What is an anomeric carbon?
What are the three examples of Disaccharides?
What does Maltose consist of?
2 molecules of glucose in an alpha (1-4) linkage
What does Lactose consist of?
Galactose and Glucose in beta (1-4) linkage
What does Sucrose consist of?
Glucose and fructose linked through anomeric carbons
Monosaccharides may combine through glycosidic linkages to form ________.
What are the 5 examples of polysaccharides?
- Glycosaminoglycans (GAGs)
What are some examples of GAGs
- Chondriotin Sulfate
- Keratan Sulfate
- Dermatan Sulfate
- Haparan Sulfate
- Hyaloronic Acid
What is Chondroitin Sulfate involved with?
Bone, Cartilage, cornea formation
What is Keratan Sulfate involved with?
Cornea, connective tissue
What is Dermatan Sulfate involved with?
Binds LDL to plasma walls
What is Heparan Sulfate involved with?
Aortic wall, basement membrane
What is Heparin involved with?
What is Hyaluronic Acid involved with?
Cell migration, lubricant
What enzyme defect is associated with Pompe’s?
The enzyme defect iduronate sulfatase is associated with what syndrome?
What defect is associated with Hurler’s and Schele A?
The enzyme defect Beta-Glucoronidase is associated wit hwaht syndrome?
T/F: I-cell Disease only has one enzyme defect