Causes of restrictive cardiomyopathy.
Idiopathic
Amyloidosis
Haemochromatosis
Sarcoidosis
Scleroderma
Clinical features of restrictive cardiomyopathy (RCM).
Similar to constrictive pericarditis with features of RVF, raised JVP
Hepatomegaly
Oedema
Ascites
Kussmaul’s sign
Quiet heart sounds
Diagnosis of RCM.
Echo
MRI
Cardiac catheterisation
Management of RCM.
Treat cause