Sarcoidosis Flashcards Preview

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Flashcards in Sarcoidosis Deck (9)
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1
Q

What is sarcoidosis?

A

Multisystem granulomatous disease of unknown cause

2
Q

Symptoms of sarcoidosis?

A

Dry cough
Progressive dyspnoea
Reduced exercise tolerance
Chest pain

3
Q

Features (different to symptoms) of sarcoidosis?

A

Erythema nodosum (painful/tender, red/purple, lesions on the shins)
Lupus pernio (sarcoidosis lesions on the skin)
Arthralgia
Lymphadenopathy

4
Q

What special blood result might be associated with sarcoidosis and why?

A

Hypercalcaemia

- sarcoid tissue can activate vitamin D and cause hypercalcaemia

5
Q

What investigation results does sarcoidosis show?

A

Elevated calcium
Elevated ACE (angiotensin-converting enzyme)
Tuberculin test is negative
Biopsy + histology show non-caseating granulomas

6
Q

How is sarcoidosis diagnosed?

A

Biopsy + histology showing non-caseating granulomas

7
Q

What test USED to be done for sarcoidosis?

A

Kveim-Siltzbach test

- not done anymore

8
Q

How is sarcoidosis staged and what are the stages?

A

CXR findings

  • Stage 1 - bilateral hilar lymphadenopathy
  • Stage 2 - bilateral hilar lymphadenopathy + lung involvement
  • Stage 3 - lung involvement only
  • Stage 4 - lung fibrosis
9
Q

How is sarcoidosis treated?

A

Steroids + immunosuppressants