15b Devo abnoramlities Flashcards Preview

03 GI Nutrition > 15b Devo abnoramlities > Flashcards

Flashcards in 15b Devo abnoramlities Deck (12)
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0
Q

VACTERL

A

Vertebral, anorecctal, cephalic, cardiac, TEF, Renal, Limb

1
Q

Esophageal atresia

A

Associated with VACTERAL

2
Q

Neonatal jaundice

A

Formula fed peak at 6mg/dL by day 3
Breast fed peak at 15-18 mg/dL by day 4
* Decr. by day 6

3
Q

Abnormal jaundice

A

*>2 wks
Direct bili >2mg/dL
Toatal >12(term or >14(preterm)

4
Q

Biliary atresia

A

*presents at 4-6 wks with jaundice and conj hyperblirubinemia
*Light stool, dark urine
inflammatory Distruction of extra-hepatic biliary tree.
*Bile plugs on liver biopsy
*Bile ductal proliferration (CK19 pos)
*Later total bile ducct obliteration and fibrosis

5
Q

Biliary atreasia Tx

A

ADEK supplement
Ursodeoxycholic acid 20 mg/day- 2 years
Ampicillin for cholangitis prophylaxis

6
Q

Malrrotation

A

Ladds bands- Attachment of cecum to gut wall

*Contrast doesnt cross spine- should go to ligament of treitz

7
Q

Duodenal atresia

A
  • Double bubble sign

* Association with trisomy 21

8
Q

JEjunoileal atresia

A

Ischemic

  • thromosis
  • vasoactive medications
9
Q

Meckels diverticulum

A

True diverticulum from failed regression of vitelline duct
Rule of 2- 2% population, 2 feet of ileocecal valve, 2 inches in length, presents by age 2
*Gastric mucosa -true diverticulum with all layers

10
Q

Hirsprungs

A

Associated with Trisomy 21

  • RET mutations- TKreceptor
  • aganglionic (big round cells), Huge nerves
11
Q

Necrotizing enterocolitis

A
  • Sometimes treatment with antibiotics or peritoneal drainage is sufficient
  • 5% stage II with occasional need for surgery and 15% mortality
  • 5% stage III with Needed surgery 28-54% mortality

Overal 20-30% mortality
*Short gut, nerodevelopmental dela, bronchiopulmonary dsplasia