is seen with WWS, also associated with occipital encephalocele

A

Walker-Warburg syndrome

30
Q

seen in LV enlargment on a lateral radiograph; when the LV extends >1.8 cm posterior to the IVC at a level 2 cm cephalad to the intersection of the LV and

A

Hoffman-Rigler sign

30
Q

reservoirs created by the closure of the aortic valve and from which the right and left coronary arteries arise

A

sinuses of Valsalva

30
Q

ASD associated with MS; combination of MS with a pre-existing ASD, resulting to marked right-sided enlargement

A

Lutembacher syndrome

30
Q

lateral retropharyngeal nodes

A

nodes of Rouviere

31
Q

perforated thin eustachean valve that partially guards the opening of IVC in the RA

A

network of Chiari

31
Q

triad of acute onset of ocular movement abnormalities, ataxia, and confusion

A

Wernicke encephalopathy

31
Q

Wernicke encephalopathy + persistent learning and memory deficits

A

Wernicke-Korsakoff syndrome

32
Q

separated the intra- and extraconal spaces

A

annulus of Zinn

32
Q

AVMs are found in both the retina and brain

A

Wyburn-Mason syndrome

32
Q

other term of mitral valve prolapse aka floppy mitral valve

A

Barlow syndrome

33
Q

SMALL and MEDIUM vessel system vasculitis; inflammatory condition of the coronary arteries, probably attributable to prior viral syndrome, which results

A

Kawasaki syndrome

33
Q

heart-hand syndrome; CHD (ASD [MC], VSD, or PS) associated with radial ray hypoplasia (hypoplasia of the UE, specifically, radius and thumb -

A

Holt-Oram syndrome

33
Q

noninfectious valvular vegetations that may be seen in association with SLE

A

Libman-Sack vegetations

34
Q

morbid obesity affecting pulmonary mechanics, which may be a cause of cor pulmonale

A

Pickwickian syndrome

34
Q

angina secondary to prolonged coronary spasm

A

Prinzmetal variant angina

35
Q

incomplete transposition of the great vessels; the pulmonary artery arises from both the right and left ventricles and overrides the VSD; aka DORV type II

A

Taussig-Bing anomaly

36
Q

rare; focal or complete absence of the RV myocardium leading to an RV that becomes a thin-walled fibroelastic bag

A

Uhl’s disease

36
Q

hypercalcemia, efin facies, mentral retardation, and supravalvular aortic stenosis

A

Williams syndrome

36
Q

rare acquired (initially thought to be congenital) cardiomyopathy in infants or adults with parchment-like thinning of the RV; aka arrythmogenic RV

A

Uhl anomaly

36
Q

congenital aplasia of RV myocardium, RV CMY

A

Uhl syndrome (anomaly)

37
Q

severe pulmonary stenosis with intact interventricular septum (so ASD or patent foramen ovale) and right-to-left atrial shunt

A

trilogy of Fallot

37
Q

dilatation at the origin of an aberrant right subclavian artery

A

diverticulum of Kommerell

37
Q

least vascular area of the kidney

A

Brodel plane

37
Q

example of aortoiliac occlusive disease - bilateral buttock claudication, impotence, absent femoral pulses; typically associated with the occlusion of the infrarenal abdominal aorta

A

Leriche syndrome

38
Q

variable communication between SMA and IMA located more centrally in the mesentery than the marginal artery

A

arc of Rioloan

38
Q

provides anastomosis between the right colic, right and left branches of the middle colic, and the left colic arteries

A

marginal artery of Drummond

38
Q

short ventral artery between the main celiac and SMA representing a persistent fetal communication

A

arc of Buehle

38
Q

rare malignant neoplasm arising from the chest wall of CHILDREN and YOUNG ADULTS, which arises from primitive neuro-ectodermal rests in the chest wall; very agressive with a high mortality rate

A

Askin tumor

38
Q

compression of the left iliac vein by the right iliac artery crossing over it

A

May-Thurner syndrome

38
Q

compression of the subclavian vein by a cervical rib, soft tissue anomaly, or scar tissue after clavicle fracture -> thrombosis and swelling

A

Paget-Schroetter syndrome

39
Q

rare cause of lung cysts or bullae; skin fibrofolliculomas, malignant renal tumors, and thin-walled lung cysts

A

Birth-Hogg-Dube syndrome

39
Q

surgical anastomosis of the proximal subclavian artery to the ipsilateral pulmonary artery; causes unilater rib notching

A

Blalock-Taussig procedure

40
Q

channels bridging preterminal bronchioles with alveoli

A

canals of Lambert

40
Q

interalveolar channels

A

pores of Kohn

41
Q

persistent communication of an enteric cyst with the spinal canal

A

canal of Kovalevski

42
Q

Castleman disease

A

angiofollicular LN hyperplasia

42
Q

calcified granuloma/Ghon focus or lesion + calcified LN or calcified Ghon complex

A

Ranke complex

42
Q

multiple peripheral cavitating nodules; nodules in the lungs of coal miners and silica or asbestos workers with RA as a hypersensitivity response to inhaled dust particles; rheumatoid pneumoconiosis

A

Caplan syndrome

43
Q

allergic angiitis and granulomatosis

A

Churg-Strauss syndrome

43
Q

aka postmyocardial infarction syndrome; autoimmune, pleural and pericardial effusion/inflammation after MI

A

Dressler syndrome

43
Q

congenital defect in COLLAGEN SYNTHESIS associated with joint laxity, skin stretchabillity, aneurysms, and mitral regurgitation

A

Ehlers-Danlos syndrome

43
Q

pleura-based wedge-shaped; typically in the posterior or lateral costrophrenic sulcus; blunted apex of the wedge points toward the occluded feeding vessel

A

Hampton hump

44
Q

uncorrected left-to-right shunts, hypertrophy of the pulmonary arterioles (medial hyperplasia and intimal fibrosis) -> increased pulmonary vascular resistance

A

Eisenmenger syndrome

44
Q

granuloma/Ghon focus or lesion + ipsilateral lymphadenopathy

A

Ghon complex

44
Q

autoimmune, damages the alveolar and renal GBM by a cytotoxic antibody

A

Goodpasture syndrome

44
Q

granuloma (so parenchymal) (pag lesion/focus, isang finding lang. pag complex, more than 1 finding)

A

Ghon lesion/focus

45
Q

other term for acute interstitial pneumonia

A

Hamman-Rich syndrome

45
Q

Kartagener syndrome

A

triad of sinusitis, situs inversus/dextrocardia, and bronchiectasis

45
Q

shorter (1-2 cm) thin lines, PERIPHERAL and PERPENDICULAR TO THE PLEURA near the costrophrenic angle; represent thickened peripheral subpleural
interlobular septa

A

Kerley B lines

46
Q

parotid enlargement, uveitis, facial nerve paralysis

A

Heerfordt’s syndrome

46
Q

rare; localized PERIPHERAL OLIGEMIA w/ or w/o distended proximal vessels

A

Westermark sign

47
Q

linear, 2-6 cm long, <1-mm-thick, OBLIQUELY oriented and course TOWARD THE HILA; correspond to distended perivenous and bronchoarterial lymphatics / thickening of the central connective tissue

A

Kerley A lines

48
Q

NETWORK of thickened interlobular septa; random reticular lines throughout the lungs

A

Kerley C lines

49
Q

bronchial endocrine cells; thymic cells of neural crest origin; aka amine precursor uptake and decarboxylation (APUD) cells

A

Kulchitsky cells

50
Q

rare form of endomyocardial fibrosis associated with eosinophilia

A

Loffler endocardial fibrosis

50
Q

simple pulmonary eosinophilia / acute allergic eosinophilic pneumonia associated with parasite infestation; consolidation is typically migratory

A

Loffler syndrome

50
Q

triad of B hilar AD, erythema nodosum, & polyarticular arthritis (in sarcoidosis)

A

Lofgren’s syndrome

50
Q

uncommon finding on the frontal radiograph in LUL atelectasis; crescent of air along the left upper mediastinum, which represents a portion of the overinflated superior segment of the LLL interposed between the aortic arch medially and the collapsed upper lobe laterally

A

Luftsiche

51
Q

optical illusion caused by a retinal reinforcement response

A

Mach bands / effec

52
Q

extra-alveolar air first collects within the bronchovascular interstitium and then dissects centrally to the hilum and mediastinum

A

Macklin effect

52
Q

gastric fluid aspiration

A

Mendelson syndrome

52
Q

benign pleural effusion and pelvic tumor

A

Meigs syndrome

52
Q

autoimmune, necrotizing granulomatous vasculitis involving the upper and lower respiratory tracts and kidneys

A

Wegener granulomatosis

52
Q

Pulmo: unilateral hyperlucent lung that follows infection with adenovirus, measles, or mycoplasma during infancy/early childhood; produced by asymmetric obliterative/constrictive bronchiolitis with severe air trapping and secondary unilateral pulmonary artery hypoplasia, Pedia: acquired hypoplastic lung that develops following severe obliterative bronchiolitis, leading to bronchiolar obstruction, bronchiectasis, and distal airspace destruction

A

Swyer-James syndrome / Macleod’s syndrome

53
Q

Sclerodermaa with other connective tissue dse

A

Overlap syndrome

53
Q

tracheobronchomegaly; congenital disorder of the elastic and smooth muscle components of the tracheal wall

A

Mounier-Kuhn syndrome

53
Q

unilateral absence/hypoplasia of the pectoralis muscle (most frequently sternocostal portion of the pectoralis major), ipisilateral hand and digit anomalies,
including symbrachydactyly, and rib anomalies; there may be associated aplasia of the ipsilateral breast

A

Poland syndrome

54
Q

peripheral neoplasm arising in the superior sulcus/lung apex indented superiorly by the subclavian artery

A

Pancoast tumor

54
Q

hypervascularity of any chronic infection Pulmo Reid index ratio of mucous gland thickness to bronchial wall thickness; abnormally high index (>50%) correlates sttrongly with symptoms of excess mucus production

A

Reid index

54
Q

small vessel vasculitis of the eyes, joints, skin, CNS, and intestinal tract

A

Behcet disease

54
Q

Pulmo: erosion of a TB cavitary focus into a branch of the pulmonary artery can produce this aneurysm / Cardio: caused by TB and systemic

A

Rasmussen aneurysm

55
Q

other name for NF 1

A

von Recklinghausen disease

55
Q

GI: obstruction to hepatic venous outflow involving 1 or more hepatic veins, Vascular: occlusion of the hepatic veins caused by hepatic venous or IVC

A

Budd-Chiari syndrome

55
Q

congenital saccular ectasia of the IHBD w/o biliary obstruction; associated with medullary sponge kidney and ARPKD

A

Caroli disease

55
Q

proximal gallstone impaction resulting in duodenal or pyloric obstruction

A

Bouveret’s syndrome

56
Q

fever, pain, and jaundice (Acute bacterial cholangitis)

A

Charcot triad

57
Q

dorsal pancreatic duct, drains major portion of secretions (body and tail) into minor papilla

A

duct of Santorini

57
Q

thin lucent line traversing orifice of ulcer (think H=Harmless=benign)

A

Hampton line

57
Q

ventral pancreatic duct, drains minor portion of secretions (head and uncinate process) into major papilla in association with CBD

A

duct of Wirsung

58
Q

Siderotic nodules - small hemorhages in the spleen caused by portal HPN resulting in foci of hemosiderin deposits

A

Gamna Gandy bodies

58
Q

congenital asplenia assoc with bilateral right-sidedness, midline liver, and bilateral 3 lobed lungs

A

Ivemark syndrome

58
Q

major sign of ascites on radiograph; medial displacement of the lateral edge of the liver

A

Hellmer’s sign

58
Q

MC LYSOSOMAL storage disease, deficient glucosylceramidase

A

Gaucher’s disease

58
Q

asplenia; associated with GU and endocrine abnormalities

A

Ivemark’s syndrome

59
Q

large flat-based ulcer with heaped-up edges that fold inward to trap a lens-shaped barium collection that is convex toward the lumen (think M=Malignant)

A

Carmen/Carman meniscus sign

59
Q

endocrine cells from which carcinoid tumors arise; aka enterochromaffin cells

A

Kulchitsky cells

60
Q

spontaneous perforation/rupture of esophageal wall after severe, prolonged, forceful vomiting; vertical tear along the left (pag adults, left. pag pedia, right) posterolateral wall just above the EGJ, leading to acute mediastinitis

A

Boerhaave syndrome

60
Q

Hilar cholangiocarcinoma

A

Klatskin tumor

60
Q

biliary obstruction from a gallstone in the cystic duct eroding into the adjacent common duct and causing an inflammatory mass that obstructs the common duct

A

Mirizzi syndrome

60
Q

malignancy in the ovary that metastasized from a primary site, classically the GIT, although it can arise in other tissues such as the breast

A

Krukenburg tumors

60
Q

tear, only the MUCOSA and not the full thickness of the esophagus, violent retching

A

Mallory-Weiss tear

60
Q

Giant hypertrophic gastritis

A

Menetrier disease

61
Q

Colonic pseudoobstruction - acute colonic distention with abd pain and distention without mechanical obstruction

A

Ogilvie Syndrome

61
Q

Hereditary hemorrhagic telangiectasia; can present with pseudocirrhosis

A

Osler-Weber-Rendu Syndrome

61
Q

hereditary hemorrhagic telangiectasia characterized by epistaxis, mucocutaneous telangiectases, and visceral (including pulmonary) AVMs

A

Rendu-Osler-Weber disease

62
Q

multiple inflammatory (hamartomatous din ata to) polyps involving the SI in 50% of cases and always the colon and stomach; skin: nail atrophy, brownish pigmentation, and alopecia

A

Cronkhite-Canada syndrome

62
Q

multiple HAMARTOMATOUS polyps in the SI, colon, and stomach; melanin freckles on the face, palmar aspect of fingers and toes, and mucous membranes

A

Peutz-Jeghers syndrome

PBR 2 and 3 (41 decks)

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