Peds GI Disorders Flashcards

1
Q

What is Esophagreal atresia?

A

blind esophageal pouch w/ or w/o a fistulous connection between the proximal or distal esophagus & trachea

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
2
Q

Clinical Presentation of Esophagreal Atreasia

A

Polyhydramnios (excess amniotic fluid)infants in the 1st few hrs of life w/ copious secretions, choking, cyanosis & respiratory distress

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
3
Q

What imaging test is best used for Congenital Tracheoesophageal Fistulas and Esophageal Atresia

A

U/S followed by MRI

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
4
Q

How does TE fistulas present on X-ray vs EA?

A

TE fistula distal to the esophagus = gas PRESENT in bowel

EA WITHOUT TE fistula = NO gas seen in bowel

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
5
Q

Treatment of Congenital Tracheoesophageal Fistulas and Esophageal Atresia

A

NG tube in proximal pouch on low intermittent suction elevate head of bed to prevent reflux
IV glucose & fluids
O2
Surgery

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
6
Q

What is the most common FB ingested? How do these present on CXR if in the esophagus or trachea?

A

CoinsSee slide 9

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
7
Q

Treatment for button battery ingestion?

A

Requires endoscopic retrieval if lodged in the esophagusIf in stomach,

watch for 24-48 hours to see if it passes if not, must be removed endoscopically

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
8
Q

What happens in magnets are ingested in a child and how is it treated?

A

multiple magnets can lead to fistula formation w/in bowel wall… these need surgical intervention!

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
9
Q

Difference between GER vs GERD

A

GER: Reflux of gastric contents into the esophagus

GERD: present when reflux causes secondary sx or complications

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
10
Q

What situations cause GER?

A

Occurs during relaxation of of LE sphincter small stomach capacity
large volume feedings
short esophageal length
supine positioning

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
11
Q

Treatment for GER?

A

Usually benign expected to resolve by 12-18mo of life

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
12
Q

What GER symptoms are concerning

A
When infants develop sx like FTT, 
food refusal, 
pain, 
GI bleeding, 
upper or lower airway sx, etc. 
GER becomes GERD
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
13
Q

What Symptoms are seen with GERD in older children?

A

Older children = heartburn, dysphagia

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
14
Q

What are complications seen with GERD?

A

esophagitits recurrent pneumonia, recurrent cough dental erosions

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
15
Q

How is GERD treated?

A

Reflux usually resolves 85% of time in infants by 12 mo
Can use thickened foods with oat cereal
Milk free and soy free diet
PPI medicines have shown better improvements

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
16
Q

What risk is associated with given a PPI with infants?

A

risk for infection

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
17
Q

What are the 2 most common complications of Eosinophillic Esophagitits (EoE)

A
  1. esophageal food impactions

2. esophageal stricture

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
18
Q

How is EoE diagnosed?

A

Endoscopy

esophageal mucosa w/ thickening, mucosal fissures, strictures & ringsesophagus sprinkled w/ pinpoint white exudates (resembles candida)white spots composed of eosinophils

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
19
Q

How is Eosinophilic Esophagitits treated?

A

elimination of food allergens

swallowed topical steroids (MDI)2 puffs of Fluticasone BID

Do NOT rinse mouth (unlike w/ asthma) & avoid eating for 30min to improve effectiveness

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
20
Q

What is Pica?

A

Persistent eating of nonnutritive substances Animal feces, Clay, Dirt, Hairballs, Ice, Paint, SandAt least 1 month

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
21
Q

What labs should be order to determine PICA?

What is the treatment?

A

CBC
Zinc levels
Lead levels

Tx: Address nutrient deficiency or lead poisoning
Behavioral therapy and family education

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
22
Q

What is Rumination?

A

Repeated regurgitation and re-chewing of food At least 1 month

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
23
Q

complications of Rumination?

A
Associated with depression and eating disorders
Malnutrition
Failure to thrive
Weight loss
Bad breath
Tooth caries
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
24
Q

Malabsorpion

A

slide 22

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
25
Q

Malabsorption

A

slie 23

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
26
Q

What is the Most common inborn error of amino acid metabolism

How is this caused?

A

Phenylketonuria (PKU)

Decreased activity of phenylalanine hydroxylase (enzyme that converts phenylalanine to tyrosine)

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
27
Q

Clinical Presentation of PKU

Which is the MC finding?

A

Intellectual disability (the most common finding overall)

Fair skin and hair (impairment of melanin synthesis)
Atopic dermatitis
hyperactivity seizures
Musty or mousy odor to body & urine 
Epilepsy (50%)
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
28
Q

How can PKU be managed

How much phenylalanine should be consumed ideally?

A

Dietary restriction of phenylalanine and aspartame Goal is <6mg/dL phenylalanine a day

Tyrosine supplementation
Elimination of all high-protein foods (meat, dairy, nuts, legumes)Restrict starches

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
29
Q

MC food allergy in peds?

A

Cow’s milk (12%)

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
30
Q

What is the MC presentation of a Food allergy?

A

Skin: Urticaria and angioedema (most common)

31
Q

How are Food allergies diagnosed?

A

In vivo IgE against a specific food (skin testing)
In vitro for specific IgE
- RAST (radioallergosorbent testing )
-FEIA (fluorescent-enzyme immunoassay)
Removal and re-challenge
Clinical reactivity vs IgE antibodies

32
Q

Treatment for Food allergies?

A

Avoidance and re-introduction annuallyEpinephrineH1 blockers

33
Q

What is Celiac disease?

What are signs and symptoms?

A

Immune mediated enteropathy triggered by glutenabdominal pain, diarrhea, vomitingabdominal bloating or distention sometimes constipation

34
Q

What are GI complications that occur with Celiac disease?

A

chronic diarrhea, abdominal distention, irritability, anorexia, vomiting, poor weight gain

35
Q

What are non-GI complications that occur with Celiac disease?

A

delayed puberty or short staturedelayed menarche think CD w/ unexplained Fe def anemia

36
Q

How is Celiac’s Diagnosed?

How can it be treated?

A

Diagnosis: serology &/or duodenal biopsy (villous atrophy w/ increased intraepithelial lymphocytes)

Tx: gluten restriction for life (wheat, rye & barley)

37
Q

Essentially what is Omphalocele and Gastroschisis

A

Abdominal wall defects

38
Q

What is Omphalocele?

A

Membrane covered herniation of the abdominal contents into the base of the umbilical cord

39
Q

What is an GastroschisisWhat is the reason for incrased incidence of these?

A

Uncovered (no sac) intestine through small abdominal wall defect to the right of the umbilical cord Why?illicit drugs like meth & cocaine possible link w/ aspirin & ibuprofen use during pregnancy young maternal age

40
Q

How does someone with Diaphramtatic Hernia present?

A
Respiratory distress - intestines poking through to the lungs
Retractions, cyanosis, 
grunting respirations 
Scaphoid abdomen,
barrel-shaped chest
41
Q

How does someone with Diaphragmatic hernia present on CXR

A

bowel loops seen in chest w/ mediastinal shift to opposite side on CXR

42
Q

How is a Diaphragmatic hernia treated?

A

intubation, mechanical ventilation & decompression of the GI tract w/ OG tube

43
Q

What are Indirect hernia?
Who are they most common in?
What side is it most common?

A

Passes LATERAL to the deep epigastric vessels
Follows tract THROUGH the inguinal canal (goes “IN” the “Inguinal canal”)

Mostly male (9:1)

More common than direct & most common in childrenMC on the right side

44
Q

What is a Direct hernia? Where are these located?

A

Passes MEDIAL & INFERIOR to the deep epigastric vessels
Does NOT go through the inguinal canal
Hesselbach triangle
RARE in children

45
Q

What are Femoral hernias?
Where are they located?
Who are these most common?

A

Follows the tract below the inguinal ligament through the femoral canalMedial to the femoral vein and lateral to the lacunar ligamentMost common in females

46
Q

Who are umbilical Hernias most common?

A

More common in full term, African American infants

47
Q

What is Pyloric Stenosis?

A

Postnatal muscular hypertrophy of the pylorus

Progressive gastric outlet obstruction

48
Q

What is the MC presenting symptom of Pyloric Stenosis?

A

projectile postprandial vomiting

49
Q

What is a Hallmark sign on physical exam that indicates Pyloric Stenosis?

A

Hallmark sign: olive mass “stenosis” (mass in RUQ esp. after vomiting)

50
Q

What imaging is best used to diagnose Pyloric Stenosis?

A

Ultrasound

51
Q

What would be seen on Barium upper GI for pyloric Stenosis?

A

String sign- indicating the elongated narrowed pyloric canal

52
Q

What is a genetic cause of Duodenal atresia?

A

Associated with Trisomy 21 (30%)

53
Q

What findings will see on CXR with Duodenal atresia?

A

“Duodenal-Double bubble”Double-bubble sign (on abdominal xray) Dilated stomach & proximal duodenum

54
Q

What is a sign that is seen right after birth in an infant with duodenal atresia?

A

Bilious vomiting hours after birth

55
Q

What is Short Bowel syndrome?

A

A condition resulting from reduced intestinal absorptive surface

56
Q

What is Intussusception?

A

Telescoping of one segment of the intestine into another segment

57
Q

What are signs of Intussusception?

A

Passage of rectal blood and mucous“Red current jelly”- pathognomonicPalpable right-sided sausage-shaped massAbsent right-sided and cecal gas shadow on abdominal x-ray

58
Q

What is seen on abdominal x-ray with Intussusception?What imagining test is most sensitive for Intuussusception?

A

“target sign” (2 concentric radiolucent circles superimposed)Ultrasound

59
Q

What is the best therapeutic approach with Intussusception?

A

Air enema is the BEST therapeutic approach in the stable pt

60
Q

What is Meckels Diverticulum?

A

Outpouching or bulge lower part of the small intestineLeftover umbilical cord

61
Q

What is MC congenital anomaly of the GI?

A

Most common congenital anomaly of the GI tract

62
Q

How do you treat Jaundice?

A

Treatment by exposure to bright lights – phototherapy

63
Q

What affect does CF have on the pancrease?Intestine affects?

A

fat soluble vitamin deficiency intussception, rectal prolapse, carb intolerance

64
Q

Cystic Fibrosis

A

Oral supplementation of pancreatic enzymes improves digestion

65
Q

What is Pilonidial Cysts

A

Infection of the skin or subcutaneous tissue at or near the upper part of the natal cleft of the buttock

66
Q

Treatment for Pilonidial cysts?

A

Soaking in warm water ease pain of pilonidal cystsSurgical opening and draining of the infected sinus

67
Q

What signs and symptoms of Pinworms?

A

Worms in the stool or eggs on perianal skinintense anal pruritus - kids will scratch at the butt and contaminate fingers

68
Q

Diagnosis for for Pinworms?Treatment for pinworms? What instructions need to be followed?

A

Scotch tape testOTC: Pyrantel pamoate Instructions: treat all household members at the same time to prevent reinfections repeat therapy after 2 weeks

69
Q

What is Encopresis?

A

Repeated passage of feces into inappropriate places due to children not fully developing bowel control

70
Q

How is Encopresis treated?

A

Behavioral-educational treatment of encopresis:1) Educating both child and parents about the disorder and its relation to regular bowel action2) Designing a feasible program of consistent toilet use3) Positive reinforcements for successful use of the toiletScheduled toileting shortly after meals- gastrocolic reflux

71
Q

What pharmacotherapy can be used to treat Encopresis?

A

Initially – suppositories and enemasMiralax usually better

72
Q

HOw is Constipation defined?

A

Chronic constipation is defined as 2 or more of the following characteristics for 2 months:1) < 3 BMs per wk2) > 1 episode of encopresis per wk3) impaction of the rectum w/ stool4) passage of stool so large it obstructs the toilet5) retentive posturing & fecal witholding6) pain w/ defecation

73
Q

How is constipation treated?

A

diet changes “P” fruitsMedications:Miralax (polyethylene glycol) 0.8-1g/kg/dLactulose 1-2g/kg/dMilk of Magnesia