Hirschsprung Disease Flashcards
which part of the intestine does hirschsprung disease usually occur
large intestine
the absence of what causes this disease
ganglion cells
what is the result of no ganglion cells
obstruction
accumulation of intestinal contents
distention of bowel
what are signs of this disease in the newborn
no meconium within 24-48 hours
refusal to feed
bilious vomiting
abdominal distention
what are signs of this disease in the infant
failure to thrive
constipation
explosive V/D
fever
what are signs of this disease in the child
constipation
ribbon-like stools
visible peristalsis
palpable fecal mass LLQ
what does an abdominal xray show
dilated loops of bowel
what does an unprepped barium enema show
visualize the dilated & narrow segments of the colon
what is the definitive test that reveals the absence of ganglion cells
rectal biopsy
what are 3 alternatives to surgery
dietary modifications
stool softeners
isotonic irrigations
how often would isotonic irrigations need to be done
daily
when should enemas be avoided
why
suspect enterocolotis
potential for perforation
what are the 2 phases of surgical management
temporary colostomy
close colostomy
at which weight can the colostomy be closed
20 lbs
what kind of diet is needed pre-op
high calorie
high protein
low fiber
