Exam 1: Pediatric General Surgery Part 2 Flashcards
(49 cards)
How many types of Tracheoesophageal Fistulas (TEF) are there?
- 5 Types
- A, B, C, D, and E
Which Tracheoesophageal Fistula (TEF) is the most common?
- Type C (80-85%)
- Proximal esophageal pouch and a Distal tracheoesophageal fistula
Often associated with VACTERL
Where are Tracheoesophageal Fistulas (TEF) usually located?
1-2 rings above the carina
When does Tracheoesophageal Fistula (TEF) occur during gestation?
4th to 5th week of gestation d/t error in separation of trachea from floor of foregut
What is Tracheoesophageal Fistulas (TEF) often associated with?
- VACTERL
What does VACTERL stand for?
Acronym for a spectrum of congenital anomalies:
Vertebral anomalies
Imperforated Anus
Congenital heart disease
TracheoEsophageal fistula
Renal anomalies
Limb anomalies
How is Tracheoesophageal Fistulas (TEF) prenatally diagnosed?
- Polyhydramnios (↑amniotic fluid)
- Small/absent gastric bubble
- Blind ending upper pouch in the fetal neck.
What are postnatal S/S of Tracheoesophageal Fistulas (TEF)?
- Excessive salivation
- Choking
- Coughing
- Regurgitation at first feeding → Cyanosis/ distress
- Distended abdomen from baby crying
- Inability to pass NGT
What are the three C’s of Tracheoesophageal Fistulas (TEF)?
- Choking
- Coughing
- Cyanosis
Tracheoesophageal Fistulas (TEF) is confirmed with the inability to pass NGT into the stomach more than how many centimeters?
7 cm
Other ways to confirm diagnosis include dilated proximal esophagus with air in conjunction with air in the distal stomach on Xray, CT or direct visualization via bronchoscopy/endoscopy
What does the yellow circle indicate?
What does the red arrow indicate?
What is the suspected diagnosis?
- Yellow Circle: Feeding tube coiled in the esophageal pouch
- Red Arrow: Large volume of gas in the abdomen.
- Dx: Tracheoesophageal fistula with esophageal atresia
For pre-surgical goals of TEF, the proximal pouch should be secured and placed to ____ suction.
Continuous
Why should mask ventilation be avoided in TEF patients about to undergo surgery?
Mask ventilation can exacerbate gastric distention
What position is used for a thoracoscopic TEF procedure?
Left lateral decubitus position for a right thoracotomy approach to avoid the aortic arch
Why is the fistula ligated first in a TEF procedure?
Prevent further air entrapment in the stomach
Primary “End to End” anastomosis of the esophagus follows the ligation
ETT placement for TEF procedures
- The tip of the ETT is placed above the carina but distal to the fistula
- This is achieved by purposeful right main stem intubation and withdraw ETT while auscultating the left chest until breath sounds are first heard bilaterally
Can also verify with fiberoptic scope to correct placement
Anesthetic Considerations for TEF
- Keep the infant spontaneously breathing.
- IV induction w/ muscle relaxants can optimize intubation.
- Gentle mask ventilation with low peak pressure
- Frequent ETT suctioning
- After surgical correction ventilation with increased I:E time to re-expand alveoli
- Leave pt intubated, transfer to NICU
- Maintain head in neutral position (prevent pulling on the esophageal anastamosis)
- An epidural catheter from the caudal space or an intrapleural catheter can be left in place for post-op analgesia
Is pyloric stenosis more common in firstborn males or females?
More common in firstborn males (4:1)
When and how is pyloric stenosis diagnosed?
- Usually dx b/w 2-8 weeks of age with non-bilious projectile vomiting
- Immediate post-prandial vomiting
- Hungry in b/w feedings
Define pyloric stenosis
- Hypertrophy and hyperplasia of the muscular layer of the pylorus
- Causes a gastric outlet obstruction
Treatment of pyloric stenosis
- Supportive treatment (treat lytes imbalance)
- Pyloromyotomy (laparoscopically)
What kind of acid-base imbalance does pyloric stenosis cause?
Hypochloremic hypokalemic metabolic alkalosis
Severe cases can progress to metabolic acidosis
How is the hypertrophied pylorus muscle often presented?
Olive-shaped mass in RUQ
What IV fluids are administered to infants with pyloric stenosis
Dextrose IVF