Esclerose tuberosa Flashcards

1
Q

Especto de achados no SNC

A

Túbers corticais e subcorticais
Nódulos subependimários
Heterotopia na substância branca
SEGA (astrocitoma subependimário de células gigantes)

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2
Q

Túbers - Aspecto na TC

A

Hipodensos com focos de calcificação

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3
Q

Túbers - Sinal na RM

A

T1: hipointenso
T2: hiperintenso

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4
Q

Túbers - SWI

A

Artefatos de susceptibilidade magnética

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5
Q

Túbers - Outros achados

A

Degeneração cística

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6
Q

Túbers - Quais os mais associados a epilepsia?

A

Sinal heterogêneo: centro hipointenso com halo hiperintenso

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7
Q

Heterotopia - Sinal na RM

A

T1: iso ou hipointenso
T2: hiperintenso

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8
Q

Heterotopia - Realce

A

Tênue e homogêneo

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9
Q

Heterotopia - Aspecto geral

A

Focos lineares com extensão do córtex ao ventrículo

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10
Q

Nódulos subependimários - TC

A

Lesões calcificadas junto aos ventrículos laterais

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11
Q

Nódulos subependimários - Sinal na RM

A

T1: Iso/hiperintenso
T2: Iso/hiperintenso

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12
Q

Nódulos subependimários - Realce

A

Variável

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13
Q

Nódulos subependimários - SWI

A

Artefatos de susceptibilidade magnética

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14
Q

SEGA - Local comum

A

Ao redor do forame de Monro

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15
Q

SEGA - Tamanho em comparação com nódulos subependimários

A

> 1 cm

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16
Q

SEGA - Outros achados que diferenciam dos nódulos subependimários

A

Calcificação incompleta

Realce mais ávido

17
Q

SEGA - Espectroscopia

A

Aumento de colina

Queda NAA