Pediatrics 7,9,10 Flashcards Preview

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Flashcards in Pediatrics 7,9,10 Deck (97)
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1

What should be suspected in a baby with DiGeroge syndrome

- low serum calcium levels
- get echocardiography

2

CATCH for DiGeorge

- Conotruncal cardiac defects
- Abnormal facies
- Thymic aplasia
- Celft palate
- Hypocalcemia

3

In patients with hypertrophic cardiomyopathy, maneuvers that increase preload or afterload

- squatting
- leg raise
- hand grip

4

Maneuvers that decrease LV cavity by decreasing preload

- Valsalva
- abrupt standing
- amyl nitrite administration

5

hypertophic cardiomyopathy is common in who and how is it inherited

African American
Autosomal Dominant

6

Appears in age less than 1 with respiratory ( stridor, wheezing, coughing) and/or esophageal (dysphagia, vomiting, difficulty feeding) symptoms. Stridor is biphasic. Improves with neck extension

vascular ring

7

Laryngomalacia

collapse of the supraglottic structures during inspiration and presents with chronic inspiration stridor that improves with prone positioning

8

Pansystolic murmur that is loudest at the left lower sternal border and a diastolic rumble at the apex due to increased flow across the mitral valve

large ventricular septal defect

9

a 2 hour child with single loud second heart sound has what wrong with them

- single loud second heart sound

10

most common congenital cyanotic heart disease in the neonatal period

D-transposition of the great vessels

11

x-ray finding for D-transposition of the great vessles

"egg on a string" ( narrow mediastinum)

12

Beck's triad

- distant heart sounds
- distended jugular veins
- hypotension

13

Trisomy 18 baby with murmur at left lower sternal bordner

VSD

14

Most common heart defect in down syndrome

complete atrioventricular septal defect

15

what is an innocent cardiac murmur

-intesnity is grade I or II
- decreases with standing

16

what maneuvers reduce the intensity of innocent murmurs

decrease venous blood return ( standing, Valsalva)

17

patients with prolonged QT intervals are at risk for

- syncope
-ventricular arrhythmias
- sudden cardiac death

18

Those with congenital QT prolongation should avoid

- electrolyte derangements
- medications that block potassium channels

19

how do you prevent cardiac arrest in prolonged QT syndrome

beta blockers with pacemaker

20

greater than 5 day fever, bilateral nonexudate conjunctivitis, mucositis, cervical lymphadenopathy, rash and extremity changes

kawasaki

21

treatment for kawasaki

aspirin and intravenous immunoglobulin

22

Most serious potential sequelae of Kawasaki

coronary artery aneurysms

23

hear a harsh III/VI holosystolic murmur, next step

- echocardiography, not reassurance because it is harsh III/VI

24

can viral myocarditis cause liver problems

yes, hepatomegaly

25

Difficulty swallowing, feeding refusal and vomiting should raise concern for

foreign body ingestion

26

what ethnicity has decreased UGT activity

asians

27

child with impaired adaption to darkness, photophobia, dry scaly skin, xerosis conjunctive, sources cornea keratomalacia, bitot spots and folllicular hyperkeratosis of shoulders, buttocks, and extensor surfaces

vitamin A deficiency

28

white baby with growth failure and recurrent sinopulmonary infections typically raise concern for

cystic fibrosis

29

pancreatic insufficiency in baby can lead to

- steatorrheahea
- failure to thrive
- vitamin deficiencies

30

Common associations with celiac disease

- type 1 diabetes
- dermatitis herpetrifromis