Congenital Gastric And Duodenal Anomalies Flashcards
(10 cards)
Hypertrophic Pyloric Stenosis
Presentation: projectile non bloody emesis at 3-6 weeks. Dehydration, weight loss, FTT< jaundice, persistent hunger. Hypochloremic, hypokalemic metabolic alkalosis.
DDX: GER, Increased ICP, pylorospasm, metabolic disorder, other causes of gastric outlet obstruction.
PEx: palpable olive.
US: target sign. UGIS: “string sign.”
Management: correct electrolytes, then surgery.
Pyloric atresia/webs
Clinical sxs: dependent on degree of obstruction (antenatal polyhydramnios, nonbilious vomiting, early satiety, and weight loss).
Diagnosis: XR: solitary gastric bubble, US, UGIS.
Management: correct electrolytes, then surgery.
Microgastria
Solitary or Syndromic (intestinal malrotation, VACTERL).
GER, vomiting, aspiration pneumonia, FTT.
Prenatal US: mimic esophageal atresia: mega esophagus, failure to visualize distended stomach.
Gastric Duplications
Usually doesn’t communicate with stomach.
May contain ectopic gastric or ectopic pancreatic tissue.
Vomiting, feeding intolerance, palpable mass, PUD-like, Perforation.
Diagnosis: US: antenatal. CT: postnatal.
Duodenal Duplications
Obstructive symptoms related to compression.
Diagnosis: US: antenatal. CT: postnatal.
Gastric Volvulus: Emergency
Acute: sudden onset, severe epigastric abdominal pain, respiratory distress, nonbilious emesis.
Chronic: recurrent emesis, distension, FTT
Dx: unable to pass NGT, AXR, UGIS.
Bezoars
Trichobezoar: hair
Pharmacobezoar: drugs
Lactobezoar: milk
Vegetable: phylobezoar.
Tx: surgical.
Gastric perforation: neonates
Spontaneous: RF: asphyxia, prematurity, steroids, NEC.
Traumatic: intubation, NGT
Clinical: acute surgical abdomen, sepsis, high mortality.
Management: surgery
Gastric perforation: children
Trauma/child abuse
Duodenal hematoma
Blunt abdominal trauma,
Post EGD (coagulopathic, BMT)
SXS: obstructive with vomiting, abdominal pain,
+/- pancreatitis, biliary obstruction.
Anemia.
Diagnosis: imaging: filling defect on UGIs, CT.
Managment: conservative, responds with time.