Urine Odor

Question 1

Normal (due to presence of volatile acids from food)

Answer 1

Aromatic, faintly

Question 2

Acute tubular necrosis (acute renal failure)

Answer 2

Odorless

Question 3

UTI (ex. Proteus vulgaris), old urine

Answer 3

Foul, ammoniacal

Question 4

Ketones (Diabetes Mellitus, starvation, vomiting)

Answer 4

Fruity, sweet

Question 5

Maple syrup urine disease (MSUD)

Answer 5

Caramelized sugar,
Maple syrup urine disease (MSUD)
curry, maple syrup

Question 6

Phenylketonuria (PKU)

Answer 6

Mousy, musty, barny

Question 7

Tyrosinemia

Answer 7

Rancid butter

Question 8

Isovaleric acidemia, glutaric acidemia

Answer 8

Sweaty feet, acrid

Question 9

Phenol-containing medications

Answer 9

Menthol-like

Question 10

Methionine malabsorption (Oasthouse syndrome)

Answer 10

Cabbage, hops

Question 11

Specimen adulteration or container contamination

Answer 11

Bleach

Question 12

Cysteine disorder

Answer 12

Sulfur

Question 13

Trimethylaminuria

Answer 13

Rotting fish; galunggong

Question 14

Ingestion of onions, garlic, & asparagus
(methylmercaptan), UTI (Brunzel)

Answer 14

Pungent, fetid

Question 15

Hawkinsinuria

Answer 15

Swimming pool

Question 16

3-hydroxy-3-methylglutaric aciduria

Answer 16

Cat urine

Question 17

Multiple carboxylase deficiency

Answer 17

Tomcat urine