Peds Cardiology Flashcards
(170 cards)
1
Q
R–> L shunts
A
- tetraology of fallot
- transposition of great vessels
- tricuspid atresia
**Cyanotic lesions
2
Q
never clear an athlete for sports if you hear a murmur or anything about their history is suggestive of cardiac pathology or a FH of cardiac pathology. It is safest for them (and you) to refer them to a cardiologist for a complete evaluation. Additionally, if a caregiver or athlete reports that they had to see a cardiologist before “for that murmur” what should you do?
A
send them back to the cardiologist for eval and clearance
BC
HCM is often a condition that is evolving as the intraventricular septum thickens and the athlete could be more at risk in a later year than they were when they were younger.
3
Q
The AAP recommended in 2010 that providers use the ____ to screen athletes prior to clearance for sports
A
Pre-participation physical evaluation version 4 (PPE-4)
4
Q
when would you expect a PFO murmur and when should you call/refer to cardiology?
A
- It is not uncommon to hear a Grade 1-2 murmur in an infant less than 3 weeks old as the foramen ovale is still open.
- If the history and remaining exam are reassuring, it is acceptable to observe and bring the infant back weekly to recheck and see if there are any concerning symptoms/signs developing.
-If the murmur hasn’t resolved by 4 weeks of age, call the pediatric cardiologist for guidance
5
Q
when does cardiac output increase in peds?
A
- fevers
- anemia
- exercise
- hyperthyroidism
*causes murmurs to be louder
6
Q
Tx of tet spells
A
- shift pressure L–> R by increase SVR: knee to chest mechanism
- oxygen
- morphine decreases RR (vasodilator and decreases preload)
- NaHCO3
7
Q
describe the different grades of a mumur
A
Grade I- barely audible Grade II- soft, easily audible Grade III- loud, no thrill Grade IV- loud, with thrill Grade V- heard with edge of stethoscope, with thrill Grade VI- heard without stethoscope
*grade 1-3 are somewhat subjective
8
Q
Explain the management approach of pediatric patients with cardiac murmurs in the primary care setting
A
- All children with a 3/6 or greater murmur, or holosystolic murmur, need pediatric cardiology referral
- If history/exam is + in less than 2 m/o, get pediatric cardiology consult ASAP
- If older and stable, can screen with EKG, and refer if abnormal
*PCP do not interpret EKG
9
Q
What murmur?
- Heard best at 2nd ICS
- radiates to left axilla
A
Coarc- early presentation and late presentation
10
Q
treatment of VSD
A
- see back 3-4 weeks of age–> if murmur is still there get echo w/ cardiologist
VSD w/ CHF manifestations: meds and surgery
*need to be over 25lbs for anesthesia and surgery
11
Q
What murmur?
- Heard best in left and right infraclavicular areas
- Diminishes by turning the patient’s head
A
Venous Hum
12
Q
most murmurs occur when?
A
during early systole
13
Q
Sx of CHF
A
- fatigue
- diaphoresis with feeds
- fussiness.
- Tachypnea without significant dyspnea may be present.
Older children with heart failure may have:
- easy fatigability
- shortness of breath on exertion
- sometimes orthopnea.
- decreased exercise intolerance
14
Q
innocent cardiac mumurs
A
- peripheral pulmonary stenosis
- Still’s murmur
- Pulmonary Ejection Murmur
- Venous hum (only functional diastolic murmur)
15
Q
Infants with heart failure exhibit poor growth, with __ being more significantly affected than __ and __
A
with weight being more significantly affected than height and head circumference
16
Q
It is currently standard of practice to screen all neonates in the newborn nursery with ___ between 24 hours of age and discharge in order to detect critical congenital cardiac defects
A
pulse oximetry
17
Q
what sports are riskiest for a SCD/ cardiac event
A
basketball and football
*other sports list on UTD
18
Q
What murmur?
- Heard best at 2nd ICS
- radiates to whole back
A
pulmonary stenosis
19
Q
-cyanosis w.o resp. distress
A
-RH obstruction
ex. tricuspid atresia
pulm. stenosis
tetragology
20
Q
what is the purpose of the sports clearance
A
to perform a history and exam looking for evidence of cardiac pathology, neurologic risk factors and musculoskeletal disorders which may put them at risk for an adverse event during sports or put other players at risk
- From a cardiac standpoint, we are most concerned with the risk of Sudden Cardiac Death.
21
Q
what is transposition of the great artery/vessel (TGA/TGV)
A
- aorta comes off LV and feeds into lungs
- Pulm. artery comes off RV and goes to aorta
- VSD
- ASD
22
Q
Xray:
boot-shaped heart
A
tetrology of fallot
23
Q
CXR and EKG findings for pulmonary stenosis
A
CXR:
-normal or RVH
EKG:
-normal or RAD
24
Q
What murmur?
- Heard best at 2nd ICS
- Continuous during systole and diastole- machine like
A
PDA
25
Office work-up/referral tips
1) All children with a 3/6 or greater murmur, or holosystolic murmur, need pediatric cardiology referral--> likely underlying cardiac defect
2) If history/exam is + in les than 2m/o, get pediatric cardiology consult ASAP (ie. call)
3) If older and stable, can screen with EKG, refer if abnormal
**Don't order an echo in PCP
26
CXR and EKG findings of tetrology of fallot
CXR:
- RVH
- widen mediastinum
- "boot-shaped heart"
EKG:
-RAD
27
peripheral pulmonary stenosis is most common in what age group?
newborns-6 months
*may persist until age 15-18 months
28
what is a peripheral pulmonary stenosis murmur?
Starting in the right ventricle (R.V), blood travels into the pulmonary artery (P.A). As it reaches the bifurcation leading to each lung, the blood gets restricted down into these smaller outflow tracts, producing a murmur sound.
29
CXR and EKG findings of coarctation of the aorta late presentation
CXR:
- LVH
- rib notching (collateral circulation of intercostal arteries)
- scalloping of AA
EKG:
-LAD due to LVH
30
PE findings of coarctation of the aorta in the newborn
- check femoral pulses against brachial
- check pulse ox between upper and lower extremity ---3% difference
- murmur at 2nd ICS- radiates to L axilla
31
3 types of cardiomyopathy
1. dilated (most common)
2. hypertrophic
3. restrictive
32
the heart is unable to pump blood out efficiently and it backs up into systemic circulation
CHF
33
what are the Ghent nosology?
associated w/ Marfan's syndrome
includes:
1. hypermobile joints
2. long upper extremities compared to lower and
3. height much greater than genetic potential would predict.
34
What do tet spells cause
1. rapid cyanosis
2. acidotic w/ cyanosis
3. rapid increased PVR (from crying or feeding typically)
*in kids w/ tetrology of fallot
35
Marfan’s syndrome is more associated with __ due to ___ resulting in __
sudden cardiac death due to abnormal aortic roots resulting in aortic dissection
36
when does total anomalous venous return (TAVR) typically present
4-6 weeks of life
37
Despite our best attempts at screening, it is important to realize that only __% of patients who experienced SCD actually had a history suggestive of pathology
50%
38
mixing heart lesions
1. truncus
2. TAPVR
3. Hypoplastic L heart syndrome
39
AHA guidelines suggest antibiotic prophylaxis to protect agains bacterial endocarditis. They are needed for:
1. Prosthetic valve
2. Previous bacterial endocarditis
3. Congenital heart disease:
- Unrepaired cyanotic CHD
- Completely repaired but with prosthetic device, only in first 6 months after surgery
- Repaired CHD, but with residual defects
- Cardiac transplantation patients who develop cardiac valve abnormality
40
tx of ASD
1. can leave alone or cardiac cath --coil embolization procedure
41
Sx/PE of total anomalous venous return (TAVR)
1. cyanotic 1st 2 days of life when PDA starts to close
2. RVH and RAE
3. presents 4-6 weeks of life
4. increased fluid in lungs
5. tachypnea
6. CHF
7. coughing
8. poor weight gain/feeding
42
what heart defects cause RAD on EKG?
1. coarctation of aorta of newborn (late presentation has LAD)
2. hypoplastic L heart syndrome
3. ASD
4. pulmonary stenosis
5. tetrology of fallot
6. transposition of great artery/vessels (TGA/TSV)
7. total anomalous venous return (TAVR)
43
who is hypertrophic cardiomyopathy most common in?
males of african descent
44
a huge coarctation of the aorta of the newborn presents when
4-7 days of life as PDA closes
45
when does hypoplastic left heart syndrome present?
often detected pre-natally
-presents in 48 hrs of life (when PDA starts to close)
46
Cardiac defects associated w/ Down's syndrome (trisomy 21)
50% have ASD, VSD, or AVSD
47
describe the normal heart sounds
S1 –Closing of tricuspid and mitral valves
-Beginning of systole
S2 – Closing of aortic and pulmonary valves
-End of systole
Diastole- cardiac filling- no heart sound
48
Cardiac defects associated w/ Marfan's syndrome
90% have MVP, aortic root ectasia (resulting in AR), predisposed to aortic dissection
*should be ruled out in sport screenings!
49
CXR and EKG findings for VSD
CXR:
- increased pulmonary vascular markings (pulm. edema)
- LVH
EKG:
-LAD due to LVH
50
what procedures are indicated for SBE prophylaxis?
1. Dental procedures involving gingival tissues, oral mucosa, periapical region of teeth
* None needed for routine fillings
2. Procedures on respiratory tract, infected skin or musculoskeletal tissue
* No longer recommended for GI/GU procedures, including hysterectomy
51
what is the leading cause of SCD in children
hypertrophic cardiomyopathy
*accounts for 36% of deaths
52
how can you decrease cardiac output
move the patient from a supine position to a sitting or standing position. In that brief period of time, the positional change will decrease venous return to the heart which decreases stroke volume and therefore cardiac output. This is the reason we get dizzy if we get up too fast!!
53
SBE prophylaxis medications
1. Amoxicillin, Adults 2g (Peds 50mg/kg) 1 hour before
If PCN-allergic:
1. Clindamycin- Adults 600mg (Peds 20mg/kg ) 1 hour before
2. Cephalexin- Adults 2g (Peds 50mg/kg)
3. Azithromycin/Clarithromycin- Adults 500mg (Peds 15mg/kg)
54
Respiratory rate may be increased when there is a ___ shunt or ___
left-to-right
pulmonary venous congestion
55
___is the most common cyanotic congenital heart defect, representing about __% of all congenital heart defects
Tetralogy of Fallot
10%
56
what is a Still's murmur caused by?
blood traveling into the right outflow tract from the right ventricle. The sound is generated near the entrance to the pulmonary artery and travels along the pulmonary artery, therefore, it is heard along the left sternal border on the anterior chest.
57
what creates turbulent flow
Blood flow from high pressure area to low pressure across a defect
-Produces a varying frequency “whooshing” sound
58
many children with Down’s Syndrome have congenital cardiac defects that it is recommended that all neonates with Down’s Syndrome be evaluated by a cardiologist how soon?
in the first 4 weeks of life
59
CXR and EKG findings of ASD
CXR:
- increased pulmonary vascular markings
- normal RVH
EKG:
-normal or RAD
60
is split S1 or S2 more common in pediatrics?
split S2 (common w/ inspiration) aka physiological splitting
*split S1 is NOT common--> commonly confused with S4
61
describe the critical time periods for cardiac changes
48 hrs- change in oxygenation close--close PDA from pulmonary artery side first
4-7 days- PDA closes all the way across (anatomically closes)
4-6 weeks- pulmonary artery lining thins out and decrease in PVR and get good blood flow to lungs
62
what is a venous hum murmur caused by?
caused from blood that is returning to the heart via the subclavian and jugular veins creating noise in the right and left infraclavicular areas.
63
tx of PDA
1. indomethacin (NSAID)
| 2. ligature procedure to ligate off before 1 y/o--> reduces risk for Eisenmeger syndrome
64
describe the SVR and PVR of blood in-utero
high PVR- not much blood flow to lungs
| low SVR
65
how does CHF present in infants
-In adults, the fluid ends up in their feet and legs.
- In infants, it will travel to dependent areas such as their sacrum, but that may not be obvious with their chubby behinds!
* Look for it in their face, specifically around their eyes.
66
how do we tell if a murmur is pathologic?
- Our little test of moving them supine to sitting will not change the sound of the murmur if it is pathologic.
- Additionally, the constricted area will initiate the murmur sound and the sound will radiate in the same direction as the blood is flowing. We use this to help us determine the most likely cardiac defect.
*Will not diminish/resolve with cardiac output changes
67
PE/Sx of transposition of the great artery/vessel (TGA/TGV)
1. RVH
2. tachypnea
3. male
4. large babies
5. no murmur
"large blue baby boy"
68
when do VSD present
-4-6 weeks old when PVR decreases and they shunt L--> R = increased blood in lungs
69
what causes a Tet spell
* from crying or feeding= increased pulmonary shift, increase PVR (rapid)
- PVR increases rapidly so deoxygenated blood is shunted through VSD from RV to LV
70
significant differences in the chest x-rays of adult vs. children (less than 2y/o)
1. infants are born with a more prominent right ventricle due to fetal circulation- on CXR bc of rotation of the heart, most of the hearts silhouette is RV
(only 10% of the curve seen along the left side of the heard is LV)
2. hearts of young children look very large in their chest cavity on CXR and it is easy to think you are seeing an enlarged heart when you aren’t. It is normal for children less than 2 y/o to have normal heart silhouettes which are taking up 50% of their chest cavity on x-ray vs. the 1/3 rule used in adults
3. infants are born with a large thymus gland overlying their upper mediastinum and giving it an enlarged appearance
71
what is a pathologic murmur
when blood travels across a constricted area
72
what cardiomyopathy:
often idiopathic, but may be due to infection (echovirus or Coxsackie B virus) or be postinfectious, familial, or secondary to systemic disease or to cardiotoxic drugs.
dilated
73
what is the treatment for HCM?
1. Beta blockers- slow HR to allow better ventricular filling
2. prohibited from basketball and football/ intense physical activity
74
in pediatric EKGs, ___ is common until age 3
RV dominance
75
Most common causes of SCD
1. Hypertrophic cardiomyopathy
2. Arrythmias, specifically prolonged QT syndrome
3. Aortic stenosis
4. Anomalous coronary arteries
76
what are some genetic syndromes that are associated w/ cardiac defects?
1. Down's syndrome (trisomy 21)
2. Turners syndrome
3. Edwards syndrome (trisomy 18)
4. Marfans syndrome
77
What murmur?
- Heard best at 4th ICS
- Pansystolic
- no radiation
VSD
*only one heard at 4th ICS
78
how does LVH present on a pediatric EKG
1. Tall R waves in Lead II, aVF, V5, V6
79
____ screens for children with significant shunting of blood into the right side of their heart down into their lungs
Observing respiratory rate
80
describe a Still's murmur
- best heard between apex and LSB
- distinctive higher-pitched sound that is sometimes described as musical or vibratory (ie. bass guitar string vibrating)
- diminished/resolved murmur w/ moving from supine to sitting or turning head
- continous
81
tx of tetrology of fallot
1. relieve pulmonary artery valve via surgery (decreases risk of CHF)
2. meds
3. full VSD surgery closure by age 1
82
how is pulse oximetry obtained in neonate?
- obtained from right hand and either foot and is consider normal if over 95% and not more than 3% difference between upper/lower extremity.
* At our altitude, a slightly lower pulse ox may be used as the cutoff.
83
what is the only innocent diastolic murmur
venous hum
*diastolic murmurs are always pathologic as the heart is supposed to only be filling with blood not pumping it anywhere
84
why do peds w/ heard disease sometimes present w/ cough
- If their cardiac defect shunts blood into their lungs, they will have tachypnea and for that reason, I have “radar” for neonates with a complaint of cough.
- Infants have a high threshold for reflexive coughing until they are about 3 months old, so they need significant lung pathology such as bronchiolitis or pertussis before they will cough, not just a mild URI.
85
how can you tell if a patient has an innocent murmur?
(most patients are noted to have a cardiac murmur when they are seated): lie the patient supine and locate the place on their chest where the murmur is most audible, with your stethoscope still in place, move them to a seated position. If the murmur diminishes or resolves completely, the child most likely has an innocent murmur.
*Be sure to collect an appropriate history, which I will review shortly, to be sure of your diagnosis.
86
Sx/PE of PDA
1. murmur- 2nd ICS, across diastole and systole/continous, machine-like
2. tachypnea
3. cough
4. increased fluid in lungs
5. LAE and LVH
6. widen pulse pressure
87
document murmurs by:
grade
location
radiation
88
what is the most common congenital heart defect?
VSD
89
how does RV dominance present on a pediatric EKG
1. Dominant S in Lead I
| 2. Dominant R in lead III
90
how does hypertrophic cardiomyopathy lead to SCD/syncope?
- the intraventricular septum becomes thickened causing the LV outflow tract to be narrowed.
- These patients depend on a large end-diastolic ventricular volume to stretch the outflow tract wide enough to maintain good cardiac output.
- During exercise, diastolic fill time is shortened due to increased heart rate. For patients with HCM, this doesn’t allow the necessary stretching of their LV outflow tract and they have decreased cardiac output at a time when exercise is demanding more. They will have near syncopal or syncopal episodes and may have SCD with their 1st episode of syncope
91
failure of development of the mitral or aortic valve or the aortic arch.
hypoplastic left heart syndrome
92
why is there a split S2 with inspiration?
Physiologically, the act of inspiration increases the amount of right ventricular filling. Because the right ventricle now has more blood to eject, the valve remains open just a bit longer after the aortic valve has closed, leading to a split S2 with inspiration
*This is an important concept to remember when we talk about some of the heart defects which result in overfilling of the right side of the heart
93
tx of coarctation of the aorta of the newborn
1. fluid bolus (increase BP)
2. give oxygen
3. labs
4. give prostaglandins E1 to open PDA
5. septic workup
94
Xray:
- rib notching caused by the dilated intercostal arteries
- prominent aortic knob w/ narrowing of aorta and then dilated descending aorta
coarctation of the aorta
95
CXR and EKG findings of hypoplastic L heart syndrome
CXR:
- RVH/cardiomegaly
- increased pulmonary vascular markings
EKG:
-RAD due to RVH
96
what causes an S4
- Indicates a hypertrophic, stiff left ventricle
| - Produces a gallop rhythm
97
ductal dependent heart lesions
1. Coarctation of the aorta of the newborn
2. hypoplastic L heart syndrome
3. critical aortic stenosis
4. pulmonary atresia
5. severe tetralogy of Fallot
6. tricuspid atresia
98
describe what a holosystolic murmur sounds like
heard where S1 and S2 should be but often obscure the sounds of the valve closures
99
Cardiac defects associated w/ Edward's syndrome (trisomy 18)
99% have VSD
100
Patients with cardiac syncope will usually have a history of:
- sudden syncope, not the vaso-vagal syncope of feeling lightheaded, vision fading, nausea and then fainting.
* These patients often hurt themselves because their syncope comes completely without warning and they are unable to protect themselves the way a person with a vaso-vagal episode will by sitting down, trying to lie down, etc.
101
sx hypoperfusion
```
LH obstruction
ex:
-TAPVR
-Aortic stenosis
-HLH
```
102
-Cyanosis with respiratory distress
TGA/TGV
103
All would-be athletes, starting in __ , are required to have a “sports” physical performed and be cleared for play.
middle school
104
what cardiomyopathy:
| rare; they may be idiopathic or associated with systemic disease
restrictive
105
CXR and EKG findings of PDA
CXR:
- increased pulmonary vascular markings
- normal or LVH
EKG:
-LAD
106
What is Eisenmenger Syndrome
- inside lining of lungs change to become more resistant to BF--> leads to PHTN (irreversible)
- R--> L shunt (cyanotic lesion)
107
treatment of hypoplastic L heart syndrome
- give PGE1 from birth
- surgery 1st week of life and 2 more later in life (last around 4y/o)
- transplant
108
what causes an S3
due to large atrial volume, delays the closure of mitral or tricuspid valve
109
how should you check pulses in a neonate
- Comparing amplitude and timing of the brachial pulse to the femoral pulse screens for coarctation of the aorta, as does checking the blood pressure specifically from the right arm against either thigh.
* femoral pulses are weaker and delayed compared with the right radial pulse
110
Acyanotic heart lesions
1. PDA
2. VSD
3. critical aortic stenosis
4. Coarctation of the aorta
5. hypoplastic L heart syndrome
6. ASD
111
how does RVH present on a pediatric EKG
1. deep S waves in V6
| 2. tall R waves in V1
112
Sx/PE of pulmonary stenosis
1. RVH and RA enlargment
2. narrowed pulmonary valves
3. murmur 2nd ICS that radiates to BACK (the smaller the louder)
4. tachypnea (presents before liver congestion)
5. liver congestion (long term complication)
6. If high enough pressure in RA, can cause FO to stay open
113
characteristics of innocent cardiac murmurs
1. Produces a musical, single frequency sound
2. Louder with increased cardiac output
3. Decreased cardiac output= decreased murmur sound
*laminar flow
114
What murmur?
- Holosystolic murmur 2 and 4 ICS
- radiates to chest and back
Tetrology of fallot
| - Depends on which is the major defect
115
Sx/PE of VSD
1. tachycardia
2. increased RR (increased blood in lungs)
3. ashen color (esp. around lips)
4. coughing
5. poor feeding w/ sweating
6. fussy
7. fluid in lungs
8. murmur at 4th ICS-pansystolic
9. enlarged LV
116
sx/PE of coarctation of the aorta late presentation
1. increase BP in right arm
2. HA due to increased blood flow in carotids
3. murmur- 2nd ICS that radiates to left axilla
4. enlarged LV
5. leg discomfort
6. epistaxis
7. decreased femoral pulses compared to right radial pulse
117
CXR and EKG findings for coarctation of the aorta of the newborn
CXR:
- Enlarged heart/cardiomegaly
- increased pulmonary vascular markings
EKG:
-RAD due to RVH
118
presentation of tetrology of fallot
1. murmur- 4th ICS and 2-4th ICS that radiates to BACK
| 2. RVH
119
what is total anomalous venous return (TAVR)
- PV inserts in odd places like superior vena cava
| - PFO
120
where is a peripheral pulmonary stenosis murmur best heard?
- best heard in 2 ICS and axilla
- radiates to the back
-systolic ejection, harsh
121
sx of coarctation of the aorta of the newborn
1. poor perfusion
2. poor feeding
3. Shocky lookings-- bc can't breath
4. lethargic
5. normal femoral pulses
122
stenotic heart lesions
1. aortic stenosis
2. pulmonary stenosis
3. coarctation of the aorta
123
most common cause of death from cardiac defects in the first month of life
hypoplastic left heart syndrome
124
What murmur?
- Best heard in axilla bilaterally
- Radiates to back
- Will not hear anything or very low sound when auscultating the anterior chest
Peripheral pulmonary stenosis
125
what direction is blood shunted with VSD?
L--> R because RVpressure is less than LV pressure
126
what should you do if you are concerned about a murmur in an older child and aren’t sure of your positional change exam, but their history seems benign?
screen them w/ EKG:
- if it is abnormal: refer to cardiology
- if it is normal: observe
127
The focus of history taking around the risk of SCD is:
1. looking for syncopal or near-syncopal episodes
| 2. chest pain which occur with exercise.
128
tx of total anomalous venous return (TAVR)
surgery
129
the PPE-4 history and exam focuses on:
- The history focuses on cardiorespiratory diseases, previous orthopedic injuries, current skin infections, history of neurologic disorders, including head trauma, and family history of cardiac death.
- The exam focuses on skin, MSK, cardiac and neurologic.
130
Sx/PE of ASD
1. RVH
2. migraine HA
3. TIA
4. murmur- 2nd ICS w/ widely split fixed S2
131
why is anomalous coronary arteries dangerous?
Imagine a coronary artery coming off the aorta down near the valve and between the aorta and pulmonary artery. Obviously with exercise, this coronary artery would get compressed between the two large outflow tracts. A patient with this will have a syncopal episode and potentially SCD.
132
what is tetrology of fallot
1. pulmonary stenosis
2. VSD
3. RVH
4. over-riding aorta (PA is shifted ofter and pushes against the aorta)
*cyanotic heart lesion
133
PE of hypoplastic L heart syndrome
- NO murmur
| - RVH
134
What murmur?
- Heard between apex and LSB on the anterior chest
- Vibratory/musical, higher pitched sound (bass guitar string vibrating)
Still's murmur
135
cause of S4
due to a stiffened left ventricle which is unable to eject the final amount of blood through the aortic valve
*not common in pediatrics
136
what are the most common innocent murmur of childhood.
Still's murmur
heard in 2y/o+ (3-6yrs*)
137
abnormal heart sounds
1. click- most common
2. S3
3. S4
138
describe a pulmonary ejection murmur
- heard typically in slightly older kids (3+)
- LUSB
- Systolic ejection
- -diminished/resolved murmur w/ moving from supine to sitting (innocent)
139
What CHD do not have a murmur associated w/ them
- HLHS
- TAPVR
- TGA
140
if you hear a blurred or “whishing” sound across S1, you would call that what type of murmur?
-where that sound across S2 would be called ___
an early systolic murmur
a late systolic murmur
141
when do you hear a "click"
common w/ stenotic valves
*"snap" during valve closure
142
what cardiac disease have a risk of Eisenmenger Syndrome
1. VSD
| 2. PDA
143
why do children have innocent/functional murmurs
- due to their small cardiac size and, therefore, the small size of their cardiac outflow tracts, specifically the pulmonary artery, but also the left ventricular outflow tract.
- As blood travels from a larger “pipe” into a smaller one, it creates noise. Therefore, 100% of children will have an innocent murmur if their hearts are auscultated frequently enough. When cardiac output increases, the amount of blood squeezing into the “small pipe” from the big one will produce a murmur sound
144
what cardiomyopathy:
| usually familial with autosomal dominant inheritance, but may occur sporadically
Hypertrophic
145
describe the split heart sounds
Split S1: MV closing just before TV
Split S2: AV closing just before PV
*Physiologic S2 splitting is common with inspiration
146
Comparing pulse oximetry between the___ and ___ may allow diagnosis of a ___ lesion in which desaturated blood flows right to left across a PDA to perfuse the lower body
right arm
lower extremity
ductal dependent lesion
147
L--> R shunts
1. PDA
2. VSD
3. ASD
* *Acyanotic lesions
- results in increased pulmonary blood flow
148
CXR and EKG findings of transposition of the great artery/vessel (TGA/TGV)
CXR:
- RVH
- narrowing mediastinum-- "egg of a string"
EKG:
-RAD
149
effects of coarctation of the aorta on the heart
enlarged LA, RV, and LV
150
What murmur?
- Heard best at 2nd ICS
- Widely fixed splitting S2
- no radiation
ASD
151
Cardiac defects associated w/ Turner's syndrome
20-40% have coarctation of the aorta
152
Describe the appropriate historical questions to elicit in evaluating a pediatric patient for congenital heart disease
1. Feeding difficulties**- feed only for short period
2. Sweating (diaphoresis) with feeds-- cannot tolerate breastfeeding
3. 1st degree relatives with cardiac problems
4. Poor growth/weight gain
5. Delayed gross motor skills-- due to exercise intolerance
6. Rapid breathing, ??neonate with cough-- if CHD shunts blood to lungs causes tachypnea
7. Gray cyanosis- (w/ feeding)
8. Cyanosis with exercise, exercise intolerance
153
what heart defects cause LAD on EKG?
1. coarctation of aorta late presentation (newborn has RAD)
2. VSD
3. PDA
154
treatment of coarctation of the aorta early presentation
- balloon angioplasty to open PDA
| - surgical repair
155
tx of pulmonary stenosis
balloon angioplasty
156
why is prolonged QT syndrome dangerous?
QT interval becomes prolonged resulting in ventricular arrythmia and syncope, followed by torsades de pointes (a form of ventricular tachycardia) which is usually followed by ventricular fibrillation and death
157
the cardiac exam includes what 7 essential elements
1. Color- Consider Pulse Oximetry
2. Respiratory effort/rate
3. Auscultate
4. Palpate chest for thrills, heaves
5. Compare brachial/femoral pulses
6. Check blood pressure-right arm
7. Clubbing of fingers/toes (chronic low O2?)
8. Edema (CHF?)
158
tx of transposition of the great artery/vessel (TGA/TGV)
surgery 1st week of life
| -anastomosis and reposition vessels
159
how does the foramen ovale close?
closes w/ increased SVR from umbilical cord clamping
160
What murmur?
- Sound generated along the pulmonary valves (valves themselves though are not abnormal)
- LUSB anteriorly
- Systolic ejection murmur
Pulmonary Ejection murmur
*Sometimes cannot differentiate well from Still’s murmur, just be able to differentiate if it is innocent murmur vs a pathologic cause
161
human eyes cannot detect skin color changes until oxygen saturation is ____ and even then the child will not be “blue” just somewhat ashen or gray especially around the lips/mouth.
in the low 80’s,
**It is very easy to miss this on exam unless you are specifically looking for it. In older children, the caregiver may report grayish lips with exercise or inability to tolerate exercise that their peers can do.
162
How to get to a proper cardiac dx in peds
Know:
1. physiology of cardiac lesion
2. physics of fluid flow and sound travel
3. reasoning
163
Only __% of the population has congenital cardiac defects, so many of the murmurs you hear in children will likely be innocent.
1%
BUT! not all congenital cardiac defects have murmurs associated with them. In fact, some of the more life-threatening cardiac defects do not
164
what is hypoplastic L heart syndrome
*left side of heart is underdeveloped
- small LV, MV atresia
- causes RV enlargement
165
describe a venous hum murmur
- diastolic
- right and left infraclavicular areas
- age 2
- diminishes by turning pts head
166
5 T's of cyanotic heart lesions
1. Tetrology of Fallot
2. Transposition of the Great Vessels (TGA)
3. Tricupsid Atresia
4. Truncus Arteriosus
5. Total Anomalous Pulmonary Venous Connection (TAPVC)
6. pulmonary atresia
7. hypoplastic L heart syndrome
*caused by decreased pulmonary blood flow and R--> L shungs where blood is mixing
167
which valve closes before the other
left side valves close first (bc left side is more buff than right)
168
most common cyanotic lesion to present in the newborn period
TGA/TGV
169
Xray:
| egg-on-a-strin gappearance
transposition of great vessels
170
CXR and EKG findings of total anomalous venous return (TAVR)
CXR:
- RVH and RAH--> cardiomegaly
- "Snowman shaped heart"
EKG:
-RAD
