Chapter 53 souza

Question 1

prevalence of sickle cell

Answer 1

.3% of blacks

Question 2

1 in 10000 births

Answer 2

marfan

Question 3

fibrillin is affected in this condition

Answer 3

marfan

Question 4

occurs in 1 of 2500 births in US

Answer 4

cystic fibrosis

Question 5

asymptomatic cariers of CF

Answer 5

1 in 25 people

Question 6

life expectancy of Sickle cell

Answer 6

greater than 50 year old

Question 7

MC maligant tumor in second decade

Answer 7

osteogenic sarc

Question 8

osteogenic sarc is MC found in ___ and ____ of a joint

Answer 8

knee

metaphysis

Question 9

5 year survival rate of osteogenic sarc is

Answer 9

75% with aggressive treatment

Question 10

2nd MC malignant tumor of childhood

Answer 10

Ewing’s sarcoma - usually osteolytic and in diaphysis and febrile and increased ESR

Question 11

prognosis of Ewing’s sarcoma

Answer 11

chemotherapy and resection result in a five year survival rate of 50-60%

Question 12

confirms diagnosis of ewings sarcoma

Answer 12

biopsy

Question 13

keinbocks of navicular

Answer 13

kohlers

Question 14

What to do with kohlers?

Answer 14

adjust navicular/arch support

Question 15

osteochondrosis of capitullum of elbow with sclerosis, fissuring, fragmentation etc

Answer 15

Panner’s disease- temporary immobilization and avoid rapid movement of pronation and supination may take up to 2 years to heal

Question 16

4-12=___

13-16=___

Answer 16

4-12=Panner’s

13-16=osteochondritis dessicans

Question 17

avascular necrosis of radial head or capitullum

Answer 17

osteochondritis dessicans

Question 18

hepatosplenomegaly seen in ___% of leukemia cases

Answer 18

60%