CP Pathology and Surgeries Flashcards

1
Q

Review: Define CP

A

An inclusive term to describe a group of nonprogressive disorders occurring in young children in which disease of the brain causes impairment of motor function.
- Secondary changes in the musculoskeletal system
may progress throughout growth

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2
Q

What can spasticity cause?

A

Spasticity ->
Inability to stretch muscles during normal play ->
Muscle contractures ->
Abnormal skeletal forces

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3
Q

What are some orthopedic problems for children with CP?

A

Spastic hip disease
Spinal deformity
Ankle/Foot deformities

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4
Q

What are the four priorities for CP patients?

A
  1. Communication
  2. ADL’s
  3. Mobility
  4. Walking
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5
Q

What are some oral interventions and what do they address?

A

Diazepam, Baclofen, Tizanidine
- Decreases tone
SE: Sedation, weakness, hypotonia

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6
Q

What are the secondary problems for patients with MS that can be changed/impacted?

A

Muscle contracture/Bony abnormalities ->
PT/Orthotics ->
Orthopedic surgery ->
Muscle lengthening, Muscle transfer, Osteotomy/Arthrodesis

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7
Q

What are some injectable interventions and what do they address?

A

Botulinim toxin A (botox)
- Irreversibly blocks acetylcholine release by nerves at motor end point (Reversible chemical denervation)

Phenol/Alcohol nerve block
- Similar to Botox but lasts longer

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8
Q

Who is a good candidate for botox and how long does it last?

A

Lasts ~4-6 months

Patient selection
- Dynamic muscle contracture
- Limited number of muscles involved (< 4)

Goals
- Delay surgical intervention
- Facilitate stretching
- Adjunct to PT, casting
- Simulates surgery

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9
Q

What is a surgical intervention and what does it address?

A

Dorsal Rhizotomy
Decreases stimulation from muscle spindles – section of sensory rootlets
- Weakens muscle
- Prevents need for
orthopaedic surgery ~ 50%

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10
Q

Who is a good candidate for Dorsal Rhizotomy surgery?

A

Patient selection is critical to success
- Pure spasticity
- No fixed contractures
- Good selective motor control
- 4-8 years old
- Adequate cognition to cooperate with rehab

Ideal SDR Candidate
- 3-8 y/o spastic diplegic
- Former preemie, LBW, with severe, pure spasticity
- Extensive postop rehab required

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11
Q

What is the result of Dorsal Rhizotomy surgery and what are some side effects?

A

Results
- Permanent decrease in spasticity
- Supraspinal effects
- Upper extremity function
- Bladder function
- Speech, swallowing

Complications
- Dysesthesias, weakness, neurogenic bladder, sensory loss

Effects on musculoskeletal system
- Effect the need for orthopaedic surgery?
- Spinal deformity
- Scoliosis, spondylolisthesis, hyperlordosis
- ? Hip subluxation

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12
Q

What is an Intrathecal Baclofen and why would one have that surgery?

A

Neurosurgical procedure
- Local delivery to spinal cord
- Intrathecal catheter
- Subcutaneous pump
- Complications in up to 25%

Indications
- Spasticity
- Interferes with function or ease of care

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13
Q

When does PT intervene for CP patients?

A

Children < 3 (early intervention)
Post-operative PT
Targeted interventions
“Primary care”

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14
Q

When would a serial cast be used and how often are they changed?

A

Mild spasticity/contractures
Dynamic deformities
Casts every 1-2 weeks for 6-8 weeks
Recurrence a problem

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15
Q

When would an orthotic be used and what can they help?

A

Prevent deformity
Stabilize joints
Substitute for weak muscles
Rarely go above knee

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16
Q

What are the primary problems in orthopedic treatment of CP?

A

Loss of selective motor control
Balance
Spasticity - leads to secondary problems
(permanent)

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17
Q

What are the secondary problems in orthopedic treatment of CP?

A

Soft tissue contracture
Bony deformities
(may be corrected)

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18
Q

What are the tertiary problems in orthopedic treatment of CP?

A

Compensation for primary and secondary problems

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19
Q

What is “Lever arm dysfunction”?

A

Alteration in the leverage relationships necessary for normal gait
Correction increases magnitude of moment acting on joint

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20
Q

What is included in a preoperative evaluation?

A

Collect data
- Functional level
- ROM, strength, selectivity
- Observational Gait Analysis
- Radiographs
Generate problem list
Instrumented motion analysis

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21
Q

What are the goals for a multiple LE procedure?

A

Correct lever arm problems
Lengthen muscles that are short
Transfer muscles that are out of phase or creating deformities
Adequate rehabilitation

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22
Q

Describe muscle-tendon lengthening and what are some issues that may occur?

A

For dynamic and static soft tissue contractures
- Multiple techniques
- Weakens muscle
- May decrease tone elsewhere

23
Q

Describe tendon transfers and what are some issues that may occur?

A

Substitutes for weak muscles
- Changes pull of overactive muscles
- Weakens muscle
- Complete vs. Split transfers

24
Q

Describe bony surgeries and what do they provide?

A

Osteotomies
- cutting and realigning bones
- corrects deformity
(Hip)

Fusions
- joining bones together
- decreases motion
- stabilizes
(Spine, Foot)

25
Q

What are interventions for ambulatory (hemiplegia/diplegia) CP patients?

A

Both soft tissue and bony pathology may occur at hip, knee, and ankle

Address all components at once
- Lengthen muscles that are short
- Transfer muscles that are out of phase or creating deformities
- Correct lever arm problems

Have realistic goals

Adequate rehabilitation

Will still need orthotic support

Will still have problems with selectivity, balance, and spasticity!

26
Q

What are some common gait deviations for the hip?

A

Internal rotation gait
- Femoral torsion
- Muscular forces (Glut Min, TFL)

Flexion deformity

27
Q

What are some surgical interventions for internal rotation gait hip?

A

Intramuscular Psoas lengthening

Derotational Osteotomy:
- Internal femoral torsion +/- coxa valga

28
Q

What are some common gait deviations for the knee?

A

Excessive flexion in stance phase
- Hamstring contracture
- Torsional deformity

Impaired clearance in swing phase
- Spastic rectus femoris

29
Q

What is a surgical interventions for knee gait deviations?

A

Fractional Hamstring lengthening: for “functional” HS contracture

Rectus femoris transfer: for spastic RF

Medial Hamstring Lengthening

Tibial derotational osteotomy: torsional deformity

30
Q

What are some common gait deviations for the foot/ankle?

A

Loss of Stance phase stability

Impaired clearance in swing phase

Impaired prepositioning

31
Q

What is a surgical interventions for equinus?

A

Preferably using a gastroc soleus recession technique

Avoid Z-lengthening if possible

  • Soleus essential for stance phase support and power generation
32
Q

What is Equinovalgus and what causes it?

A

Muscle imbalance of gastroc - make foot move into valves
Most common in diplegia

33
Q

What is the surgical treatment for Equinovalgus ?

A

Treat equinus first

Lateral column lengthening
- Gastrocsoleus lengthening
- Calcaneal osteotomy
- Forefoot varus (bone block for lengthening)
OR
Triple Arthrodesis (fusion surgery)

34
Q

What is the surgical treatment for FLEXIBLE Equinovalgus? (club foot)

A

Tibialis Posterior, Tibialis Anterior, both

Intramuscular Tibialis Posterior lengthening

Gastrocsoleus lengthening

Split tendon transfer

35
Q

What is the surgical treatment for FIXED Equinovalgus? (club foot)

A

Hindfoot (Calcaneal osteotomy)
- Lateral closing wedge
- Sliding

Midfoot
- Dorsolateral closing wedge of cuboid

Forefoot
- Dorsiflexion osteotomy medial column

Triple arthrodesis

36
Q

What results from a crouch gait?

A

Loss of PF/KE Couple. (Lever-arm dysfunction, Soleus insufficiency)

2 degree Contractures of hip & knee flexors

Contracture of posterior knee capsule

Quadriceps insufficiency/Patella alta

37
Q

How can crouch gait be treated?

A

Serial casting

Hamstring lengthening

“Guided growth” with Plate or staples

Hamstring lengthening + posterior capsulotomy

Distal femoral extension osteotomy and patellar ligament advancement

38
Q

What are the priorities for Quadriplegia/non-ambulatory CP patients?

A

Communication
Activities of daily living
Mobility
Only ~20% Ambulate

39
Q

What are the goals for Quadriplegia/non-ambulatory CP patients?

A

Wheelchair to maximize function
Spine: straight enough to sit
Hips: located, mobile, painless
Knee: motion for sitting and transfers
Feet: plantigrade

40
Q

What are some issues that result if a patient has hip displacement?

A

Pain
Sitting difficulty
Pelvic obliquity/scoliosis
Ease of care

41
Q

What causes spastic hip disease?

A

Soft tissues
- Spasticity/muscle imbalance
- Adduction contracture

42
Q

How do we screen for spastic hip disease?

A

Imaging, using Reimer’s Migration Index

CP Normal: < 30%
Subluxation: >30%
Dislocation: >90%

43
Q

How to screen for dislocation potential?

A

Clinical = hip abduction
Baseline AP pelvis at 18 months
AP pelvis every 6 mos if “at risk”

44
Q

What are the treatment options for hip subluxation in each phase?

A

Early = Soft tissue lengthening (preventative)

Bony changes = Reconstruction

End stage = Salvage

45
Q

What are some surgical treatments for hip subluxation?

A

Soft tissue lengthening (early)
Femoral Osteotomy
Pelvic Osteotomy
Open reduction
Acetabuloplasty

46
Q

What % of CP patients with spastic Quadriplegia will have scoliosis?

A

39-75%
Gets worse with skeletal maturity

47
Q

What are treatment options for scoliosis?

A

Observation
- Small or nonprogressive curves

Nonoperative
- Wheelchair modifications (controls pelvis, trunk, head/neck)
- Bracing (does not prevent progression, improves function)

Operative
- Spinal arthrodesis (fusion)

48
Q

What are the indications/considerations for surgical interventions for scoliosis?

A

Curve magnitude/progression > 40 - 50°

Sitting imbalance (loss of UE use)
Visceral problems or pain

Degree of intellectual disability?

49
Q

What are the benefits for spinal fusion to address scoliosis?

A

Sitting balance/endurance
Use of upper extremities
Pulmonary function
Feeding/nutrition
Ease of care, transportation
Decreased pain

50
Q

What are the complications for spinal fusion to address scoliosis?

A

Occurs in 48-81%
Respiratory (Atelectasis, Pneumonia)

Gastrointestinal (Reflux/aspiration, Ileus, SMA syndrome)

Skin/Wound

Infection (Superficial, Deep [5-8%])

Implant Related

Pseudarthrosis

51
Q

What is athetoid CP?

A

Abnormal tone and
tension
Increases with activity
Squirming or writhing motion
Constant
Disappears during sleep

52
Q

Complications and considerations for athetoid CP?

A

Kernicterus
Many are non ambulators
Soft tissue surgery unpredictable
Scoliosis
Cervical spine disease in adults

53
Q

What is the orthopedic treatment process (summary)?

A

Define problem list

Address all components at once

Have realistic goals

Adequate rehabilitation

Pts will still need orthotic support and will have problems with selectivity, balance, and spasticity!