UROGENITAL SYSTEM ABNORMALIES Flashcards
(35 cards)
most common renal anomaly is
the most common renal anomaly is the duplex collecting system, also referred to as a duplicated or double collecting system. In this variant, the kidney is composed of two separate collecting duplex collecting system,
divided into what is termed an upper pole moiety and a lower pole moiety.
urachus
the bladder is continuous with the allantois, although eventually this channel closes and develops into a fibrous cord referred to as the. urachus
VACTERL ASSOCIATION
vertebral anomalies, anal atresia, cardiac anomalies, tracheoesophageal fistula or esophageal atresia, renal anomalies, and limb anomalies
most frequent cause of oligohydramnios.
SOUND OFF
Renal abnormalities are the most frequent cause of oligohydramnios. Therefore, if oligohydramnios is discovered, a thorough analysis of the fetal urinary tract is warranted.
if a normal amount of fluid is noted during a sonogram, one can assume that there is
if a normal amount of fluid is noted during a sonogram, one can assume that there is at least one functioning fetal kidney present.
lying down sign
The “lying down” adrenal sign is associated with renal agenesis.
Features of Potter syndrome
Bilateral renal agenesis
Abnormal facial features (Potter facies) Pulmonary hypoplasia
Limb abnormalities
Intrauterine growth restriction
Fetal Renal Cystic Disease
autosomal recessive polycystic kidney disease (ARPKD), autosomal dominant polycystic kidney disease (ADPKD), multicystic dysplastic kidney (MCDK) disease, and obstructive cystic dysplasia.
The typical sonographic findings of a fetus affected by ARPKD
bilateral, enlarged, echogenic kidneys, nondetectable urinary bladder, and oligohydramnios
One condition associated with ARPKD
Meckel–Gruber syndrome, which is a fatal disorder that includes renal cystic disease, occipital encephalocele, and polydactyly
SONOGRAPHIC FINDINGS OF AUTOSOMAL DOMINANT (ADULT) POLYCYSTIC KIDNEY DISEASE
Normal-appearing or bilateral, enlarged echogenic kidneys
2. Visible urinary bladder
3. Normal amniotic fluid volume
4. Cysts do not manifest until approximately the fifth decade of life
SONOGRAPHIC FINDINGS OF BILATERAL MULTICYSTIC
Bilateral, smooth-walled, noncommunicating cysts of varying sizes located within the renal fossae
2. Absent urinary bladder 3. Oligohydramnios
SONOGRAPHIC FINDINGS OF UNILATERAL MULTICYSTIC DYSPLASTIC RENAL DISEASE
Unilateral, smooth-walled, noncommunicating cysts of varying sizes located within the renal fossa
2. Compensatory hypertrophy of the contralateral kidney
3. Visible urinary bladder
4. Normal amniotic fluid volume
SONOGRAPHIC FINDINGS OF BILATERAL OBSTRUCTIVE CYSTIC DYSPLASIA
Small, echogenic kidneys
2. Peripheral renal cysts
3. Bilateral hydronephrosis
4. Thick-walled urinary bladder 5. Oligohydramnios
Lead to bilateral obstructive cystic
ureterocele, or a severe bladder outlet obstruction, early in gestation, to bilateral obstructive cystic dysplasia, in which case oligohydramnios will be present
Unilateral obstructive cystic dysplasia is most often caused
obstructive cystic dysplasia is most often caused by a pelviureteral junction or vesicoureteral junction obstruction
Renal pelvis diameter measurements indicative of fetal hydronephrosis
Before 20 weeks After 20 weeks
Renal Pelvis Diameter Measurement
≥7 mm (borderline between 4 and 6 mm) ≥10 mm (borderline between 5 and 9 mm)
29-2
SONOGRAPHIC FINDINGS OF URETEROPELVIC JUNCTION
Hydronephrosis (dilated renal pelvis and calices) 2. Normal ureters (nonvisualization)
3. Normal bladder
SONOGRAPHIC FINDINGS OF POSTERIOR URETHRAL VALVES
. “Keyhole” sign (dilated bladder and urethra)
2. Bilateral hydroureter
3. Bilateral hydronephrosis
4. Oligohydramnios
5. Thickened bladder wall
SONOGRAPHIC FINDINGS OF PRUNE BELLY SYNDROME
. Dilated bladder and possibly urethra (“keyhole” sign)
2. Absent abdominal musculature
3. Undescended testis
4. Urinary tract abnormalities (megacystis and hydronephrosis
SONOGRAPHIC FINDINGS OF URETEROVESICULAR JUNCTION OBSTRUCTION
. Hydronephrosis
2. Dilated ureter
3. Normal bladder
4. Normal amniotic fluid (if unilateral)
SONOGRAPHIC FINDINGS OF BLADDER EXSTROPHY
Lower abdominal wall mass inferior to the umbilicus
2. Absent urinary bladder
3. Normal kidneys
cloacal exstrophy,
OEIS complex stands for omphalocele, bladder exstrophy, imperforate anus, and spina bifida
SONOGRAPHIC FINDINGS OF THE MESOBLASTIC NEPHROMA
Solid, homogeneous mass within the renal fossa and may completely replace the kidney.
The most common solid fetal renal mass is the mesoblastic nephroma.