1. Congenital Flashcards
(43 cards)
The uterus in a neonate
cervix often larger than the fundus.
The uterus in prepuberty
tube-like, with the cervix and uterus the same size.
The uterus in puberty
(pear-like) - with the fundus larger than the cervix
visible endometrium
Turner syndrome
45 XO + CoA + Horseshoe Kidney +
+ Prepuberty uterus (cervix = uterus) + Streaky Ovaries
The mullerian ducts make up these parts
Uterus + Upper 2/3 of the vagina
What grows up to meet the mullerian duct and make the bottom 1/3 of the vagina?
Urogenital sinus
This ducts regress completely in girls
Wolffian
Mullerian ducts
Uterus
Fallopian Tubes
Upper 2/3 of the vagina
Wolffian Ducts
Vas Deferens
Seminal Vesicles
Epididymis
Urogenital sinus
Prostate
Bottom 1/3 of the vagina
3 ways the whole process of embryology gets screwed up
- Failure to form
- Fail to fuse
- Fail to cleave
Explain the concept of embryology?
Failure to form conditions:
- Mullerian agenesis
- Unicornuate Uterus
Failure to Fuse
Uteru Didelphys
Bicronuate uterus
T-shaped uterus
Failure to cleave conditions
Septate
Arcuate Uterus
Mullerian Agenesis ahs three features:
- Vaginal atresia
- Absent or rudimentary uterus (unicornuate or bicronuate
- Normal ovaries
Kidneys have isssues in 50% of cases
Cornus =
Collis =
Cornus = uterus
Collis = cervical
Mullerian agenesis AKA
Mayer-Rokitansky-Kuster-Hauser syndrome
4 variants of Unicronuate uterus
Most common unicronate uterus subtype
ISolated unicronuate
If you see a unicomuate utems the classic teaching is to
Look for a rudimentary horn
Rudimentary horns have endometrium - phantom female belly pain = risk of miscarriege
Risk of non-communicating unicornuate subtype?
Rudimentary horn rupture (life threatening bleeding
Most common abdnormality in unicronute uterus
Ipsilateral renal agenesis contralateral to main uterin horn (Ipsilateral to rudimentary horn)
This is a complete uterine duplication (two cervices, two uteri, and two upper 1/3 vagina).
Uterus Didelphys