MTB - Pediatrics - Cardiology and GI

Question 1

Tetraology of Fallot consists of?

Associated with what genetics?

Answer 1

#RV hyperplasia
#Pulmonary Stenosis
#Overriding aorta
#VSD

Chromosome 22 deletions

Question 2

VSDs are seen in what syndromes?

Answer 2

#Down
#Edwards
#Patau

Question 3

Boot shaped heart - suspected diagnosis?

Egg on a string?

Pear Shaped?

Answer 3

Tetralogy of fallot

Transposition of great arteries

pericardial effusion

Question 4

Holosystolic murmurs?

Answer 4

#MR
#TR
#VSD

Question 5

Pt presents with single S2 and cyanotic? Suspected diagnosis? (In order to survive, baby also needs?)

Single S2 and grey (rather than blue)? Most accurate test?

Single S2 and recurrent respiratory infections? PE sign?

Answer 5

Transposition of great arteries
(VSD or ASD or PDA)

Hypoplastic Left heart syndrome; ECHO

Truncus Arteriosus; Bounding peripheral pulses

Question 6

Management of Transposition of great arteries?

Answer 6

Prostaglandin E1 to keep PDA open (do not give NSAIDs)

Question 7

Most common cyanotic condition in neonate? After neonatal period?

Answer 7

Transposition of great arteries

Tetralogy of fallot

Question 8

Hypoplastic Left heart Syndrome?

Answer 8

#LV hypoplasia
#Mitral atresia
#Aortic Valve lesions

Question 9

TAPVR with obstruction vs TAPVR with obstruction - presents when? Symptoms? CXR shows? Diagnosed with?

Answer 9

Early in life vs age 1-2

Respiratory distress/cyanosis vs right HR and tachypnea

Pulmonary Edema vs “Snowman”

ECHO for both

Question 10

Most common congenital heart lesion?

Treatment?

Answer 10

VSD

#Smaller lesions close by age 2
#Diuretics and digoxin

Question 11

If persistant and untreated, a VSD can lead to?

Answer 11

#CHF
#Endocarditis
#Pulmonary hypertension

Question 12

Fixed splitting suggests? Definitive test?

Answer 12

ASD; Cath or ECHO

Question 13

PDA is pathologic when?

Treatment?

Answer 13

Persists for over 24 hours

Indomethacin

Question 14

Sequela for PDA?

Answer 14

#Endocarditis
#Repiratory infections

Question 15

Tricuspid/pulmonary value murmurs radiate to?

Answer 15

back

Question 16

Globular-shaped heart with pulmonary edema?

Cardiomegaly with increased pulmonary markings?

Answer 16

Hypoplastic Left heart syndrome

Truncus Arteriosus

Question 17

Jug handle appearance on CXR - suspected diagnosis?

Answer 17

Primary pulmonary artery hypertension

Question 18

Child with hearing loss and syncope - think?

Answer 18

Long QT

Question 19

Most accurate test for coarctation of the aorta?

Answer 19

Cath