CV Disorders 1 - Long QT, AS, Muscular Dystrophy

Question 1

How to measure QT interval

Answer 1

Beginning of QRS complex to end of T-wave

Question 2

Most common ion channel dysfunction causing congenital long QT syndrome

Answer 2

Loss of function of K+ channels

Question 3

2 types of meds that may help pts w/ congenital long QT syndromes

Answer 3

β-blockers, spironolactone

Question 4

Answer 4

Brugada syndrome

Question 5

Define low output aortic stenosis

Answer 5

CI <3.0 L/min/m2, mean gradient <30 mm Hg

Question 6

On dobutamine stress echo for pts w/ low output aortic stenosis, if the CI increases, the valve gradient will _____.

Answer 6

increase to a commensurate degree

Question 7

2 meds for Afib/flutter in WPW

Answer 7

Ibutilide, procainamide

Question 8

Main cause of death in Duchenne muscular dystrophy

Answer 8

Cardiomyopathy

Question 9

Rx for Duchenne muscular dystrophy and related cardiomyopathy

Answer 9

Corticosteroids

Question 10

EKG findings of Duchenne muscular dystrophy-related cardiomyopathy

Answer 10

RBBB or R-axis deviation, tall R waves, q waves in left precordial leads

Question 11

Test to distinguish true severe aortic stenosis from pseudostenosis

Answer 11

Dobutamine stress echo