Pediatrics Flashcards

Question

Homolateral synkinesis

Answer 1

* resist flexion involved UE = get flexion involved LE | * resist extension involved UE = get extension involved LE

Answer 2

* resist adduction normal extremity get adduction involved extremity * resist abduction normal extremity get abduction involved extremity

Answer 3

• elevation of the involved arm above horizontal may elicit an extension and abduction response of the fingers

Answer 4

as involved extremity is performing a task it also takes place in the normal extremity i.e thumb to finger

Answer 5

• performed at 1 minute then again at 5 minutes • graded on 5 criteria: activity (muscle tone), pulse, grimace (reflex irritability), appearance (skin color), respiration • each criteria is graded on a scale of 0 to 2 1) Activity (muscle tone): 0=absent, 1=UE and LE flexion, 2=active movement 2) Pulse: 0=absent, 1= <100 bpm, 2= >100 bpm 3) Grimace (reflex irritability): 0=flaccid, 1=some flexion of extremities, 2=active motion (cough, sneeze, withdrawal) 4) Appearance (skin color): 0=blue, pale, 1=pink body, blue extremities, 2=pink 5) Respiration: 0=absent, 1=slow, irregular, 2=vigorous, cry • Total points are then added: - 0-3: severely depressed - 4-6: moderately depressed - 7-10: excellent condition

Answer 6

* Neonate: 0-10 days * Infantile: 0-3 months * Preparation: 4-6 months * Modification: 7-9 months * Refinement: 10-12 months

Answer 7

1 Month: Important notes: • decreased physiological flexion Standing/ Walking: • automatic walking reflex

Answer 8

2 Months: Important notes: • hypotonia/asymmetry Prone/ Supine: • (P) head turning/lifting improved, cannot yet hold in midline • (S) head rotates further to the side through asymmetrical extensor pull, which stimulates ATNR, leads to improved lateral vision Sitting/ Other: • (sit) head bobbing (due to lack of neck flexor strength) Standing/ Walking: • automatic walking no longer present

Answer 9

3 Months: Important notes: • symmetry- midline orientation of hands, eyes, and head Prone/ Supine: • (P) puppy position- forearm WB, foor on foot desensitization contact • (S) head can be held in midline. Hands to chest for increased body awareness Sitting/ Other: • can sustain head elevation- develops a "neck" Standing/ Walking: • takes weight on feet again, LEs abd/ knees stiffly extend

Answer 10

Neonate 0-10 days: Important notes: • physiological flexion Standing/ Walking: • automatic walking reflex (continues through 1 month)

Answer 11

4 months: Important notes: • lateral neck flexion Prone/ Supine: • (P) start to roll from prone to sidelying and able to achieve prone on elbow position • (S) start to roll from supine to sidelying, which is helped by hands on knees position. Also able to put hands together in space

Answer 12

5 months: Prone/ Supine: • (P) elbow extension in prone position + weight shift and reach while prone on elbows. Start to roll from prone to supine • (S) feet to mouth leads to increased desensitization Sitting/ Other: (sit) when pulled to sitting by their head no longer lags. Can also ring sit with arms forward.

Answer 13

6 months: Important notes: • Landau reflex (superman position when held horizontal in air in prone) complete • may say first word (often dada) Prone/ Supine: (S) able to roll from supine to prone with LEs out in space and able to transfer objects from one hand to the other. Sitting/ Other: • (sit) nice and erect sitting posture with protective extension forward Standing/ Walking: • bounce

Answer 14

7 months: Important notes: • equilibrium reactions present in supine and starting in sitting Prone/ Supine: • (P) baby can pivot in a circle Sitting/ Other: • (sit) sits unsupported with protective extension sideways • (O) can go from prone to quadruped then rock to sit Standing/ Walking: • from quadruped may pull to stand

Answer 15

8 months: Important notes: • equilibrium reactions in sitting beginning in quadruped Prone/ Supine: • (P) creeping Sitting/ Other: • (O) goes from sitting to quadruped to kneeling to standing Standing/ Walking: • must "plop" to get down. Cruises sideways on furniture, needs both UEs

Answer 16

9 months: Important notes: • feed themselves "pinch" with fingers • constant movement Sitting/ Other: • (sit) able to side, and w sit. Protective extension backwards begins. • (O) crawling over objects Standing/ Walking: • cruising semi-turned

Answer 17

10 months: Sitting/ Other: • (sit) protective extension backwards Standing/ Walking: • cruise with one UE and can lower to sit slowly

Answer 18

11 months: Sitting/ Other: • (sit) long sit • (O) half kneeling more functional Standing/ Walking: • can stand by leg extension rather than UE extension • reach for objects, which leads to falls in standing • high guard appearance

Answer 19

12 months: Important notes: • roll ball • say 2 words Standing/ Walking: • able to weight shift and lift one leg

Answer 20

drink out a cup

Answer 21

starts climbing, walks sideways and backwards, ascends and descends stairs and small elevations, turns pages

Answer 22

kick ball, running, feed self with spoon

Answer 23

talk in sentences

Answer 24

stand on one foot, jump in place, ride tricycle, walks heel to toe

Answer 25

skips, alternate feet up and down stairs, throw overhead, put shoes on correct feet, brush hair and teeth

Answer 26

hop, catch a ball, jump off object and land on 2 feet

Answer 27

handedness established

Answer 28

due to non-progressive damage to the CNS before age 3 in single or multiple locations of the immature brain. Can be prenatal (before birth), perinatal (during birth), or postnatal (after birth) in origin. Usually results from lack of oxygenation but may also result from infection, trauma, cranial hypoxia, consanguinity (inbreeding=genetic issue), or baby's blood is just not compatible with the mother's. • Frequently associated with placental insufficiency, prematurity, grade III or IV intraventricular hemmorrhage, or periventricular leukomalacia (the death of small areas of brain tissue around fluid-filled areas called ventricles. A major cause is thought to be changes in blood flow to the area around the ventricles of the brain). • difficult to diagnose during infancy, often diagnosed between 8-12 months of age

Answer 29

• impaired voluntary muscle control and coordination may be accompanied by or associated with: - mental retardation - learning disabilities - speech disorders - auditory impairments, seizures, and abnormalities of vision

Answer 30

* Monoplegia * Diplegia * Triplegic * Hemiplegic * Quadraplegic

Answer 31

one limb involved | *trunk and face may also be involved

Answer 32

2 limbs involved- usually the LEs and you may see a scissor gait *trunk and face may also be involved

Answer 33

3 extremities involved | *trunk and face may also be involved

Answer 34

1 UE and 1 LE on the same side of the body involved (just like with CVA) *trunk and face may also be involved

Answer 35

4 extremities and the trunk involved | *trunk and face may also be involved

Answer 36

areas of the brain affected and tone

Answer 37

* Spastic * Dyskinetic/Athetoid * Ataxic

Answer 38

most common due to involvement of motor cortex or white matter -corticospinal tract- to and from cortical sensorimotor sections of the brain

Answer 39

due to involvement of the basal ganglia

Answer 40

due to involvement of the cerebellum

Answer 41

* spastic diplegia is the most common classification (35%) * UMN s/s: spasticity, (+) Babinski, clonus, hyperreflexia * location of the lesion: corticospinal tracts (pyramidal tracts) * etiology: periventricular leukomalacia * presentation: scissor gait- increased hip adductor tone, commando crawl (legs drag behind due to weakness)

Answer 42

* spastic hemiplegia is the second most common CP classification (25%) * UMN s/s * location of the lesion: corticospinal tracts * etiology: CVA, IVH * presentation: cirumductive gait (on weak side), early handedness (decreased use of affected side)

Answer 43

* spastic quadraplegia is the third most common type of CP (20%) * location of the lesion: corticospinal tract * etiology: PVL * presentation: most severe form of CP, affects all limbs and often impacts swallowing, high likelihood of seizures and cognitive impairment

Answer 44

* 4th most common CP classification (15%) * no UMN s/s: hypotonia with increased tone later in life * location of the lesion: extrapyramidal tracts (basal ganglia) * etiology: birth asphyxia * presentation: involuntary contraction of all muscle groups. Difficulty with speech and swallowing, normal intelligence and low risk of seizures, upper body slightly more affected than lower body

Answer 45

* mental retardation: (30%) * seizures: 1/3, tegrotol, dilantin, phenobarbitol * vision impairments * ortho issues: decreased ROM * oral motor dysfunction * dental problems * hearing loss * decreased spatial awareness

Answer 46

* address impairments (ROM, normalized movement, sensory deficits) and functional limitations (mobility, weight shift, rolling, WB, transitional movements, walking) * decrease tone * increase ROM (with precautions if orthopedic issues present) * increase strength * increase functional motor skills and mobility * educate caregivers- feeding, ROM, dressing, influencing, tone, facilitating normal movement * identify barriers and recommend medications- AD, adaptive equipment

Answer 47

* scale for spasticity * 0: no increase in muscle tone * 1: slight increase in muscle tone, manifested by a catch and release or by minimal resistance at the end of ROM when the affected part is moved into flexion or extension * 1+: slight increase in muscle tone, manifested by a catch, followed by minimal resistance throughout the remaining (less than 1/2) of the ROM * 2: more marked increase in muscle tone through most of the ROM, but affected part moves easily * 3: considerable increase in muscle tone; passive movement difficult * 4: affected part(s) rigid in flexion or extension

Answer 48

* meds: baclofen, valium, dantrolene sodium, clonidine, zanaflex * surgery: rhizotomy (nerve roots cut) * hippotherapy= horse back riding

Answer 49

* birth defect 1/1,000 babies * bones of spine form improperly (when the neural tube doesn't close) * malformation, or opening in the spine * spinal cord exposed (in severe cases) * 3 types: spina bifida occulta, meningocele, myelomeningocele

Answer 50

* spina bifida occulta * meningocele * myelomeningocele

Answer 51

congenital condition caused when the neural tube doesn't fully close, forming at approx 4 weeks gestation • the skin over the involved area may be closed (occulta) or open (aperta) with a cyst (cystica)

Answer 52

* neural arches do not connect but there is no neural material outside of the spinal canal * most commonly occurs in the lower lumbar spine * most benign with no neuro effects (pt doesn't even know) * clinical s/s: skin depression or dimple, dark tufts of hair, telangiextasis (dilated blood vessels), soft subcutaneous lipomas (fatty tumors) * asymptomatic in 40% of cases

Answer 53

* neural arches do not connect and the meningeal membranes protrude through the opening in the child's spinal column. * the cord is not trapped so the child often doesn't exhibit any neuro s/s * may possibly have bowel and bladder dysfunction

Answer 54

* both the SC and the meninges protrude through the vertebral defect into a sac or open area in the back * the SC and surrounding tissue may be visible and exposed to the environment, which places the child at high risk for infection * the SC is malformed and the child exhibits atypical development including flaccid LEs and loss of sensation below the level of the myelomeningocele * possible bowel and bladder dysfunction * the defect can occur at any spinal level, but is often seen in the L/S area spinal level * accompanying the myelomeningocele are abnormalities of the brain such as Arnold-Chiari malformation (type II) in which the cerebellum, pons, and medulla, are elongated and protrude into the foramen magnum * hydrocephalus (obstructed CSF and head enlargement) is seen in 80% due to obstructed flow of CSF * can be prevented (up to 72%) if women take folic acid

Answer 55

* meningocele can be treated surgically to restore normal SC function * myelomeningocele spina bifida is operated on within 48 hours after birth to prevent infection. Surgeons place the SC back in the canal and cover with muscle and skin. Paralysis and bowel problems still persist after surgery.

Answer 56

• the enlargement of the ventricular system (which produces CSF) in the brain due to an increase in CSF • could be the result of Arnold-Chiari malformation • hydrocephalus requires immediate treatment and correction in the form of a ventriculoperitineal (VP) shunt (goes from ventricles to under the skin behind the ear, under the clavicle, to the peritoneal abdominal area), with an extra length of tubing for growth (could also do an atrioventricular shunt, brain to atrium) • Caregivers must be taught to watch for shunt malfunction including: -irritability -increased sleepiness -personality changes -sunset eyes, downward gaze -HA

Answer 57

* bowel and bladder dysfunction- children may need to self cath * latex allergy present in 73% of children with spina bifida * tethered cord occurs when the SC is fixed caudally because of pathology. The tethered cord becomes stretched (especially as the child grows), distorted, and ischemic and may show atypical neuro signs such as decreased strength, and increased LE spasticity, changing urologic patterns. Surgery to free the cord is usually performed. * PI's due to decreased sensation below lesion level and incontinence * contractures due to muscular imbalances * osteoporosis due to decreased WB and decreased muscle pull

Answer 58

* address functional deficits and capitalize on the child's strengths * family education on: optimal positioning, importance of WB and upright positioning, shunt care and signs of malfunction and infection, skin check, ROM, orthotics, AD, and adaptive equipment * static and dynamic balance training * independence in functional skills * mobility training

Answer 59

* a group of genetic diseases in which muscle fibers are unusually susceptible to damage. These damaged muscles become progressively weaker. Most people who have muscular dystrophy will eventually use a w/c * there are many different kinds of MD. Symptoms of the most common variety begin in childhood. Occurs primarily in boys. Other types of MD don't surface until adulthood. * people with MD may have respiratory issues (this is often an eventual fatality) and trouble with swallowing. Also contractures and organ problems. * there is no cure but meds and therapy can slow it down

Answer 60

* all forms are due to a genetic disorder * progressive loss of muscle contractility due to destruction of myofibrils * diagnosis made with clinical exam, EMG, muscle biopsy, DNA analysis, enzyme lab * primary impairments include insidious weakness: scoliosis, winging of the scapula, increased lordosis * secondary impairments = decreased respiratory capacity, easy fatigability, occasional obesity * PT used to prolong pt independence with increased use of AD, w/c, and adaptive equipment as the disease progresses

Answer 61

• 4-5 y/o onset of classic clinical features • psuedohypertrophy of calves and possibly also delts, quads, and forearm extensors- not actually hypertrophy but rather deposits of fat as the muscle breaks down. • tightness of gastroc and TFL • initial s/s: clumsiness (muscle weakness), falling, inability to keep up with peers • Trendelenburg and toe walking with shoulder retraction, and decreased UE swing * (+) Gowers sign- use of UE's to push up on thighs to attain standing from the floor • ambulation frequently impossible by age 12

Answer 62

* function (anything to keep them participating in the community) * aquatics

Answer 63

• genetic life-long disorder characterized by RBC that assume abnormal, rigid, sickle shape • prevalence in US is approx. 1 in 5,000 mostly affecting black people • sickle shaped RBC obstruct capillaries and restrict blood flow, resulting in clotting, ischemia, pain, and often organ damage • hand and foot swelling • painful crises are treated with hydration and analgesics, NSAIDs -> opiod -> PCA devices • complications include: CVA, cholelithiasis, avascular necrosis, osteomyelitis, leg ulcers, retinopathy, jaundice, decreased immune reactions, due to hyposplenism, pneumonia, pulmonary hypotension, chronic renal failure, chronic pain TX: children- folic acid, penicillin, bone marrow transplants

Answer 64

* group of heritable disorders characterized by impairment of collagen maturation (gene mutation) * collagen forms a major portion of bone, dentin (teeth), sclerae (eyes), ligaments and skin * genetic (autosomal dominant defect) bone disorder. Pt's are born with defective CT or without the ability to make CT * 8 different types of OI

Answer 65

• bones fx easily, short stature, spinal curvature, barrel-shaped rib cage, bone deformity mild to mod, early loss of hearing, poor muscle tone, discoloration of sclera (blue grey)

Answer 66

* increase overall bone strength to prevent bone fx, while maintaining mobility. PT used to strengthen muscles and improve mobility in a gentle manner while minimizing risk of fx. * often involves hydrotherapy, support cushions for improved posture * pt's encouraged to change positions frequently to change pressure on bones * use of assistive and adaptive devices, meds, biphosphonates, surgery- metal rods, spinal fusions

Answer 67

• genetic diagnosis made by physical and behavioral characteristics rather than genetic testing • causative factor- partial deletion of chromosome 15 • characteristics: small hands, feet, and sex organs, hypotonia, almond-shaped eyes, obesity, and a constant desire for food, coordination impairments and mental retardation Tx: posture control, exercise, fitness, gross and fine motor skills

Answer 68

• genetic abnormality with an extra 21st chromosome • advanced maternal age increases risk • characteristics: mental retardation, hypotonia, joint hypermobility, flattened nasal bridge, narrow eyelids, epicanthial folds (skin fold of the upper eyelid covering the inner corner of the eye), small mouth, feeding impairments, flat feet, scoliosis, congenital heart disease, visual and hearing loss. Tx: exercise, fitness, stability, maximizing respiratory function, caregiver ed, may need heart surgery *Downs children tend to have atlanto-axial subluxation in the neck

Answer 69

• literally means joint many at birth fused • multiple, non-progressive joint contractures are noted at birth. The cause is unknown; may be an underlying neuropathy or myopathy. The limbs appear atrophic, with waxy skin lacking normal joint creases (caused they're fused). The elbows are extended, the wrists flexed and ulnarly deviated, the thumb adducted and clasped and the fingers flexed. TX: treatment is difficult. Serial splinting is started soon after birth, however, correction is often inadequate

Answer 70

• non-progressive muscular disorder • causative factors include: poor movement in utero due to myopathic, neuropathic, or joint abnormalities allowing fibrosis of muscles and structures within the joints, for a small percentage there is an autosomal dominant trait. • characteristics include: cylinder-like extremities, muscle contractures, joint dislocation, and atrophy TX: attain max level of development skills through positioning, stretching, strengthening, splinting, and adaptive equipment, surgery may be needed

Answer 71

*opposite of Barlow's test Purpose: assess for congenital hip dislocation Position: supine fix hips and knees @ 90° of flexion; clinician's thumbs are on the infant's medial thighs and fingers on the lateral thigh Technique: firmly traction the thigh while gently abducting the leg so that femoral head is translated anterior into the acetabulum Interpretation: (+) test = reduction of the hip; an audible "clunk" may be heard

Answer 72

*opposite of Ortolani test Purpose: assess for hip dysplasia Position: supine 90/90; clinician's thumbs are on the infant's medial thigh and fingers on the lateral thigh Technique: apply a posterior force thru the femur as the thigh is gently adducted Interpretation: (+) test = the examiner's finger that is on the greater trochanter will detect a palpable dislocation.

Answer 73

* turns head to side | * holds head up in prone position

Answer 74

* turns from side to back * sits with complete support * holds objects placed in the hand

Answer 75

* able to hold head erect * reaches for objects with both hands * starts hand to mouth activities

Answer 76

* can turn over | * rolls supine to prone

Answer 77

* reaches for objects with one hand | * completes turning and rolling

Answer 78

• sits unsupported

Answer 79

• locomotion through crawling

Answer 80

* cruises | * gets to standing position

Answer 81

* walks but very unsteady | * stands without support

Answer 82

• walks more steadily but with a wide BOS

Answer 83

* continues to improve balance when walking but still poor | * starts climbing

Answer 84

* starts running | * improves balance

Answer 85

• stands on one foot

Answer 86

* skips on one foot | * alternating feet when going up and down stairs

Answer 87

1) maturation of the nervous system 2) individual genetic coding 3) handling 4) environmental experiences (feedback)

Answer 88

* cephalo -> caudally * prox -> distal * gross movement -> fine movement

Answer 89

* tactile * proprioceptive * kinesthetic * visual * vestibular

Answer 90

* every movement involves a weight shift * weight shift is the stimulus for righting reactions and righting reactions are automatic background for all movements. Righting reactions are also the basis for equilibrium reactions * weight shift -> righting reactions -> equilibrium reactions (and all other movements)

Answer 91

Neonatal: • weak or absent sucking/swallowing • episodes of bradycardia or apnea • signs of cerebral irritation such as a high pitched cry or jitteriness • tone may be decreased • primitive reflexes (Moro, stepping) may be difficult to elicit 3 months: • difficulty feeding, tongue thrust may be present • irritability • tone usually hypotonic • brisk DTR • persistent or obligatory primitive reflexes • child keeps on or both hands fisted • strabismus (one eye going in different direction) • advanced head control- usually better in prone due to increased extensor control, difficulty maintaining head in midline in supine 6 months: • delayed motor milestones or abnormal patterns (rolls by spinal extension rather than segmental) • preferential unilateral hand use or fisting • little spontaneous movements, inability to bring hands to midline, reach • persistence of primitive reflexes • arching or strong tendency to stand (without sitting) • infant feels stiff on handling • difficult to dress 9 months: • delayed developmental/atypical movement • crawling- arm movements only, nonreciprocal, asymmetrical movement • reaching- splaying of fingers and extended wrist, tremor • kicking- nonreciprocal • holding arms flexed 12 months: • scissoring, toe-walking, athetoid movement, handedness

Answer 92

exposed, open, underdeveloped cerebrum. Brain stem and its functions preserved.

Answer 93

meninges and CSF in herniating cyst in upper cervical/lower cranial region

Answer 94

brain in an external cyst

Answer 95

foot twisted into extreme inversion so that the sole of the foot cannot touch the ground

Answer 96

* autosomal recessive genetic inheritance * certain types have mutation on chromosome 5 * there is progressive muscular weakness, atrophy, decreased DTRs, normal intelligence, intact sensation, and end stage respiratory compromise * Tx: positioning, vestibular and visual stimulation, access to play. Educate caregivers on use of AD and adaptive equipment

Answer 97

* group of hereditary genetic disorders that impair the body's ability to control blood clotting or coagulation * the hemophiliac does not bleed more intensely than the regular person but can bleed for much longer * in areas such as the brain or inside the joints, this can be fatal or permanently disabling

Answer 98

• encompasses several conditions of which absence of an entire sex chromosome is most common • characteristics: short stature, lymphedema, broad chest, low hairline, low-set ears, webbed necks, gonadal dysfunction, amenorrhea-> sterility; congenital heart disease, hypothyroidism (Hashimoto's thyroiditis), DM, vision and hearing issues, many autoimmune diseases; and specific pattern of cognitive defecits especially visuospatial, mathematical, and memory areas TX: growth hormone and extrogen replacement therapy, complications as appearing

Answer 99

• a condition in which males have an extra X sex chromosome • affected individuals have at least two X chromosomes and one Y • exists in 1 out of every 1,000 males • characteristics: small testicles, reduced fertility, some degree of language learning impairments, deficits in executive functions. Severely involved may have germ cell tumors, breast cancer, osteoporosis. Co-existing conditions include: pulmonary disease, varicose veins, DM, RA TX: testosterone, other tx per complications

Answer 100

* group of inherited CT disorders caused by defect in the synthesis of collagen * collagen helps tissues to resist deformation, in the skin, muscles, and ligaments, blood vessels, and visceral organs- insufficiency causes increased elasticity in these tissues which may vary from mild to life threatening issues. * major signs and symptoms: highly flexible fingers, toes, loose and unstable joints that are prone to dislocation, sprains, subluxations, flat feet, easy bruising, fragile blood vessels, abnormal wound healing, low muscle tone, muscle weakness, early onset OA, cardiac effects, dysautonomia, valvular heart disease * Other less common signs and symptoms: osteopenia, talipes equinovarus, scoliosis, kyphosis, tethered spinal cord syndrome: OA hypermobility, Arnold-Chiari malformation, nerve compression syndromes, fibromyalgia, delayed developmental skills due to hypotonia, Raynaud’s, irritable bowel syndrome, etc…

Answer 101

* maternal alcohol use during pregnancy * growth deficiencies * permanent brain damage, neurological abnormalities, developmental delay, learning/behavior disorders * abnormal facial features including short eye opening, short nose, flat midface, thin upper lip, and small chin

Pediatrics Flashcards

(126 cards)