Biliary Atresia (2) Flashcards
1
Q
What is this?
→ What does it lead to?
How does it present?
A
➊ Congenital narrowing/absent bile duct
→ Cholestasis and conjugated hyperbilirubinaemia
➋ • Prolonged jaundice (14+ days)
• Signs of biliary obstruction – Dark urine, Pale stools, Itchiness
2
Q
Which investigations should be done?
How is it managed?
A
➊ • Conjugated and Unconjugated bilirubin levels – High proportion of conjugated bilirubin suggests post-hepatic jaundice
• Cholangiography
➋ Surgery - Kasai procedure (Hepatoportoenterostomy) – Section of small intestine attached to opening of liver
