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Flashcards in UWorld Peds Deck (82):
1

Evaluation of 1˚ amorrhea when uterus is present

FSH
high: karyotyping
low: pituitary MRI

2

Leukocyte adhesion deficiency

delayed cord separation
recurrent infections w/o purulence

3

Onion skinning distal bone

Ewing's sarcoma

4

SCID genetics

XR

5

Chronic granulomatous disease etiology

NADPH oxidase deficiency

6

Erythromycin ointment is put on to prevent

gonococcal conjunctivitis

7

Which coxsackie causes myocarditis

B

8

Trachoma

leading cause of blindness worldwide
Chlamydia trachomatis

9

Neuroblastoma vs nephroblastoma/Wilms tumor

neuro crosses midline

10

Agammaglobulinemia
inheritance
Sx

XR (affects tyrosine kinases)
recurrent sinopulmonary and GI infections

11

McCune-Albright syndrome sx

precocious puberty, cafe-au-lait spots, multiple bone defects
3 p's: precocious puberty, pigmentation, polyostotic fibrous dysplasia

12

Tx of congenital long QT

BB + pacemaker

13

Spondylolithesis

when over vertebrae is pushed over edge of the other

14

PPx cat bite

augmentin

15

Edwards syndrome

trisomy 18
small jaw, VSD

16

Tx of sickle cell

hydroxyurea (increases HgF)
myelosuppression

17

Anemia in Fanconi anemia

macrocytic

18

Fanconi dx

chromosomal breaks seen

19

Toxo transmission

undercooked meat, cat feces

20

Subcutaneous nodules after sore throat

rheumatic fever

21

When to bolus hypotonic saline in initial resuscitation

NEVER JUST F***ING NEVER

22

Biphasic stridor in infant

vascular ring

23

Laryngomalacia stridor

inspiratory

24

Cervical lymphadenitis etiology

S aureus

25

Tx of pt with rheumatic fever, but not treated and now asymptomatic

continuous ppx, IM PCN q4wk

26

Fever with rash starting at head going to toe

rubella

27

Wehn to do renal and bladder US in UTI

if <24 mo and febrile

28

Tetrology of Fallot combination results in

right ventricular outflow obstruction
creates right --> left shunt
fixed by squatting (increased systemic vascular resistance)

29

Reye syndrome bx

micro vesicular fatty infiltration

30

Difference between CF and 1˚ ciliary dyskinesia

malabsorption

31

Congenital rubella

cataracts, hearing loss, PDA, IUGR (worst during first trimester)

32

Congenital varicella

limb defects

33

Marfan's mutation

fibrillin-1

34

When to do exchange transfusion for bili

>20-25

35

Meconium ileum is basically diagnostic of

CF
extremely thick meconium, difficult to get out
therefore small colon

36

Death in meningococcal disease

adrenal failure
bil adrenal hemorrhage
Waterhouse-Friedrichson syndrome

37

Howell-Jolly bodies

asplenia or functional asplenia
nuclear remnants of RBC not removed by a functioning spleen

38

Impetigo treatment

local if possible
muporicin

39

Kallman syndrome

X-linked recessive in boys and girls
absence of GnRH secretion

40

Deferoxamine

used in iron overdose

41

Complication of bronchiolitis in <2 mo olds

apnea

42

Tx of measles

vitamin A
(regeneration of epithelial cells in gut, lungs, retina)

43

Tx of renal tubular acidosis

oral bicarb

44

Recurrent infections in lymph nodes, neutrophils filled with organisms

chronic granulomatous disease
prevents oxidative burst with H2O2
dihydrorhodamine test/nitro blue tetrazolium

45

Organisms that cause infection in chronic granulomatous disease

gram +

46

When you done need to do a CT in meningitis before the LP

small babies, the fontanelle accommodates

47

Choanal atresia
sx

cyclic cyanosis when infant cannot breath through mouth
failure of posterior nasal passage to canalize

48

Osgood-Schlatter also called

traction appphysitis

49

EDTA for lead poisoning

only if emergent, otherwise use dimercaptosuccinic acid DMSA for chelation

50

Prader-Willi: loss of which copy?!

paternal

51

Peri-splenectomy care

vaccinations weeks before
PCN for years/until adulthood/for life

52

HUS symptoms

after diarrhea!
-thombocytopenia (petechiae)
-microangiopathic hemolytic anemia
-AKI

53

Kids with an itchy butt

pinworm
especially at night

54

Milk-protein induced enterocolitis
dx
tx

bloody stools
eliminate all dairy and soy from mother's diet, resolves by 1 yr old

55

Croup sx

barky cough, hoarseness, inspiratory stridor
laryngotracheitis

56

Contraindication to rotavirus vaccination

intuccesseption
(can cause it!)

57

Omphalocele or gastrochesis, which is associated with other anomalies such as cardiac defects

Omphalocele

58

When do not use doxy in Lyme

if <8 yr old

59

Most common cause of pneumonia in CF <20 yr old

S aureus

60

Tx common variable immunodeficiency

lifelong IVIG or subQ IG

61

+ trendelenberg sign

gluteus medius + minimus weakness, superior gluteal nerve

62

PAS+ lymphoma

ALL
TdT positive staining

63

Cause of iron deficiency in infants

premature introduction of cow's milk

64

Beckwith-Wiedemann syndrome
at birth
complications

birth: macroglossia, hemihypertrophy, umbilical hernia
complications: Wilm's tumor, hepatoblastoma

65

Dx malrotation --> volvulus

upper GI series

66

Definitive dx of muscular dystrophy

genetic testing

67

Genu varum is a result of what

vit D deficiency
Ricketts!

68

Hepatitis B renal disease

membranous nephropathy

69

Wiskott-Aldrich syndrom

eczema
recurrent infections
impaired cytoskeletal changes in WBC, platelets (WAS gene)
tx: stem cell transplant

70

Diarrhea --> nutritional deficiency with rash

pallegra (niacin/vit B3)
diarrhea
dermatitis
dementia

71

When you can start XR of hips

4 mo old

72

Common variable immunodeficiency vs Burton agammaglobulinemia

Burton's is more severe and presents earlier

73

How does standing quickly/valsalva affect hypertrophic cardiomyopathy

decrease preload, increase intensity of murmur

74

Precocious puberty in obese children etiology

increased adrenal androgen production (development of hair only)
may also occur centrally

75

Thalassemia on peripheral smear

target and teardrop cells

76

Alpha thal minor hgb electrophoresis

normal

77

Betal thal minor hgb electrophoresis

increased hgb A2

78

Diamond-Blackfan anemia

pure red cell aplasia
presents around 3 mo

79

Riboflavin deficiency

stomatitis, glossitis, angular ketosis
rash

80

Beriberi

B1, thiamine
peripheral neuropathy, heart failure

81

Breastfeeding reduces the risk of which cancers

ovarian and breast

82

CF an infertility in men

absence of vas