Idiopathic Pulmonary Fibrosis Flashcards
1
Q
Define idiopathic pulmonary fibrosis
A
- chronic, progressive fibrosing interstitial PNA
2
Q
What is the cause of IPF?
A
- unknown
3
Q
What is the MC restrictive lung disease?
A
- IPF
4
Q
What is the pathogenesis of IPF?
A
- stimuli –> lung injury –> inflammation –> wound healing –> fibrosis/decreased ventilation
5
Q
T/F: There is a cure for IPF.
A
- false, no stopping it, only slows the progression
6
Q
What are the possible inciting agents/triggers?
A
- smoke
- pollutants
- dust
- viral infx
- GERD
- chronic aspiration
7
Q
T/F: IPF has a poor prognosis with survival of 2-5 years from time of dx.
A
- True
8
Q
What are the S&S of IPF?
A
- nonspecific (dyspnea and/or nonproductive cough)
- gradual onset
9
Q
What will be pertinent findings in the hx of IPF?
A
- smoker
- progressive dyspnea
- non-productive cough
- constitutional sx
- travel
- HIV/TB
10
Q
What will be present on PE in IPF?
A
- fine basilar inspiratory crackles
- clubbing
- increased S2 intensity of fixed split S2
- holosystolic tricuspid regurgitation
- pedal edema
11
Q
What diagnostic test should be performed in IPF?
A
- CXR/CT
- PFTs
- Bx
12
Q
What will PFTs show in IPF?
A
~everything is low except FEV1/FVC~
- decreased TLC & RV
- normal or increased FEV1/FVC
- decreased DCLO
13
Q
What will be seen on CXR/CT in IPF?
A
- reticular opacities (honeycombing)
- ground glass opacities
14
Q
T/F: Hypoxemia is always present in IPF.
A
- False
15
Q
What is the tx of IPF?
A
- lung transplant
- manage complications
- smoking cessation
- vaccinations
- pulm rehab
- refer to dietician
