Hirschsprungs Disease Flashcards
1
Q
RF
A
Males, Downs, Fam Hx
2
Q
Presentation
A
Adbo distension, billious vomiting, no passing of mecionium within day 2 after birth.
Mass felt in LLQ.
3
Q
Investigation
A
Abdo XRAY, contrast enema (contra in bowel perf)
Gold standard for diagnosis is rectal suction biopsy.
4
Q
Management
A
IV abx, NG feeds and bowel decompression.
Definitive manage is bowel resection and reattachment to above dentate line.
5
Q
Complications
A
Hirschsprung associated enterocolitis.
