198 Congenital GU anomalies Flashcards

1
Q

What is the most likely cause of congenital GU anomalies that are found on prenatal ultrasounds and persist after birth?

A

ureteropelvic junction obstruction

antenatal urinary tract dilation is the most common self-resolving cause

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2
Q

What is a common cause of recurrent UTIs in children?

A

vesicoureteral reflux

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3
Q

What is the management for vesicoureteral reflux?

A

prevention of further UTIs and renal scarring

can treat with prophylactic antibiotics and correction of bowel and bladder dysfunction

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4
Q

What is the most common cause of bladder outlet obstruction in boys?

A

posterior urethral valve

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5
Q

When should you intervene to correct undescended testes?

A

after 6 months

testes rarely descend spontaneously after 6 months of age and require surgical correction

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6
Q

A 28 yo pregnant woman is seen as a consultation for prenatally-detected urinary tract dilation. The most likely diagnosis is:

a) vesicoureteral reflux
b) ureteropelvic junction obstruction
c) ureterocele
d) multicystic dysplastic kidney
e) a benign condition that will resolve on its own

A

e) a benign condition that will resolve on its own

50-80% of all antenatal hydronephrosis will resolve on its own

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7
Q

A 14 year old boy presents with intermittent flank pain for the past 2 months. Ultrasound and MAG-3 diuretic renogram are suspicious for a ureteropelvic junction obstruction. The most likely etiology is:

a) adynamic ureteral segment
b) fibroepithelial polyp
c) a crossing vessel
d) a high insertion of the ureter into the pelvis
e) an intrinsic narrowing at the ureteropelvic junction

A

c) a crossing vessel

  • the intermittency of his symptoms most likely represents an intermittent UPJ obstruction - crossing vessel is the most common etiology of an intermittent UPJ obstruction*
  • choice A, D, and E are associated with asymptomatic or constant obstruction; choice B is a very rare cause*
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8
Q

Orichiopexy for an undescended testis discovered at birth should be performed at:

a) the time of discovery
b) 3 months of age
c) 6 months of age
d) 7 years of age
e) puberty

A

c) 6 months of age

it is unlikely to spontaneously resolve at this point, waiting longer poses risk to spermatogonia

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9
Q

A 5 yo girl presents after a febrile UTI. To determine whether vesicoureteral reflux is present, the diagnostic imaging study that should be performed is:

a) VCUG
b) Mag 3 diuretic renogram
c) CT scan of the abdomen and pelvis
d) cystoscopy
e) renal and bladder ultrasound

A

a) VCUG

a voiding crystourethrogram is the gold standard for diagnosing vesicoureteral reflux

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10
Q

What is the most common cystic disease of childhood?

A

multicystic dysplastic kidney

diagnosis made on prenatal ultrasound, associated with contralateral vesicoureteral reflux and ureteropelvic junction obstruction

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11
Q

What is the most common intrinsic cause of ureteropelvic junction obstruction?

A

adynamic ureteral segment

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12
Q

What is the most common extrinsic cause of ureteropelvic junction obstruction?

A

crossing vessel at an accessory lower pole renal artery

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13
Q

What is the most common cause of renal scarring in children?

A

vesicoureteral reflux

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14
Q

What is the Weigert-Meyer rule?

A

a rule to predict pathology of ureteral duplications which states that the ureter associated with the lower pole of the kidney inserts more laterally and refluxes while the ureter of the upper pole that inserts more medially will obstuct

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15
Q

What are ureteroceles?

A

saccular dilation of the distal ureter with variable presentation and complication

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16
Q

What is hypospadias?

A

failure of uretra to completely form to the tip of the penis, leading to a displaced urethra

17
Q

What is the treatment for ureteropelvic junction obstruction?

A

open or laparaoscopic pyeloplasty

18
Q

What is the treatment for vesicoureteral reflux?

A

low grade = prevent UTIs (prophylactic antibiotics)

high grade = surgery

19
Q

What radiographic finding is associated with multicystic dysplastic kidneys?

A

“bunch of grapes” on ultrasound

may also have signs of vesicoureteral reflux on VCUG

20
Q

How is antenateal urinary tract dilation assessed?

A

usually diagnosed on prenatal ultrasound at 20 weeks

21
Q

What are the signs of posterior urethral valve on prenatal ultrasound?

A

bilateral hydronephrosis

thick walled bladder with key hole sign

oligohydramnios (and possible Potter’s sequence)

22
Q

When does testis descent begin? What are the phases?

A

starts at 3 months of embryogenesis

transabdominal phase (from by kidney to inguinal canal) - 3-7 months

inguinoscrotal phase (down canal –> scrotum) - 7-8 months

spontaneous descent (within first 3 months of life)