Dermatofibrosarcoma protuberans Flashcards

1
Q

Tissue sarcoma arising in the dermis and often penetrates into fat.
■ Etiology is unknown but has been reported to arise in scars. It is caused by a translocation between
chromosome 17 and 22.

A

Dermatofibrosarcoma protuberans

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2
Q

Peak age

A

20-50 yo

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3
Q

Presentation

A

non specific plaque often resembling a keloid w purplish to brown ish coloration

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4
Q

histo

A

a spindle cell proliferation often arranged as whorls

so-called herring bone pattern

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5
Q

Tx

A

mohs micrographic sx.
RT
In resection; prognosis is good

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