Other Congenital Conditions

Question 1

True or Flase.Radial glial fibers guides the neurons in their proper sites then forming the six layered cerebral cortex

Answer 1

True

Question 2

Absence of cerebral convolutions and a poorly formed Sylvian fissure due to faulty neuroblast migration

Answer 2

Lissencephaly or Agyria

Question 3

Presence of cysts or cavities in the brain from developmental defects or acquired lesions, including infarction of tissue

Answer 3

Porencephaly

Question 4

There is unilateral or bilateral clefts within the cerebral hemispheres due to abnormal morphogenesis

Answer 4

Schizencephaly

Question 5

The most common malformation of the posterior fossa and hindbrain

Answer 5

Chiari Malformation

Question 6

Abnormal development of the bones of the skull leading to a small posterior fossa with herniation of cerebellar tonsils

Answer 6

Chiari Malformation

Question 7

A posterior fossa abnormality with cystic dilatation of the fourth ventricle, hypoplasia of cerebellar vermis and hydrocephalus

Answer 7

Dandy-Walker Malformation

Question 8

Represents a diverse group of conditions that result from impaired circulation and absorbtion of CSF

Answer 8

Hydrocephalus

Question 9

Normal volume of CSF produced in a child

Answer 9

20ml/Hr

Question 10

Total CSF Volume in a Child

Answer 10

50ml

Question 11

Total CSF volume in an adult

Answer 11

150ml

Question 12

Type of hydrocephalus wherein there is a problem within the vebtricular system

Answer 12

Obstructive or non-communicating hydrocephalus

Question 13

A type of hydrocepgalus where in, it most commonly follows a subarachnoid hemorrhage

Answer 13

Non-obstructive or communicating hydrocephalus

Question 14

Most prominent sign of hydrocephalus

Answer 14

Accelerated enlargement of the head

Question 15

This manifestation of hydrocephalus is due to the impingement of the dilated suprapineal recess on the tectum

Answer 15

Setting-sun eye sign

Question 16

MacEwan’s Sign

Answer 16

Cracked pot sound upon percussion of the skull due to the separation of sutures

Question 17

Type 1 Chiari Malformation is associated with hydrocephalus in children

Answer 17

False

Question 18

Type 1 Chiari malformation is due to the displacement of the cerebellar tonsils into the cervical canal

Answer 18

True

Question 19

Type 2 Chiari Malformation has progressive hydrocepgalus and a myelomeningocoele

Answer 19

True

Question 20

It is an anomaly of the hindbrain due to failure of the pontine flexure and results in the elongation of the 4th ventricle and kinking of the brainstem with displacement of the inferior vermis,pons and medulla

Answer 20

Type II Chiari Malformation

Question 21

Megalencephaly is an anatomic disorder not associated with macrocephaly

Answer 21

False

Question 22

Prognosis of patients with hydrocephalys depends on the size of the cortical mantle

Answer 22

False. Depends on the cause of the dilated ventricle