Congenital heart disease

Question 1

Cyanotic R>L

Answer 1

C/f: cyanosis, normal pulses, no response to hyperoxia
5T’s
Truncus arteriosus
Transposition of great vessel
Tricuspid atresia
Tetralogy of Fallot
Total Anomalous Pulm Venous Return

Question 2

Acyanotic L>R
(non duct dependent lesions)

Answer 2

C/f: asymptomatic at birth, murmur, heart failure (sweaty, poor feed, Inc WOB)
PDA
ASD
VSD

Question 3

Duct dependent lesions
- Systemic circulation

Answer 3

Hypoplastic L heart
Critical AS
Coarctation of aorta

Question 4

Duct dependent lesions
- Pulm circulation - no response to hyperoxia test (10mins 100% FiO2)

Answer 4

Tricuspid atresia
Pulm atresia
Severe TOF
Critical pulm stenosis

Question 5

Tetralogy of Fallot

Answer 5

P - Pulm stenosis
R - RVH
O - Overiding Aorta
V - VSD

Question 6

Treatment

Answer 6

Prostaglandin E1 - 50ng/kg/min IV - duct dependent