Quiz

Question 1

DO mitochondrial myopathies have acquired symptoms

Answer 1

YES! Ptosis, EOMS, are acquired

Question 2

What gaze may be unaffected in mitochondrial myopathies

Answer 2

Downgaze

Question 3

Kearns Sayer key symptoms

Answer 3

Night blindness, short stature. Dementia, DM. Heart. Pigment retinopathy.

Question 4

Kearns Sayer tx

Answer 4

low carbs, high lipid, B1 and B7 (biotins) COQ10,

Question 5

What to avoid in Kearns sayer

Answer 5

valproate and phenobarbital. Seizure meds.

Question 6

MELAS

Answer 6

have lactic acidosis, have encephalopathy with developmental delay seizures and dementia. Opthamologples, optic atrophy. Pig retinopathy.

Question 7

MNGIE

Answer 7

GI problems and leukoencephaly

Question 8

SANDO syndrome

Answer 8

Sensory, Ataxic neuropahty, dysarthria, opthamoplegia. Furrowed tongue.

Question 9

Leigh Syndrome

Answer 9

Subacute necrotizing enechalomyelopathy. Atonia. Occurs in children. Strabismus, pig retinopathy, optic atrophy, ptosis, nystagmus, skew.

Question 10

TX for eight syndrome

Answer 10

Decreased carbs, increased lipids, B1, COQ10. Sodium citrate for lacticacidosis

Question 11

Mito myopathies with pig retinopathies

Answer 11

Kay’s sayer (night blindness), Minas, Leight.

Question 12

Myotonic Dystrophy

Answer 12

Look aged, Christmas tree cataract. Mitotic pupils. Retinal dystrophy with sclera showing.

Question 13

TX for myotonic dystrophy

Answer 13

phenotonin for myotonia. Cataract, ptosis, prism for diplopia

Question 14

Oculopharyngeal dystrophy

Answer 14

Hispanic. Dysphagia, Astrologist posture. Ptosis is bilateral and complete and EO is mild if present.

Question 15

DX of oculopharyngeal dystrophy

Answer 15

High creatine phosophkinase. Vacuoles in muscle.

Question 16

Grave’s Disease

Answer 16

Fibrotic. IM SLO. Tendons will be spared.

Question 17

Myositis

Answer 17

IIOP (idiopathic inflammatory orbital psudotumor). Inflammation where tendons are not spared. Treat with steroids. Have painful acute onset of diplopia, conj chemises with edema or proptosis.

Question 18

Brown SO tendon sheath

Answer 18

difficulty for adduction and up gaze. IF acquired treat with corticosteroids.

Question 19

Eye questions for como

Answer 19

1. misalignment 2. conjugate gaze deviation 3. spontaneous eye movements 4. doll’s eye?

Question 20

horizontal deviation with hemiparesis

Answer 20

if hemispheric lesion it will be away from the hemiparesis. If thalamus or pons it will be toward the hemiparesis.

Question 21

Caloric testing

Answer 21

COWS. The fast phase. Cold=away. Warm=same.

Question 22

Lesion in horizontal canal with testing

Answer 22

Fast will be contralesional

Question 23

Atypical bobbing

Answer 23

Horizontal movements too

Question 24

Reverse bobbing

Answer 24

Quick phase up

Question 25

Inverse bobbing

Answer 25

very slow downward

Question 26

Converse bobbing

Answer 26

very slow upward

Question 27

Depressants HGN, VGN, pupils, body temperature, pulse, convergence, lids, light

Answer 27

Alcohol, barbiturates, soma (qualludes). HGN yes, VGN with big amounts, pupils (normal except with soma), decreased pulse (except with qualludes and etch), normal temperature, convergence decreased, ptosis. slow reaction to light. flaccid muscle tone.

Question 28

Stimulants

Answer 28

Meth and cocaine. Only dilate eyes. Slow reaction to light. Have increase temperature, pulse rate, blood pressure. Rigid muscle tone.

Question 29

Number one drug in oregon

Answer 29

Meth

Question 30

Prescription Stimulants

Answer 30

Ritaline, Adderal, Dexedrine, Atomoxetrine (non prescription but serious SE)

Question 31

HGN

Answer 31

Depressants, Inhalents, PCP

Question 32

VGN

Answer 32

Depressants, Inhalts, PCP

Question 33

Lack of convergence

Answer 33

Cannabis, Inhallents, Depressents, PCP

Question 34

Dilation of eyes

Answer 34

Cannabis, stimulants, hallucinogens.

Question 35

Constriction of eyes

Answer 35

narcotics

Question 36

Slow light response

Answer 36

Stimulants, Narcotics, inhalents, Depresessents.

Question 37

Normal light response

Answer 37

PCP, hallucigenics, Cannabis.

Question 38

Myopathies and pig retinopathy

Answer 38

kauert sauer, MELAS,