PULMONARY ARTERIOVENOUS MALFORMATION Flashcards
1
Q
PULMONARY ARTERIOVENOUS MALFORMATION
A
MOST CONGENITAL
MAJORITY WITH HHT
OTHERS: CIRRHOSIS,
SCHISTOSOMIASIS,
THYROID CARCINOMA
2
Q
HHT
A
AUTOSOMAL DOMINANT
CUTANEOUS AND VISCERAL ARTERIOVENOUS MALFORMATIONS
3
Q
PAVM SYMPTOMS
A
DYSPNEA THA IS WORSE WHEN PT IS SITTING OR STANDING, AND RELIEVED BY LYING DOWN.
PLATYPNEA
THIS IS ORTHODEOXIA, DECREASE IN PO2 WHEN IN UPRIGHT OR SEATED POSITION
4
Q
PAVM PROGNOSIS
A
LEFT UNTREATED RISK OF STROKE IS 11% RISK OF BRAIN ABSCESS 7% SEIZURE, MIGRAINES HEMOPTYSIS ENDOCARDITIS
5
Q
PAVM TREATMENT
A
EMBOLIZATION
