Phaeochromocytoma Flashcards
1
Q
define phaeochromoctyoma?
A
catecholamine-producing tumours that usually arise from chromaffin cells of the adrenal medulla
2
Q
what are the tumours called if they are not on the adrenal glands?
A
paragangliomas
3
Q
what is a big risk factor for phaeochromocytoma ?
A
• Familial cases are seen in patients with:
o MEN2a
o von Hippel-Lindau syndrome
o Neurofibromatosis type 1
4
Q
what are the classical features of phaeochromocytoma ?
A
- Headache
- Sweating
- Palpitations
5
Q
what are the signs of phaeochromocytoma ?
A
- Hypertension
- Postural hypotension
- Pallor
- Tachycardia
- Fever
- Weight loss
6
Q
what is the first line investigation for phaeochromocytoma ?
A
• 24 hr urine collection of metanephrines
7
Q
what investigation should be carried out after urinary collection?
A
CT chest abdomen and pelvis
