Cystic Fibrosis

Question 0

Pathology of cystic fibrosis

Answer 0

Initially it is an obstructive lung disease caused by overall obstruction of the airways of mucus; later it progresses for restrictive lung disease because of the fibrosis, lung destruction and thoracic wall changes

Question 1

Define cystic fibrosis

Answer 1

AutoSomal recessive, multi system disease characterized by altered function of the exocrine gland primarily involved in the lungs, pancreas, and sweat glands

Question 2

Goals of therapy for CF

Answer 2

To promote clearance of secretions, control infection in the lungs, and provide adequate nutrition

Question 3

Nursing care for patient with CF

Answer 3

Revolves around the diagnosis of ineffective airway clearance, impaired gas exchange, ineffective breathing pattern’s, and imbalanced nutrition and ineffective coping