Flashcards in Deck 1 Deck (9)
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1
Clinical clues for ASD
- Right ventricular heave
- Wide, fixed splitting of the second heart sound
- Mid systolic pulmonary flow or ejection murmur
- Right axis deviation and incomplete RBBB
2
Important ASD complications
- Atrial arrhythmias (Afib and flutter)
- Stroke due to paradoxical embolization
- Migraine headache
- Pulmonary hypertension and Eisenmenger syndrome
3
Clinical features of CVID (common variable immune deficiency)
- Recurrent infections (rhinosinusitis, pneumonia, conjunctivitis)
- Chronic lung disease (bronchiectasis)
- Autoimmune disorders (vitiligo, RA, thyroid)
- GI disorders (IBS, malabsorption)
- Granulomatous dz
- Increase risk of malignancy (lymphoma, gastric CA)
4
Diagnosis of CVID (common variable immune deficiency)
Extremely persistent low IgG levels
Low IgA and/or IgM levels
No response to vaccinations
Exclusion of other immunodeficiency disorders
5
Treatment of CVID (common variable immune deficiency)
Immunoglobulin replacement therapy
Age-appropriate cancer screening
Monitoring for lymphoma
6
Adult CF
Mild respiratory infections, GI disease (recurrent pancreatitis, biliary cirrhosis, portal HTN), abnormal reproductive function
7
Myeloperoxidase deficiency
Asymptomatic or recurrent Candida infections
8
Primary ciliary dyskinesia
Nasal polyposis, otitis, recurrent respiratory infections, situs inversus (50% of pts), infertility
9
