Peds GI/GU

Question 1

Cholestasis in newborn

Answer 1

alpha-1 antitrypsin

Question 2

Galactosemia caused by what infx

Answer 2

E. Coli septicemia

Question 3

Fitz-Hugh-Curtis

Answer 3

Pain in liver capsule from ascending infx.

Question 4

What factor causes pain during mestrual cramps

Answer 4

Prostaglandin

Question 5

UTI in kids tx

Answer 5

Bactrim

Question 6

Resistant UTI in kids

Answer 6

Cipro

Question 7

Orthostatic Protenuria

Answer 7

2-5% of normal adolesents

Question 8

what is cryptorchidism

Answer 8

failure of testes to descend.

Question 9

when to surgically correct cryptorchidism

Answer 9

1 year old

Question 10

Breast mild jaundice

Answer 10

Hyperbili for 4-7 days … tx: supplement with formula

Question 11

Decreased urine,
HTN,
facial and pretibial swelling

Answer 11

Nephritic Syndrome (coca-cola urine)

Question 12

why measure complement in kidney dz

Answer 12

low C3 means postinfectious AGN or MPGN

Question 13

best tx for bed wetting like monosymptomatic enuresis

Answer 13

1. alarm
2. desmopressin
3. TCAs

Question 14

large flank masses
pulmonary hypoplasia
Potter faces

Answer 14

Auto Recessive PKD

Question 15

What is Potters faces

Answer 15

flattened ears/nose, micrognathia from oligohydramnios

Question 16

Monosymptomatic Enuresis

Answer 16

twice a week after age 5

Question 17

mcc renal insufficiency/obstruction

Answer 17

posterior urethral valves

Question 18

Wilms Tumor age and presentation

Answer 18

nephroblastoma

age 2-5 with large flank mass and no symptoms

Question 19

cyclical vomiting syndrome

Answer 19

recurrent predictable vomiting in kid

associated with abdominal migraines

Question 20

Mesenteric Adenitis

Answer 20

mistaken for appendicitis

Question 21

delayed passage of meconium

Answer 21

Meconium Ileus or

Hirschsprungs

Question 22

Meconuim ileus cause

Answer 22

CF

Question 23

Orchitis from?

Answer 23

Mumps (think foreign non-vaccinated kid)

Question 24

wilms tumor associate with what syndromes

Answer 24

WAGR (wilms, aniridia, genitoruinary, retardation)

Beckwith Wiedemann

Denys-Drash

Question 25

wilms tumor metastasizes where

Answer 25

lungs

Question 26

triple bubble with gasless colon

Answer 26

Jejunum atresia

Question 27

bloody stools, | abdominal distention

Answer 27

pneumotosis intestinalis from NEC

Question 28

Top 4 causes of Intussuscpetion

Answer 28

1. viral gastroenteritis 2. Meckels 3. polyps 4. Hematoma from Henoch-Schonlein

Question 29

Meckels scan

Answer 29

technicium 99

Question 30

what enzyme conjugates bilirubin

Answer 30

UGT

Question 31

what de-conjugates bilirubin

Answer 31

intestinal B-glucuronidase

Question 32

physiologic jaundice of newborn

Answer 32

high hematocrit sterile gut resolves day 4

Question 33

Red urate crystals in stool

Answer 33

signs of infant dehydration. Check for more than 7% wt. loss

Question 34

breast feeding failure jaundice tx

Answer 34

promote breast feeding to promote fecal urobilinogen

Question 35

threshold for phototherapy

Answer 35

12-20mg/dL?

Question 36

Common associations with Celiac

Answer 36

``` DM1 Dermatitis Herpetiformis (itchy skin rash) ```

Question 37

anyone with UTI wearing diapers needs

Answer 37

straight catheterization and culture instead of clean-catch

Question 38

Hepatomegally Jaundice Pale Stools

Answer 38

Biliary Atresia

Question 39

how do you dx biliary atresia

Answer 39

U/S

Question 40

biliary atresia tx

Answer 40

Kasai procedure (Hepatoenterostomy)

Question 41

what level is conjugated hyperbilirubinemia

Answer 41

>20% of total bili

Question 42

breast milk jaundice when

Answer 42

week 2

Question 43

Crigler-Najjar/ Gilberts enzyme?

Answer 43

UDP-GT deficiency

Question 44

Alloimmune Hemolytic Disease may result in conjugated or un-conjugated

Answer 44

Erythroblastosis fetalis unconjugated hyperbili and Coombs +

Question 45

physiologic jaundice conjugated or un-conjugated

Answer 45

resolves in 1st week of life unconjugated

Question 46

bloody stools

Answer 46

``` milk enterocolitis intussuception meckels e. coli shigella campylobacter? ```

Question 47

Beckwith Weidman

Answer 47

Macroglossia Omphalocele dysregulation 11p15 Wilms Tumor!

Question 48

Fitz Hugh Curtis

Answer 48

Liver capsule inflamm from ascending pelvic infx