Congenital Heart Diseases Flashcards

0
Q

Schmitar syndrome

A

Snowman appearance
Hypo plastic lung
Pulm vein drain into ivc

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1
Q

All asd should be closed

A

If the RV begin to dilate

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2
Q

Fontan

A

For tricuspid atresia

Watch for anemia

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3
Q

Coarctation

A

Collaterals or gradient more than 20 mm need surgery

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4
Q

Tetralogy

A

May develop low pressure severe PR pt may not have a pulmonic valve mat have severe PR which may interfere with fontan

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5
Q

Deferential cyanosis

A

PDA

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6
Q

Down

A

Trisomy 21

Asd primum, vsd, TOF

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7
Q

Turner

XO

A

Coarctation.

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8
Q

Turner

XO

A

Bicuspid valve

Ascending aneurysm in 50%

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9
Q

Marfan

A

Aortic root use ARB, statin

Greater than 6 ___30% risk of rupture

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10
Q

Noonan

A

Web neck

Peripheral pulm stenosis

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11
Q

Root bicuspid

A

Surgery>5.5
Family history,expansion >5.0..

Dietz/ loeys bifid uvula surgery for 4.5 Aldo look for cerebral aneurysm

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12
Q

Eisenmenger

A
Ps may be protective 
Bleeding 
Air thromboembolic
CHF 
Arrhythmia 
Hyper uricemia
Watch for anemia and ferritin
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13
Q

Sudden death

A

HOCM
Commotio cordid
Anomalous coronary

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14
Q

Infective endocarditis

A

Prosthetic valves
Previous IE
Cyanotic heart disease

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15
Q

Fontan

A

Tricuspid atresia ivc to PA .
It duesnt work well with afib, thrombi,
Protein losing enteropathy

16
Q

Glen and bidirectional Glenn

A

Bypassing ivc SVC to PA

17
Q

Asd

A

Fishhook appearance on the r wave on the EKG
Chambers enlarge RA RV and pa
PDA RV and RA are spared

18
Q

Sinus node dysfunction

A

SVC obstruction
SA node dysfunction
Afib

19
Q

AV septal defect

A

EKG
First degree AV block
RBBB lafb
CHB

20
Q

Asd closure

A

RV enlargement
Paradoxical emboli
Orthodeoxia
Pa pressure less than2/3 systemic

21
Q

Vsd

A

Louder the murmur with thrill less serious it is

Vsd only peri membranous cN be fixed with closure device

22
Q

Vsd closure

A

Shunt less rhAn 1.5 and pap less than 2/3 systemic

If there is LV dysfunction

23
Q

PDA

A

If you can hear the murmur fix it

24
Q

Tof

A

Bla lock taussig, Potts , waterson all create shunts .
Watch for low pressure PR there may not be a valve
Qrs greater than 180 is bad
Lad from RCA in 3-7% of TOF patients
CTA is the best for diagnosisp

25
Q

Pulm valve

A

Only murmur on the right side which decrease on inspiration

26
Q

L transposition

A

CHB

Ppm difficult to put because if the baffle

27
Q

Transposition D

A

Arterial switch pa and aorta

28
Q

Congenital coronary stenosis

A

Rubella
Homocysteinuria
Supra valvular stenosis

29
Q

High RA pressure

A

Poor prognostic sign in TR

30
Q

Lower the compliance

A

Higher the V wave