Limb Deficiencies

Question 1

Rate of phantom pain/sensation in congenital limb-deficient children

Answer 1

Zero

Question 2

What is the preferred classification system for pediatric limb deficiencies

Answer 2

ISPO (international Society for Prosthetics and Orthotics)

Question 3

Most common congenital lower limb deficiency

Answer 3

Fibular longitudinal deficiency

Question 4

What is Holt-Oram Syndrome

Answer 4

Limb deficiencies associated with CHD

Question 5

Most common complication seen after amputation in an immature child

Answer 5

Terminal overgrowth

Question 6

Absence of a limb

Answer 6

Amelia

Question 7

Partial absence of a limb

Answer 7

Meromelia

Question 8

procedure for PFFD that rotates foot by 180 degrees and attached to shortened femur, allowing ankle to control prosthesis

Answer 8

Van Ness Rotation

Question 9

Treatment of choice for a transtibial deficiency

Answer 9

Knee disarticulation

Question 10

When is a more sophisticated transradial prosthesis and terminal device fitted for a child after the initial prosthesis?

Answer 10

11-13 months when child can walk

Question 11

What kind of procedure is usually done for severe forms of PFFD

Answer 11

Fusing shortened femur to tibia and doing a Syme’s amputation

Question 12

When does first prosthetic fitting for a transradial deficiency occur for a child?

Answer 12

6-7 months, when they can first sit

Question 13

MC prosthetic foot used for a child amputee

Answer 13

SACH foot

Question 14

Procedure used to separate ulna and radius in forearm to create prehensile surface

Answer 14

Krukenberg procedure

Question 15

What is VACTERL syndrome

Answer 15

Vertebral defects
Anal atresia
Congenital defect
TracheoEsophageal fistula
Renal dysplasia 
Limb deficiency

Question 16

Missing hand or foot

Answer 16

Acheiria

Question 17

At what age can a child operate all types of prosthetic components for a transradial deficiency?

Answer 17

4-5 years

Question 18

Absence of half a limb

Answer 18

Hemimelia

Question 19

MCC of pediatric acquired amputation

Answer 19

Trauma

Question 20

What kind of amputation is preferred in pediatrics to preserve the epiphyseal growth place

Answer 20

Joint disarticulation

Question 21

What procedure is done if there is fibular deficiency and severe leg length discrepancy

Answer 21

Syme’s amputation

Question 22

How often should prosthesis be replaced in a growing child?

Answer 22

<5yo = q12 mths
5-12yo = q18 mths
12-21yo = q24 mths

Question 23

According to ISPO, what does transverse vs longitudinal mean?

Answer 23

Transverse = no distal remaining portions
Longitudinal = distal portions remain intact

Question 24

Absent finger or toe

Answer 24

Aphalangia

Question 25

Absent metacarpal or metatarsal

Answer 25

Adactyly

Question 26

Which trimester are congenital limb deficiencies formed?

Answer 26

First trimester

Question 27

Most common congenital limb deficiency

Answer 27

Left terminal transradial deficiency

Question 28

At what age can you use body-powered hooks for transhumeral deficiency

Answer 28

2-3 years

Question 29

What is Fanconi's syndrome

Answer 29

Limb deficiencies associated with Anemia and leukopenia

Question 30

What is TAR syndrome?

Answer 30

Thrombocytopenia with Absence of Radius

Question 31

70-80% of patients with PFFD also present with deficiency of.........

Answer 31

Fibula

Question 32

Treatment of choice for terminal overgrowth

Answer 32

Surgical revision

Question 33

What bones does terminal growth MC occur in, in descending order

Answer 33

Humerus, fibular, tibia, femur

Question 34

At what age can children use motorized wheelchairs

Answer 34

5-6 years

Question 35

Longitudinal deficiency of the femur

Answer 35

Partial proximal femoral focal deficiency (PFFD)

Question 36

Flipper-like appendage attached to trunk

Answer 36

Phocomelia

Question 37

At what age is prosthetic fitting done for a LE amputee

Answer 37

9-10 months, when child can pull to stand

Question 38

Most frequent tumors that causes pediatric acquired amputation

Answer 38

Osteosarcoma and Ewing's sarcoma