Clotting: Hemophillia

Question 1

A genetic defect leading to deficient or defective Factor VIII; inherited as an X-linked recessive trait.

Answer 1

causes of hemophilia A

Question 2

A genetic defect resulting in deficient or defective Factor IX; inherited as an X-linked recessive trait.

Answer 2

hemophilia B Christmas disease

Question 3

What is the primary treatment for hemophilia?

Answer 3

Recombinant Factor VIII or IX replacement therapy, given during bleeding or prophylactically.

Question 4

What medication is used for mild Hemophilia A?

Answer 4

Desmopressin (DDAVP), which temporarily increases Factor VIII levels.

Question 5

What is a major complication of factor replacement therapy

Answer 5

Development of inhibitors (antibodies) to Factor VIII or IX, leading to resistance to treatment.

Question 6

What is a priority nursing diagnosis for a patient with hemophilia?

Answer 6

Risk for bleeding related to clotting factor deficiency.

Question 7

List three home safety measures for patients with severe hemophilia.

Answer 7

Avoid contact sports

Use a soft toothbrush and electric razor

Wear medical ID jewelry

Question 8

What are patients with hemophilia advised to avoid?

Answer 8

Aspirin, NSAIDs, alcohol, and unnecessary invasive procedures

Question 9

How should patients with hemophilia manage bleeding episodes at home?

Answer 9

Administer factor concentrate early, apply pressure, avoid heat, and use cold packs.