test 5 tricuspid atresia

Question 1

Tricuspid Atresia characteristics

Answer 1

1. ASD
2. Atretic Tricuspid Valve
3. Hypoplastic RV
4. Pulmonary Stenosis
5. VSD
6. PDA

Question 2

Tricuspid Atresia

Answer 2

 3% of all Congenital Heart Disease
 Cyanotic Lesion
 Absence of tricuspid valve
 Prevents normal right heart circulation
 Blood returning from the RA must flow through an ASD/ PFO
 VSD or PDA must be present to permit blood flow to pulmonary circulation

Question 3

Tricuspid Atresia Clinical Features

Answer 3

 Mortality rate is high
 50% die within 6 months
 15-30% survive the first year without surgery
 10% live to 10 years without surgery
 Severe cyanosis – complete mixing of blood
 Clubbing
 Dyspnea
 Fatigue
 Right heart failure

Question 4

Tricuspid Atresia Surgical Correction

Answer 4

 Limited to increasing pulmonary blood flow
 Use one of the systemic to PA shunts or Rashkind procedure (balloon atrial septostomy)
 Systemic – PA shunts:
 B-T Shunt
 Bidirectional Glenn
 Fontan
 Possibility of PA bands if pulmonary stenosis isn’t present
 ** Cannot do valve replacement because the RV is under developed.

Question 5

Tricuspid Atresia CPB considerations

Answer 5

 Cannulation
         Arterial: Aortic
         Venous: Bicaval
 Cardioplegia
         Antegrade
                 Usually a single dose will suffice
 Hypothermia
         Moderate (around 28o)