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Radio final > Osteoblastic dz > Flashcards

Osteoblastic dz Flashcards

1
Q

osteopetrosis aka

A

Albert-schonberg dz
marble bones
chalk bones

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2
Q

osteopetrosis is the result of what enzyme defiency

A

carbonic anhydrase

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3
Q

what function is defective in osteopetrosis?

A

osteoclast

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4
Q

you see —–apperance in osteopetrosis

A

bone within a bone

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5
Q

congenital type of osteopetrosis is

A

malignant

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6
Q

tarda type of osteopetrosis is

A

benign

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7
Q

Radiological feature of osteopetrosis

A

erlenmeyer flask deformity
Rugger jersey spine
sandwich vertebra

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8
Q

Erlenmeyer flask deformities

A
  • Gaucher’s Disease
  • Neimann-Pick Disease
  • Anemias
  • Fibrous Dysplasia
  • Metaphyseal Dysplasia (Pyle’s Disease)
  • Osteopetrosis
  • Heavy Metal Poisoning (plumbism)
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9
Q

intermittent normal and abnormal bone production results in

A

bone within a bone appearance

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10
Q

3 forms of osteopetrosis

A

tarda
congenita
marble bone

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11
Q

tarda happens in a

A

adulthood

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12
Q

congenita and marble bone happens in

A

infancy and childhood `

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13
Q

marbone causes

A

short stature
cerebral calcification
mental retardation

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14
Q

Osteopoikilosis aka

A

Osthepthia Condensans Dessminata

Spotty bone dz

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15
Q

clinical features of Osteopoikilosis

A

scleroderma

syndactyly

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16
Q

Osteopoikilosis is

A

transient

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17
Q

Osteopoikilosis

A

multiple clustered foci of radiopacity with uniform density

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18
Q

Osteopoikilosis is characterized by abnormality in what process?

A

enchondral bone maturation process that results in numerous round 2-10 mm bone islands that are symmetrically distributed within metaphysis and epiphyses of the long bones

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19
Q

Osteopoikilosis is characteristically clustred within

A

the epiphyeses around a joint

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20
Q

bone scan in Osteopoikilosis is

A

normal

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21
Q

compact bone island aka

A

Enostosis

22
Q

compact bone island

A

opaque areas of increased bone density

23
Q

Enostosis seen in

A

tubular and flat bones

24
Q

compact bone island radiographuc feature

A

brush border

1 cm or less

25
Q

plumbism

A

chronic form of lead poisoning

26
Q

most common heavy metal poisoning

A

lead poisoning

27
Q

radiographic changes occur when blood concentration of lead reaches

A

70-80 microgram /dl

28
Q

LEAD lines

A

linear transverse band at metaphysis

29
Q

lead ions are preferentially deposited at the

A

zone of provisional calcification

30
Q

lead ions inhibit

A

osteoclastic acitivity

31
Q

lead lines form due to

A
  1. radiopacity of lead itself ( little effect)

2. increase in ca deposition

32
Q

Radiographic features of plumbism

A

Erlenmeyer flask deformity
lead lines at the METAPHYSIS
delayed skeletal and dental development
soft tissue deposition of lead

33
Q

plumbism density

A

concentration of lead ingested

34
Q

plumbism width

A

Duration of intoxication

35
Q

plumbism number

`

A

of episodes of ingestion

36
Q

lead lines are more apt to be seen on

A

proximal fibula

distal ulna

37
Q

radiological features of Vitamin A intoxication

A

spalying/ cupping of metaphysis with enlargment of epiphysis
premature fusion of ossification centers/epiphyseal closure can occur
solid periosteal new bone forms at the shafts of the ulna and metacarpals resulting in cortical thickening

38
Q

hypervitaminosis D clinical fx

A

Nausea
Anorexia
Polyuria
polydypsia

39
Q

hypervitaminosis D radio

A

Extensive calcification in blood vessel walls, kidney and periarticular tissue

40
Q

Osteoblastic dz

A 
Melorheostosis of Leri
Osteopathia striata
Osteopetrosis
Osteiopoikilosis
Compact bone island 
Heavy metal poisoning
41
Q

Melorheostosis of Leri aka

A

Flowing Hyperostosis

like wax flowing down a lit candle

42
Q

Melorheostosis of Leri radio

A

wavy or streaked cortical thickening initially involving the end of bones and progressing towards the center

43
Q

Melorheostosis of Leri clinical

A

contracture of joint and limbs lead to deformities and LLD
widening of the fingers
fibrosis of the fingers

44
Q

an Erroneous diagnosis of ——is possibe with Melorheostosis of Leri

A

sarcoma -particualry when the soft tissue is unmineralized

45
Q

Osteopathia Straiata aka

A

Voorhoeve’s dz

46
Q

in Osteopathia Straiata you see

A

linear bands/ straition of dense bone measuring 2-3mm in thicnkess

47
Q

what areas are typically affected in Osteopathia Straiata

A

metaphysis and diaphysis o ftubular bones

48
Q

what is dignificant in lab values of Osteopathia Straiata dz

A

NOTHING - values are normal

49
Q

you see sunburst effect in what dz

A

Osteopathia Straiata

50
Q

when do you see sunburst effect

A

when ilium is affected

51
Q

Osteopathia Straiata is usally unilateral or bilateral

A

bilateral can be occasionaly unilateral

52
Q

Osteopathia Straiata is associated with what dz

A

Glotz synrome

Radio final (2 decks)

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