restrictive cardiomyopathy

Question 1

define

Answer 1

get restrictive fillinh of ventricles [here contractile ie squeeze function of heart = okay, but relaxation/filling of heart is abnormal]

Question 2

Causes: miSSHAPEN

Answer 2

 Sarcoid

 Systemic sclerosis

 Haemochromatosis

 Amyloidosis

 Primary: endomyocardial fibrosis

 Eosinophilia (Loffler’s eosinophilic endocarditis)

 Neoplasia: carcinoid (→ TR and PS)

Question 3

s/s

Answer 3

• There is restriction to ventricular filling which may result in dependent oedema, ascites and an enlarged liver.

The following points are noted on cardiovascular examination:

• the JVP is raised
• Kussmaul’s sign may be detected
• the apex beat is usually palpable (in contrast to constrictive pericarditis)
• heart sounds may be distant
• S3 and S4 may be present

Question 4

ix

Answer 4

Chest radiograph:

• mild cardiac enlargement

ECG:

• low-voltage
• conduction defects

echocardiogram:

• increased left ventricular wall thickness
• systolic function is normal

radionuclide studies:

• normal systolic function

cardiac catheterization:

• normal systolic function
• elevated left- and right-sided filling pressures

Question 5

rx

Answer 5

Treatment is symptomatic.