POIKILOCYTOSIS Flashcards

DESCRIPTION, OTHER NAMES, DISEASE ASSOCIATIONS (41 cards)

1
Q

amost spherical in shape; lacks the central pallor

A

SPHEROCYTE

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2
Q

elongated RBCs with a SLIT-LIKE CENTRAL PALLOR and may be considered as an artifact

A

STOMATOCYTE

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3
Q

RBCs with IRREGULARLY SPICULATED SURFACE

A

ACANTHOCYTE

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4
Q

RBCs with REGULARLY SPICULATED SURFACE

A

BURR CELL

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5
Q

oval-shaped RBCs

A

OVALOCYTE

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6
Q

elliptical (cigar-shaped) RBC

A

ELLIPTOCYTE

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7
Q

pear-shaped or TEARDROP-SHAPED RBCs

A

DACRYOCYTE

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8
Q

fragmented RBCs

A

SCHISTOCYTE

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9
Q

SICKLE- or crescent-shaped RBCs

A

DREPANOCYTE

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10
Q

RBCs which show a CENTRALLY STAINED AREA WITH A THIN OUTER RIM OF HEMOGLOBIN

A

TARGET CELL

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11
Q

HELMET-SHAPED schistocyte that may appear in MAHA

A

HELMET CELL

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12
Q

demonstrate a semicircular defect in their edge (resmbles a BITE MARK)

A

BITE CELL

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13
Q

FOLDED RBCs

A

BISCUIT CELL

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14
Q

“BIPOLAR” or CENTRAL DISTRIBUTION of hemoglobin

A

BRONZE ELLIPTOCYTE

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15
Q

as large as leukocytes; pale-pink staining ghost of the red cell membrane

A

SEMILUNAR BODY

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16
Q

other term for BITE CELL

A

DEGMACYTE

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17
Q

other terms for TARGET CELL

A
  1. LEPTOCYTE
  2. CODOCYTE
  3. PLATYCYTE
  4. GREEK HELMET CELL
  5. MEXICAN HAT CELL
  6. BULL’S EYE CELL
18
Q

other term for SCHISTOCYTE

19
Q

other term for TEARDROP CELL

20
Q

other term for BURR CELL

21
Q

other terms for ACANTHOCYTE

A
  1. THORN CELL
  2. SPUR CELL
22
Q

other term for STOMATOCYTE

23
Q

DSE ASSOC:

associated with ABETALIPOPROTEINEMIA, McLeod SYNDROME, PK DEFICIENCY

24
Q

DISEASE ASSOC:

associated with UREMIA, PK DEFICIENCY

A

ECHINOCYTE (BURR CELL)

25
# DISEASE ASSOC: associated with **SOUTHEAST ASIAN OVALOCYTOSIS**
OVALOCYTE
26
# DSE ASSOC: associated with **THALASSEMIA, HEREDITARY ELLIPTOCYTOSIS**
ELLIPTOCYTE
27
# DISEASE ASSOC: associated with **PRIMARY MYELOFIBROSIS, MEGALOBLASTIC ANEMIA, THALASSEMIA**
DACRYOCYTE
28
# DSE ASSOC: associated with **MAHA (TTP, HELLP, HUS, DIC), UREMIA**
SCHISTOCYTE
29
# DSE ASSOC: associated with **SICKLE CELL ANEMIA, Hb SC DISEASE**
DREPANOCYTE
30
# DISEASE ASSOC: associated with **THALASSEMIA, LCAT DEFICIENCY**
TARGET CELL
31
# DISEASE ASSOC: associated with **HEREDITARY SPHEROCYTOSIS, AIHA, BURNS, ABO HDN**
SPHEROCYTE
32
# DSE ASSOC: associated with **Rh DEFICIENCY SYNDROME, ELECTROLYTE IMBALANCE, DEHYDRATED HEREDITARY XEROCYTOSIS**
STOMATOCYTE | BIG CLUE: **"RHED TOMATO"** - Sir Henry
33
# DSE ASSOC: associated with **G6PD DEFICIENCY**
BITE CELL
34
# DSE ASSOC: associated with **Hb SC DISEASE**
BISCUIT CELL
35
# DSE ASSOC: associated with **SICKLE CELL ANEMIA** *(aside from Drepanocyte)*
BRONZE ELLIPTOCYTE
36
# DISEASE ASSOC: associated with **OVERT HEMOLYSIS**
SEMILUNAR BODY
37
**ABETALIPOPROTEINEMIA** is aka
**BASSEN-KORNZWEIG SYNDROME**
38
**MOST COMMON FORM OF STOMATOCYTOSIS**
DEHYDRATED HEREDITARY STOMATOCYTOSIS
39
characterized by **DEFECTIVE APO B SYNTHESIS**; VLDL, LDL, and CHYLOMICRON are NOT FOUND IN PLASMA
ABETALIPOPROTEINEMIA
40
# FORM OF DREPANOCYTE: crescent-shaped with **LONG PROJECTIONS**; **WHEN REOXYGENATED, *THEY FRAGMENT*!!!**
IRREVERSIBLE SICKLE CELLS
41
# FORM OF DREPANOCYTE: have **LESS PRONOUNCED PROJECTIONS; WHEN REOXYGENATED, THEY *RETURN TO THE ORIGINAL!!!!***
OAT-SHAPED CELLS