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Congenital Heart Disease > Tetralogy of Fallot > Flashcards

Flashcards in Tetralogy of Fallot Deck (15):
1

What are the characteristics of TET?

1. ASD and large VSD
2. RVOT obstuction or PS
3. RVH
4. PA atresia
5. Large overriding AO

2

What does atresia mean?

Not there; remnant of.

3

What went wrong during fetal development in order to cause TET?

Truncus septation did not occur normally and there is an abnormality of the truncal and conal swellings.

4

What happens to the AO in TET?

It is abnormally large, with a big LVOT that is not positioned correctly. It overrides the IVS.

5

What happens to the PA in TET?

It is very small and atretic, which leads to PS.

6

What are the physical findings in a Pt with TET?

The Pt may have a bluish tinge because TET is a cyanotic lesion that causes poor gas exchange, poor profusion, and low O2.

7

What is clubbing?

Widening of the fingertips and abnormalities of the nail beds due to interference of flow and dilatation of the capillary beds. It will not go away.

8

What is squatting and what does it help relieve?

The baby squats down to relieve pressure in the RV. It stops venous flow by increasing pressure in the abdomen.

9

What is the most severe form of TET?

Pulmonary atresia with severe RVOT obstruction.

10

What are associated congenital lesions in TET?

- Coronary anomolies
- Bidirectional shunting
- ASD
- Right sided arch (in 25% of cases)
- Bicuspid Pulmonic valve

11

With new advancements in medicine how long after birth is a baby with TET taken into surgery?

Surgery is done within the first 6 months.

12

What are the surgical repairs done for TET?

1. BT shunt (subclavian attached to RPA)
2. ASD & VSD closed
3. Closure of the PDA
4. In PS the RVOT can be resected and reconstructed with a gortex graft in the PA.
5. Pt may get a new pulmonic valve later in life

13

What does mortality mean?

Death

14

What does morbidity mean?

Incidence of disease.

15

What are some surgical complications with TET?

- Right heart failure
- Sudden death
- Ventricular arrhythmias
- Growth retardation
- Infection (due to abnormal myocardium)
- SBE: subacute bacterial endocarditis
- Pacemaker