Flashcards in Vascular Malformations Deck (7)
Types of vascular malformations?
Capillary - port wine stain
Lymphatic - develop when lymphatics fail to connect to venous drainage.
Venous- Low flow anomalies of vessels.
Arteriovenous - fast flow AV shunts that bypass high resistance capillary beds.
Pathnognomonic finding in Klippel-Tenaunay syndrome?
Embryonic sciatic vein - runs from dorsal aspect of the foot and terminates in femoral or iliac vessels.
- dilates overtime due tot valve incompetence.
*Deep venous system may be absent.
Capillary malformations presentation?
-present at birth- flat pink/red patches (highly variable size/location)
-Limb length discrepancy may be present if located on the extremities.
-may signal underlying Neuro abnormalities.
Lymphatic malformations presentation?
Highly variable presentations- cystic mass, angiokeratoma, chylous leak, Gotham-stout, generalized lymphatic anomaly, lymphedema.
Venous Malformations Presentation?
-may be seen at birth or later, usually in the skin/soft tissues.
-Grow in proportion to that of the child.
-GI Venous malformations
- Blue rubber bleb nevous syndrome- multiple small venous malformations in the skin(palms and soles) and GI tract.
GI venous malformations location and presentation?
-Most common left colon and rectum focal lesions
- may see perineal discoloration
-can cause extensive GI hemorrhage
-Risk for portal venous thrombosis.