peds gi Flashcards
(84 cards)
cleft lip
congenital fissure in the upper lip
cleft palate
congenital fissure in either the soft palate alone or both hard and soft palates
most common craniofacial malformation
cleft lip with or without cleft palate
cleft lip: pathophysiology
occurs at 6 weeks gestation
- maxillary process fails to merge with the medial nasal elevation on one or both sides
cleft lip: when does it occur?
6 weeks gestation
cleft palate: pathophysiology
occurs 7 to 12 weeks gestation
- lateral palatine processes fail to meet and fuse with each other, the primary palate, or nasal septum
cleft palate: when does it occur?
7 to 12 weeks gestation
cleft lip/palate: etiology
- multifactorial mode of inheritance
- maternal nutrition: FOLIC ACID
- maternal medication 1st trimester
- occurrence of fever, flu 1st trimester
- maternal prenatal cigarette smoking
cleft lip/palate: clinical manifestations
generally evident at birth, if not:
- feeding difficulties
- chronic upper airway congestion/infection
- 7 to 14% have other anomalies!
cleft lip/palate: therapeutic management
- team approach!
- surgical repair PRIORITY ideally before child speaks
cleft lip @ 10 wks or 10 lbs
cleft palate @ 6 months
cleft lip: when should surgical repair be done?
10 weeks or 10 pounds
cleft palate: when should surgical repair be done?
6 months
nutrition considerations for babies with cl/cp
- inability to suck = possible undernutrition
- elevate head during feeds
- special nipples
- gentle, steady pressure on bottle base
- frequent burping
- daily weight: nutritional eval, fluid volume status
- nipple way back in oral cavity
- breck feeder
breck feeder
syringe with feeding tube expansion appropriate for feeding babies with difficulty feeding due to cl/cp
significance of otitis media and cleft palate
improper middle ear drainage due to inefficient eustachian tube function s/t cp = increased middle ear pressure
- recurrent otitis media
- can lead to HEARING IMPAIRMENT
tracheoesophageal fistula aka
esophageal atresia
tef/esophageal atresia
aka tracheoesophageal fistula (tef)
failure of trachea to differentiate and separate from esophagus into separate, distinct structures
failure of esophagus to develop as continuous passage
tef/esophageal atresia % affected with associated anomalies
30-40%
tef/esophageal atresia: clinical manifestations
- inability to swallow saliva, increase in drooling, frothy saliva in mouth/nose
- gastric tube/suction catheter can’t be passed
- choking, cyanosis with feedings; cyanotic or apneic s/t aspiration
- recurrent pneumonia (typically will be caught before this)
- triad: excessive secretions, reflux, respiratory distress
tef/esophageal atresia: hallmark sx triad
excessive secretions + reflux + respiratory distress
tef/esophageal atresia: diagnosis
diagnose before feeding by catching clinical s/s
xray after passing radiopaque catheter into esophagus
tef/esophageal atresia: classic presentation
significant choking, cyanosis with feeds
tef/esophageal atresia: why frequent suctioning?
keeps blind pouch empty; secretions develop even though it is a pouch!
tef/esophageal atresia: gastric decompression
catheter in blind pouch to low wall suction, g tube inserted and open to drain