Manifestaciones Cutaneas De Otras Enf. Internas Flashcards

(30 cards)

0
Q

Manifestacion mas comun de la sarcoidosis

A

Eritema nudoso

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1
Q

Lesion mas caracteristica de la sarcoidosis

A

Lupus pernio

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2
Q

Dermatitis fotosensible que dibuja en el cuello el signo del collar de Casal

A

Pelagra

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3
Q

La pelagra se da por déficit de:

A

Niacina o triptofano

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4
Q

Piel de pollo desplumado en lateral de cuello y estrías anguiodes en la retina

A

Pseudoxantoma elastico

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5
Q

Aracnodactilia, subluxacion del cristalino y estrias de distension

A

Sx de Marfan

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6
Q

Formas cronicas de sarcoidosis

A

Fibrosis pulmonar
Uveítis cronica
Quistes oseos

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7
Q

Placa empastada, violacea en nariz, mejillas o lobulos de las orejas

A

Lupus pernio

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8
Q

Histologia de la sarcoidosis

A

Granulomas sarcoideos

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9
Q

Tx de sarcoidosis

A

Corticoides orales

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10
Q

Tx util para manejo de lesiones cutaneas cronicas

A

Cloroquina

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11
Q

Forma sistemica de amiloidosis con > afección cutánea

A

Primaria

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12
Q

Triada de la amiloidosis

A
Sx del tunel catpiano
Macroglosia
Lesiones mucocutaneas (ej. Petequias y equimosis)
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13
Q

Enfemedades a descartar en amiloidosis

A

Linfoma B

Mieloma multiple

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14
Q

Deficit enzimatico de la absorcion de zinc

A

Acrodermatitis enteropatica

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15
Q

Causa de la pelagra

A

Sx carcinoide

16
Q

Deficit de niacina y/o triptofano

17
Q

Deficit de vit C o acido ascorbico

18
Q

Cara de payaso, diarrea, caida de pelo y fragilidad ungueal

A

Actodermatitis enteropatica

19
Q

Diarrea + demencia + dermatitis fotosensible + collar de casal (papula eritrodescamativas)

20
Q

Queratosis, purpura perifolicular, sangrado de encias y hematomas subperiosticos

21
Q

Calcificacion de fibras elasticas de tejido cutaneo, ocular y vardiovascular

A

Pseudoxantoma elastico

22
Q

Manifestacion cutanea del Pseudoxantoma elastico

A

Papulas amarillas en pliegues “en piel de pollo”

23
Q

Manifestaciones oculares del Pseudoxantoma elastico

A
Estrias angioides (+ frecuente)
Alteracion en pigmento retiniano (+ precoz)
24
Claudicacion intermitente, hemorragia digestiva, HTA y oclusion coronaria son manifestaciones vasculares de:
Pseudoxantoma elastico
25
Manifestaciones cutaneas del Sx de Marfan
Estrias de distension | Elastosis perforante
26
Manifestaciones oculares del sx de Marfan
Lixacion del cristalino
27
Manifestaciones vasculares del sx de marfan
Aneurismas aorticos | Prolapso mitral
28
Manifestaciones cutaneas del sx de Ehlers - Danlos
Fragilidad | Alteraciones de la cicatrizacion
29
La hiperextensibilidad articular y ligamentosa son manifestaciones osteoarticulares del Sx de
Ehlers - Danlos