Peads PATH Flashcards

1
Q

Hemimegalencephaly features

A
  • Large cerebral hemisphere & hemicranium
  • Same hemispehre: Polymicrogyria/lissencephaly/agyria/pachygyria
    grey matter heterotopia
  • Same hemisphere: Enlarged lateral ventricle
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2
Q

Hemimegalencephaly clinical

A

(90%) of patients present with focal and generalised infantile spasms

Despite the markedly enlarged head, there are no symptoms of raised intracranial pressure

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3
Q

Scimitar syndrome Triad

A
  • PAPVR
  • Hypoplastic right lung
  • Systemic arterial supply to right lower lobe** (get heart failure)
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4
Q

Dysgerminoma appearance ?

A
  • large, solid, and be bilateral
  • Hypercalcemia*
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