248 Anomalies Of Aorta Flashcards
(17 cards)
Mutation in gene that encode TGFB receptors and 2 (increased signaling cause aneurysm)
Loeys dietz syndrome
Anatomic remnant R aortic arch
Konmerell’s diverticulum
Mutations of type III procollagen
Ehlers danlos type IV
Most common pathologic lesion associated with degenerative aortic aneurysms
Atherosclerosis
Mechanism by which ACEI and ARBs reduce the rate of aortic dilatation
Block TGF beta
Size of ascending thoracic aneurysms for surgery
More than 5 cm
Risk of rupture aneurysms
5 cm 20-40
Repair size of abdominal aortic aneurysm
5.5 cm
Initial lesion syphilitic aortitis
Obliterative endarteritis of the vasa vasorum esp in adventitia
Predilection of mycotic aneurysms
Suprerenal abdominal aprta
Mc affected by syohilis
Proximal ascending aorta
Degeneration of collagen and elastic fibers in tunica media of aorta
Cystic medial necrosis
Mutated in marfan’s syndrome
Fibrillin 1 gene
Spondyloarthropathies aorta
Ascending aorta
Predilection traumatic aneurysm
Descending aortic aorta below ligamentum arteriosum
Most common pathology with ascending aortic aneurysms
Cystic medial necrosis
Tx in aneurysm on marfans syndrome
Blocks tgf B signaling
ACEIs and ARBs