FINAL blueprint Flashcards

1
Q

what do 1-6 month old infants need for adequate nutrition?

A
  • breastfeeding
  • Vitamin D (200 IU / day)
  • iron-fortified formula (do not microwave)
  • formula 6x daily
  • iron fortified cereal (4-6 months old)
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
2
Q

what do 6-12 month old infants need for adequate nutrition?

A
  • formula / breastmilk 4-5 times a day
  • spoon feeding by pushing food to back of tongue
  • introducing solid foods one at a time
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
3
Q

when do babies get to eat finger food?

teething crackers, fruit and vegetables

A

6-7 months

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
4
Q

when can babies eat chopped table foods?

A

9-12 months

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
5
Q

what are the two oral social stages among infants?

A
  • food intake (3 -4 months)
  • grasping and bring to mouth / biting
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
6
Q

how many times do parents feed the same food to children before determining allergic reaction?

A

3 times one at a time

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
7
Q

what are the stages of play?

A
  1. unoccupied
  2. solitary
  3. onlooker
  4. parallel
  5. associative
  6. social
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
8
Q

unoccupied play

A

random movements of infants w/ no clear purpose

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
9
Q

solitary play

A
  • children start to play on their own
  • takes no notice of other children
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
10
Q

onlooker play

A
  • children just watch others play
  • they ask questions only
  • no intention to join
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
11
Q

parallel play

A
  • children play side-by-side
  • they pay attention to what each is playing
  • no interactions
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
12
Q

associative play

A
  • children interact w/ each other by asking questions)
  • similar goals
  • no established rules
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
13
Q

social play

A
  • children begin to share w/ each other
  • rules are established
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
14
Q

what are the functions of play for a hospitalized child?

A
  • provides diversion for a child
  • gives the child choices and control of the situation
  • gives the parents / family a break
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
15
Q

what are the atraumatic measures in a plan of care for pediatric patients?

(7)

A
  • use a treatment room
  • avoid safe spaces for procedures
  • allow for breastfeeding when possible
  • use appropriate terminology
  • offer choices to the child
  • allow parents to stay with their children during the procedure
  • incorporate play into explaining procedures–allow the child to use dolls or toys
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
16
Q

what is NIPS (neonatal infant pain scale)?

A

a behavioral scale that indicates pain in full-term and pre-term infants (up to 2mos. old)

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
17
Q

components of NIPS

A
  1. cry
  2. facial expression
  3. arms
  4. legs
  5. breathing pattern
  6. state of arousal

each are ranked from 0-1 (cry ranked with 0-2)

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
18
Q

NIPS interventions

A

*reassessment in 30 mins appropriate

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
19
Q

which age group is FLACC used for?

A

2mos. – 7 years old

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
20
Q

definition of FLACC

A

Facial expression
Leg positioning
Activity
Crying
Consolability

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
21
Q

FLACC pain scale

A
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
22
Q

FACES pain scale is used for which age group?

A

3 years and older

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
23
Q

what does the Hib vaccine prevent?

(4); Haemophilus Influenza Type B

A
  • bacterial meningitis
  • epiglottitis
  • bacterial pneumonia
  • sepsis
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
24
Q

what are the common infectious respiratory illness among children?

(4)

A
  • acute LTB
  • epiglottitis
  • pneumonia
  • bronchiolitis
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
25
why is diminished or cessation of breathing noise and effort alarming for nurses?
sign of impending respiratory failure
26
why is *epiglottitis* considered an emergency?
airway obstruction & tracheal occlusion
27
what is *epiglottitis* usually caused by?
Haemophilius influenza | Hib vaccine needed
28
s/s of *epiglottitis* | (7)
* dysphonia * dysphagia * drooling * tripoding * high fever * pain with swallowing * edematous epiglottis
29
what are the diagnostic procedures for *epiglottitis*?
* portable lateral neck x-ray * CBC * blood culture *(bacteremia)*
30
what are the medications for *epiglottitis*?
* ABX * corticosteroids * antipyretics
31
parents are worried their child is having *epiglottitis* for the second time, what does the nurse say?
recurring *epiglottitis* is common
32
what are the signs of water depletion *(dehydration)* in children?
* **weight loss** * **tachycardia** * **depressed fontanels** * decreased UOP * altered LOC * dry skin * tacky mucous membranes
33
lab results for water depletion
* high urine specific gravity * increased BUN * increased Hct * increased Na+ * increased serum osmolarity * variable serum electrolytes
34
what are the causes of water excess?
* water intoxication * IV overload * incorrect feeding *(parents use too much water for formula reconstitution)* * swimming lessons * too rapid dialysis * tap water enemas
35
what are the signs & symptoms of water excess?
* **crackles** * increased venous pressure * slow & bounding pulse * **weight gain** * lethargy * increased spinal pressure * seizures * **bulging fontanels**
36
lab results for water excess
* low urine specific gravity * decreased Hct * decreased serum electrolyes
37
lab results for water excess
* low urine specific gravity * decreased Hct * decreased serum electrolyes
38
conditions associated with water excess
* CHF * SIADH * increased ICP * oliguric renal failure
39
what are the signs of *increased* **ICP**? | (7)
* bulging fontanels * sunset eyes * Cri du chat * irritability * **bradycardia** * **vomiting** * respiratory changes
40
what are the ***early signs*** of increased **ICP**?
* HA * diplopia *(blurred vision)* * NV * confusion
41
what are the *nursing actions* to reduce **ICP**?
* HOB elevated 30 * avoid straining or coughing * avoid bright lights * minimize stimuli
42
what are the side effects of *Digoxin*?
* diuresis * increased PR interval * bradycardia * **nystagmus** * **NV** * **hyperkalemia**
43
what are the pharmacological actions of *Digoxin* that cause bradycardia?
* negative chronotropic * positive inotropic
44
what are the nursing actions for *Digoxin* before administering it to a patient with *CHF*?
***small children:*** hold when HR < 90 & do not give more than 1mL ***older children:*** hold when HR < 70
45
what is the therapeutic range for *Digoxin*?
0.8 - 2mcg/ L
46
why does the nurse need to question an order for *Digoxin* when a child's Potassium levels show less than 3.5mEq?
the effects of the medication will increase
47
*decreased pulmonary blood flow* causes ***cyanosis***
true
48
what are the cardiac defects that lead to a ***decrease*** in pulmonary blood flow?
* Tricuspid atresia * Tetralogy of Fallot
49
***Kawasaki disease*** is the leading cause of *acquired* heart disease in children
true
50
***ecstasia*** is one of the major complications of *Kawasaki disease*, what is it?
an aneurysm caused by overdilation of coronary artery
51
s/s of *Kawasaki disease* | (6)
* red eyes * fever * ring around the iris * **strawberry tongue** * **nonblistering rash on the perineum** * **joint pain**
52
what are the medications for *Kawasaki disease*?
* IV globulins * aspirin
53
what is *Kawasaki diease*?
acute systemic vasculitis that follow viral infections & toxic exposures
54
how are *Tet spells* relieved?
squatting position *(bringing knees to chest)*
55
which medication is used to keep *PDA*?
IV prostaglandin E
56
what are the s/s of *hypoxemia* r/t heart defects?
* cyanosis * **polycythemia** * clubbing * **squatting** * hypercyanotic episodes
57
what are the characteristics of asthma?
* **chronic** inflammatory disorder * **narrow airways** * hypersenstivity to stimuli/ irritants
58
what happens to the lungs among children with *asthma*?
* bronchial constriction * alveolar hyperinflation * air-trapping *(unable to exhale properly)* * edema * increased mucus secretion
59
what are the diagnostic tests for *asthma*?
* CXR * PFT * PEFR
60
what are the s/s for *asthma*?
* expiratory wheezing, crackles, or diminished * dry cough * sitting **retractions** * prolonged expiration * restlessness * fatigue * tachypnea * cyanosis * barrel chest
61
why do nurses need to avoid giving cold liquids to a pt w/ *asthma*?
avoid bronchospasms
62
what is the nursing care for a child w/ *asthma*?
* administer humidified O2 * high fowler's * monitor pulse ox * maintain IV access *(hydration, IV steroids)*
63
what are the medications for *asthma*?
* steroids * oxygen * IV fluids * bronchodilators *(beta agonists & anticholinergics)*
64
what is more important for patient and families to know about regulating *asthma*?
* check peak flow * keep rescue inhaler
65
LTB is usually preceded by an upper respiratory infection | RSV most common
true
66
what is the primary cause of *bronchiolitis*?
RSV
67
*RSV* is most prevalent during the first 2 years of life
true
68
what is *cystic fibrosis*?
increased production of thick mucus in bronchioles and small intestines, & pancreatic and bile ducts
69
what is the etiology of *CF*?
inherited autosomal *recessive trait* from both parents
70
what is the role of **pancreatic enzymes** in the body?
they catabolize fats, carbohydrates & protein
71
what is the pathophysiology of *CF*?
* increased viscosity of secretions * atelectasis * clogged pancreatic ducts *(–> absent enzymes)*
72
what are the diagnostic tests for *CF*? | (6)
* sweat chloride test * CXR * prenatal DNA testing *(from amniotic fluid)* * AXR *(meconium ileus)* * PFT * stool analysis *(72 hours fecal fat)*
73
how does a child with *CF* present?
* coughing * **dyspnea** * **crackles** * cyanosis * clubbing * **steatorrhea** *(frothy, foul smelling)* * low SpO2
74
how can a nurse care for a child with *CF*?
* provide high calories & high protein * administer pancreatic enzymes *(w/ meals)* * administer vitamins A, E, D, K *(fat soluble)* * increase hydration
75
what are the medications for *CF*?
* **mucolytics** * bronchodilators * ABX * **pancreatic enzymes** * **fat-soluble vitamins**
76
proper education for families with a child with *CF*
* avoid respiratory illness & infection * **chest percussion** * postural drainage * **high calorie & high protein** * physical activity *(loosens secretions)* * genetic counseling
77
what is the major cause of hospitalizations among infants?
bronchiolitis
78
what is *bronchiolitis*?
inflammation of bronchioles with edema & excess accumulation of mucus due to RSV
79
why does air trapping & atelectasis occur in *bronchiolitis*?
increased airway resistance from obstructed bronchioles
80
how is *bronchiolitis* spread?
contact with contaminated objects*(droplet precautions must be in place)*
81
what are the diagnostic procedures for *bronchiolitis*?
* nasopharyngeal swab * CXR
82
what are the symptoms of *bronchiolitis*?
* worsening upper respiratory infections * tachypnea * retractions * low-grade **fever** * anorexia * thick nasal secretions * wheezing / crackles
83
how can a nurse care for a child with *bronchiolitis*?
* **encourage feeding** * nasal suctioning PRN * **increase fluid intake** * daily weights *(I&O)* * pulse ox * humidified O2 * **contact precautions**
84
medications for bronchiolitis
* ABX * fluids * steroids
85
what is most important for families to know in caring for their child with *bronchiolitis*?
* use of **bulb syringe** * notify HCP when anorexic or **worsened breathing**
86
what are the ages of a *preschooler*?
3-6 years old
87
what are the *gross motor skills* typically learned during the **preschool** years?
* rides tricycle * up stairs alternating feet * hop on one foot & alternate feet * dress independently * throws & catches a ball
88
what are *fine motor skills* preschoolers learn?
* **lace shoes up** * **use of scissors & pencils** * can **draw** cross, circle, diamond, & triangle * count numbers * write a few letters
89
what type of play are preschoolers engaged in?
associative play
90
imaginary friends are common among *preschoolers*
true
91
*preschoolers* are more socially aware with knowledge & less egocentric
true
92
which phase of Piaget are *preschoolers* in?
preoperational phase | Stage 2
93
what is a hallmark of preschooler's cognitive development?
language *(being able to express themselves sufficiently)*
94
*preschoolers* cannot reason beyond the observable
true | literal language, not figurative
95
*preschoolers* have a lack of reversibility
true
96
which stage of *Erikson's* are preschoolers in?
initiative vs. guilt | Stage 3 ## Footnote exercise autonomy, feeling guilty for unfulfilling tasks
97
what does the nurse tell a preschooler's parent who is worried about their child's stuttering and stammering
it is a normal characteristic of language development
98
treatment for ***hypertensive*** *AKI*
* anti-HTN * limit fluids * limit salt
99
manifestations of *Wilms tumor*
* aniridia * HTN * hematuria * hemihypertrophy * overgrowth syndrome *(Beckwith-Wiedemann)*
100
diagnostic procedures for *Wilms tumor*
* radiographic studies *(x-ray)* * ABD U/S * hematologic & biochem studies * UA
101
why should nurses not palpate the protrusion in *Wilms tumor*?
to avoid rupturing the tumor
102
what is the treatment for *Wilms tumor*?
surgical removal of tumor, affected kidney, & adjacent adrenal gland
103
what is the triad for *HUS*?
* anemia * thrombocytopenia * renal failure
104
what are the *lab results* associated with **HUS**?
* decreased Hgb & Hct * elevated BUN * elevated Creatinine * elevated reticulocyte
105
what is the *nursing care* for **HUS**? | (5)
* **monitor I&O** * **fluid replacement** * treat HTN * provide **seizure precautions** * enteral nutrition
106
what is included in **renal diet**?
* low Na+ * high carbs * low protein * fluid restrictions * avoid fresh & organic produce
107
what are the implications for *AKI*? | accumulation of waste
* azotemia * uremia * inability to excrete waste, concentrate urine, & conserve electrolytes
108
diagnostic results for *AKI*
* elevated BUN * reduced GFR * elevated creatinine
109
treatment for ***hyperkalemic*** *AKI*
Kayexalate
110
treatment for ***hypertensive*** *AKI*
* anti-HTN * limit fluids * limit salt
111
treatment for ***anemic*** *AKI*
PRBC | if Hgb is < 6g/dL
112
# emesis pyloric stenosis
projectile vomiting
113
# definition pyloric stenosis
hypertrophy of circular muscle of pylorus | causes obstruction & constriction
114
therapeutic procedures for *pyloric stenosis*
* pylorotomy * laparotomy
115
hallmark signs of *pyloric stenosis*
* **moveable mass** in epigastrum * **projectile vomiting** * possible peristaltic wave while supine * dehydration
116
# characteristic celiac disease
intolerance to the protein gluten
117
what is the pathology for *Celiac disease*?
gluten-sensitive enteropathy
118
what are the common manifestations of *Celiac disease*?
* ABD distension * vomiting * diarrhea w/ foul odor * chronic malabsorption syndrome
119
cleft lip/ palate feeding bottles
120
when can *cleft palate* be repaired?
between 6-12 months of age | usually before 2 years old
121
postop nursing care for *cleft palate* repair
* elevated supine position (or on side) * cool mist tent * blended diet * elbow restraints * advice to avoid sucking for 7-10 days * no oral temps
122
for how long do children who had their cleft palate repaired stay in elbow restraints?
4-6 weeks
123
when do posterior fontanels close?
2-3 months old
124
when do deciduous teeth erupt?
6-10 months old
125
what is the recommended dose for Acetaminophen for infants?
10-15mg / kg / dose (max. 5 doses)
126
what do babies need for healthy & safe sleep?
* sleeping in their own bed close to parent's bed * no soft bedding * no smoking * no overheating * supine position
127
s/s of *GERD*
* excessive crying * arching of back * spitting up/ vomiting * cough, wheezing, stridor, gag * apnea * bloody emesis * difficulty swallowing * CP * heart burn
128
managements for *GERD*
* weight control * small frequent meals * avoid food that intensify reflux * thickened feedings * elevate HOB (or hold baby for ***one hour***)
129
what are the medications for *GERD*?
* Ranitidine * Omeprazole
130
hallmark sign of *appendicitis*
pain at McBurney's point (RLQ)
131
what are the diagnostic tests that can confirm *appendicitis*?
* CBC*(WBC)* * CT scan * CRP*(detects inflammation)*
132
what would a CT scan show for *appendicitis*?
enlarged appendix & thickening of appendiceal wall
133
what is ***osteogenesis imperfecta***?
an inherited **connective tissue disorder** that results in bone fractures along w/ restricted growth | "brittle bone disease"
134
what are the clinical manifestations of ***osteogenesis imperfecta***?
* multiple bone fractures * blue sclera * early hearing loss * hypoplastic discolored teeth
135
what is the treatment for ***osteogenesis imperfecta***?
pamidronate IV with biphosphate
136
what is the expected MOA of ***pamidronate***?
increases bone density
137
what are the signs of ***compartment syndrome*** that occurs with *casts*? | 5 P's
* paresthesia * pallor * paralysis * pain * pulselessness
138
what are the nursing priorities for a child with a *cast*?
regular *skin checks* & *neurovascular checks*
139
what are ***tractions*** used for? | (4)
* provide muscle rest * immobilization * alignment * prevent contractures
140
what are the *nursing actions* for **cast care** & **traction**? | (7)
* **use a doll** or toy for *atraumatic care* * **elevate cast** above heart level to prevent swelling * **reposition** q2hrs to *allow air drying* * keep extremity supported *(dependent position)* * monitor for drainage * notify for hot spots * ensure weights **hang freely** *(do not lift w/o HCP supervision)*
141
what are the components of ***neurovascular assessments***?
* sensation * skin temperature * **skin color** * **cap refill** * **pulses** * movement
142
what are the types of ***skin tractions***?
* Bryant * Buck * Russell
143
what is the most prominent etiology of ***cerebral palsy***?
kernicterus | elevated bilirubin in newborns
144
what is ***cerebral palsy***?
a nonprogressive **impairment of motor function** that causes *spasticity* or *dyskinesia* (involuntary movements)
145
what are the s/s of ***cerebral palsy***? | (8)
* persistent *Moro reflex* or *tonic neck reflex* * failure to smile by 3 months * persistent **tongue thrust** by 6 months * spasticity * **scissoring of legs** * nystagmus * hearing loss * feeding difficulties
146
what are the expected findings of *spina bifida* ***cystica***? | (5)
* **flaccid muscles** * lack of bowel control * rectal prolapse * spinal curvature abnormalities *(kyphosis/ scoliosis)* * **protruding sac**
147
what are the nursing actions after treating *hypoglycemia* w/ 15g carbs & glucagon?
* recheck glucose 15mins after until levels are 70mg/dL or above * continue to monitor for 2hrs
148
what is the *HgbA1c* level for ***hyperglycemia***?
< 6.5%
149
what is the *fasting BG* level for ***hyperglycemia***?
126mg/dL or above
150
what is the ***starvation response*** in *T1DM*?
fatty acid is broken down *(to obtain more energy from the body)* and in the process produced *ketone bodies*
151
*starvation response* over a prolonged period of time can lead to which complication?
diabetic ketoacidosis
152
what are the s/s of *DKA*?
* ***Kussmaul respirations*** * fruity breath
153
what are the s/s of *T1DM*? | (7)
* polyuria * polyphagia * polydipsia * flushed/ dry skin * confusion * wt loss * retinopathy
154
what is the most concerning delay in developmental milestone found in an infant?
head lagging
155
what does **head lagging** indicate?
cerebral palsy
156
what are the supplements that pregnant women should take to *prevent* **NTDs**?
* niacin * folate
157
what is the first sign of **puberty** in *girls*?
breast development
158
# definition animism
personification of inanimate objects
159
what are the nursing actions for a child with a **myelomeningocele** preop?
lay on their side with the sac covered with a sterile saline gauze
160
**Bryant's traction** is only appropriate for children with *hip dysplasia* that meet which criteria?
* younger than 3 yrs old * weighing less than 35 lbs.
161
what is the first sign of **puberty** in *boys*?
testicular enlargement
162
what is ***hemophilia***?
a group of bleeding disorders characterized by difficulty controlling bleeding due to *lack of clotting factors*
163
what are the types of ***hemophilia***?
* Hemophilia A *(classic)* * Hemophilia B * Von Willebrand Disease
164
which clotting factor does ***Hemophilia A*** lack?
factor VIII
165
which clotting factor does ***Hemophilia B*** lack?
factor IX
166
which is the most common type of ***hemophilia***?
Von Willbrand disease
167
what is ***Von Willebrand*** *hemophilia*?
the inherited **lack of the *von willebrand factor* protein** characterized by inability of platelets to aggregate
168
both ***Hemophilia A*** & ***B*** are male dominant *(x-linked recessive)*
true
169
***Von Willebrand disease*** affects both males & females
true
170
how is ***hemophilia*** diagnosed?
* hx of **bleeding episodes** * evidence of x-linked inheritance * **PTT** * factor assays * DNA testing
171
what are the medications & treatment for ***hemophilia***? | (5)
* synthetic vasopressin *(DDAVP)* * steroids * factor VIII products * pooled plasma * recombinant products
172
what is the MOA of ***DDAVP*** *(Desmopressin)* for Hemophilia?
increases plasma factor VIII *(only for **Hemophilia A**)*
173
what is the nursing care for ***hemophilia***? | (4)
* monitor urine, stool, & NG fluid for ***occult blood*** * administer ***Acetaminophen*** instead of *aspirin* * administer injections via subQ only * venipunctures are preferred for blood sampling
174
where is the most appropriate site for a **bone marrow biopsy** on a child *younger than 18 months*?
tibia
175
where is the most appropriate site for a **bone marrow biopsy** on a child *older than 18 months*?
anterior iliac crest
176
what are the *nursing actions* for a **bone marrow biopsy**?
* apply pressure dressing for 24hrs * have the patient in side-lying position * place a pillow under their hips
177
patients with ***sickle cell anemia*** have what type of *Hgb*?
Hgb S | predominantly; it replaces Hgb A
178
which diagnostic procedure is used for ***sickle cell anemia***?
* hemoglobin electrophoresis * sickledex finger stick
179
what are the nursing actions for a ***sickle cell*** *crisis*?
* adequate oxygenation * hydration * transfusion * ABX * analgesics * FEB
180
what are the s/s of *vasooculsive crisis* in ***sickle cell anemia***? | (6)
* pain * priapism * acute chest syndrome * stroke * severe joint pain * swollen joints & extremities
181
what are the *nursing actions* for **sickle cell anemia**? | (8)
* analgesics * O2 * promote rest * give oral fluids * monitor for infection * administer *PCV, Hib, Meningococcal* vaccines * apply **warm packs** to joints * administer **Hydroxyurea**
182
what is the prevention for *sepsis* in ***sickle cell anemia***?
prophylactic Penicillin | until 5 years old
183
how does **hydroxyurea** help manage *sickle cell anemia*?
reverts sickle cells to its original shape *(promoting roundness & flexibility)* | reverse sickle cell effects
184
what is the nursing care for a patient experiencing **sickle cell crisis** *(vasooclusive)*?
* administer analgesics *(acetaminophen, ibuprofen, or opioids)* * apply warm compress to joints * O2 * bed rest * increase fluids
185
which foods contain *gluten*?
* barley * rye * oats * wheat | BROW
186
what are the symptoms for *pertussis*?
* runny nose * severe cough *(whooping upon inspiration)* * spasms * flushing * cyanosis * vomiting
187
what are the precautions implemented for **pertussis**?
droplet precautions
188
what is the nursing care for ***hemophilia***? | (4)
* monitor urine, stool, & NG fluid for **occult blood** * administer ***Acetaminophen*** instead of *aspirin* * administer injections via subQ only * **venipunctures** are preferred for blood sampling
189
what is the MOA of ***DDAVP*** *(Desmopressin)*?
increases plasma factor VIII *(only for **Hemophilia A**)*
190
how is ***hemophilia*** diagnosed?
* hx of bleeding episodes * evidence of x-linked inheritance * PTT * factor assays * DNA testing
191
what are the medications & treatment for ***hemophilia***? | (5)
* synthetic **vasopressin** *(DDAVP)* * steroids * **factor VIII** products * pooled plasma * recombinant products
192
what is *Rheumatic fever*?
an inflammatory disease that occurs as a reaction to *Group A strep infection*
193
s/s of *Rheumatic fever* | (7)
* ***Aschoff bodies*** *(tiny lesions of the heart)* * carditis * murmur * ***polyarhritis*** * ***rash in trunk & extremities*** * subcutaneous nodules * CNS involvement *(uncoordination + involuntary mvmnts)*
194
what are the medications that can treat *Rheumatic fever*?
* penicillin G * sulfadiazine*(ABX)* * penicillin V
195
what is the earliest sign of dehydration?
* tachycardia * poor perfusion *(cap refill)*
196
what are the s/s of **hypoglycemia**?
* irritability * decreased LOC * slurred speech * cold & clammy * pallor * hunger
197
what are the s/s **hyperglycemia**?
* polyuria * polydipsia * polyphagia * NV * **fruity breath**
198
what is the first intervention for dehydation in pediatrics?
oral rehydration therapy with Pedialyte or Gatorade ONLY
199
what are the s/s of **Graves disease**? | (6)
* hyperactive * hyperstimulated * exophthalmos * tachycardia * diaphoretic * weight loss
200
what are the signs of ***compartment syndrome*** that occurs with *casts*? | 5 P's
* paresthesia * pallor * paralysis * pain * pulselessness
201
what is the pathophysiology of *nephrotic syndrome*?
increasing permeability of basement membrane in kidneys leading to albumin leaks & accumulation of fluid in interstitial spaces
202
what is the etiology of *nephrotic syndrome*?
inherited autosomal recessive gene
203
what are the manifestations of *nephrotic syndrome*? | (7)
* weight gain * **periorbital** edema * **ascites** * oliguria * vomiting * irritability * proteinuria *(**15g** in 24-hr urine)*
204
children with **nephrotic syndrome** have an increased risk of *upper respiratory infection*
true
205
what is the *nursing care* for **nephrotic syndrome**? | (5)
* elevate legs to relieve edema * strict I&O * measure ABD girth daily * monitor for proteinuria * salt restriction
206
what is the treatment for *nephrotic syndrome*?
* low Na+ diet * severe fluid restriction * **diuretics** *(due to edema)* * **25% albumin** * **prednisone**
207
what is the goal for treating *nephrotic syndrome*?
* **reduce** excretion of **urinary protein** * reduce **fluid retention** in tissues * **prevent infection**
208
what is ***osteogenesis imperfecta***?
an inherited **connective tissue disorder** that results in bone fractures along w/ restricted growth | "brittle bone disease"
209
what are the clinical manifestations of ***osteogenesis imperfecta***?
* multiple bone fractures * blue sclera * early hearing loss * hypoplastic discolored teeth
210
what is the treatment for ***osteogenesis imperfecta***?
pamidronate IV with biphosphate
211
what is the expected MOA of ***pamidronate***?
increases bone density
212
what are the types of ***fracture*** in children?
* bend * buckle * greenstick * complete
213
***bend fratcures*** only occur in the *ulna* & *fibula* when there is a fracture in the radius & tibia
true
214
the most common site for a fracture in a child is the ***growth plates***, where is it?
located on the ends of the hard bone *(epiphyseal)*
215
what are the styles of parenting?
* authoritarian * permissive * authoritative
216
what are the types of families? | (7)
* traditional * nuclear * blended * extended * single parent * binuclear * communal
217
# fluid calculations 1-10 kg
100mL/kg
218
# fluid calculations 11-20 kg
(1000mL) + (50mL / kg > 10)
219
# fluid calculations > 20kg
(1500mL) + (20mL/ kg > 20)
220
what kind of reflexes does a child with *meningitis* manifest?
* Brudzinsky sign * Kernig's sign * Nuchal rigidity
221
which vaccine prevents *meningitis*?
Hib vaccine
222
which bacteria causes *meningitis*?
* group B strep * Hib
223
what are the s/s of *meningitis*? | (7)
* abrupt onset fever * vomiting * photophobia * HA * **Nuchal rigidity** * **Kernig's sign** * **Brudzinski's sign**
224
what is the diagnostic procedure for *meningitis*?
lumbar puncture
225
what are the CSF characteristics for ***bacterial*** *meningitis*?
* elevated WBC * cloudy color * elevated protein * decreased glucose * ***(+) Gram stain***
226
what are the CSF characteristics for ***viral*** *meningitis*?
* **clear** color * **elevated WBC** * normal protein content * normal glucose * ***(-) Gram stain***
227
what is *Reye syndrome*?
a neurological dysfunction that causes **liver dysfunction & cerebral edema**
228
which medication is the cause for *Reye syndrome* heavily associated with?
Aspirin
229
***Reye syndrome*** typically follows a viral illness such as *flu or varicella*
true
230
what are the emergent measures for *status epilepticus*? | (5)
* airway * oxygen * suction * IV **ativan** * thermoregulation
231
what are the nursing actions *prior* to a **lumbar puncture**?
* assist client to void * apply EMLA cream
232
what are the nursing actions *after* a **lumbar puncture**?
* apply pressure dressing to site * monitor for **bleeding, hematoma, infection** * allow patient to lay flat
233
how is the child positioned for a **lumbar puncture**?
side lying w/ head & knees flexed
234
what is the ***starvation response*** in *T1DM*?
fatty acid is broken down *(to obtain more energy from the body)* and in the process produced *ketone bodies*
235
what are the s/s of *hyperthyroidism*?
* irritability * hyperactivity * ***exophthalmos*** * goiter * wt loss
236
what is *Grave's disease*?
a form of ***hyperthyroidism*** that is usually an autoimmune response to TSH receptors
237
*hyperthyroidism* is more common in girls *(at least 5x more likely)*
true
238
what are the s/s of ***Grave's disease***?
* **fever** * **enlarged thyroid gland** * exophthalmos * urticaria * vasculitis * agranulocytosis
239
children can become *hyperthermic* when in a ***toxic coma***
true
240
what are the *preoperative* actions for a patient who is scheduled for a **meningocele sac closure**?
* place infant in warmer * apply sterile, moist, & non-adhering dressing on the sac *(re-wet when dry)* * administer IV ABX as prescribed * **avoid rectal temperatures**
241
what are the *postperative* actions for a patient who had a **meningocele sac closure**? | (6)
* monitor weight * monitor I&O * resume oral feedings * **provide ROM** * **assess for bulging fontanels** * measure head circumference
242
what are the appropriate *client education* for a patient with a **meningocele**?
* avoid objects with **latex** * monitor for **bladder infection** or dysfunction * monitor widening head circumference
243
which lack of vitamins during gestation can cause **spina bifida**?
* folate * niacin * cobalamine
244
what are the *diagnostic tests* to determine **spina bifida** during gestation?
* AFP * amniocentesis * U/S
245
elevated AFP levels indicate **spina bifida**
true
246
what are the treatments for *seizure*? | (6)
* **Ketogenic diet** * **antiepileptic drugs** * **vagus nerve stimulation** * focal resection * hemispherectomy * corpus callostomy
247
what is included in a **Ketogenic diet**?
* high fat * low carbs * adequate protein
248
what are the emergent measures for *status epilepticus*? | (5)
* airway * oxygen * suction * IV access *(-zepam & phenobarbital)* * thermoregulation
249
what are the types of ***anemias***?
* iron deficiency * sickle cell * B-Thalassemia*(Cooley)* * aplastic
250
what are the various reasons for ***anemia***?
* decreased RBC production * increased loss of RBC *(from bleeding)* * increased hemolysis
251
what are common clinical manifestations of ***anemia***?
* fatigue * pallor * decrease in Hgb
252
what are the clinical manifestations of ***Cooley anemia***? | B-Thalassemia
* small stature * splenomegaly * hepatomegaly * decreased H&H * abnormal blood smear
253
what is ***aplastic anemia***?
a bone marrow failure condition in which formed elements of the blood are simultaneously depressed
254
what are the conditions associated with ***aplastic anemia***?
* anemia * leukopenia * thrombocytopenia
255
what are the manifestations of *coarctation of the aorta*? | (5)
* elevated BP in upper extermities *(> 20mmHg difference)* * bounding pulses in upper extremities * cool skin in lower extremities * nosebleeds *(epistaxis)* * absent femoral pulses
256
what is the hallmark heart sound the nurse will hear in *aortic stenosis*?
bruit
257
what are the congenital ***mixed defects*** that can be found in children?
* transposition of the great vessels * total anomalous pulmonary venous return * truncus arteriosus * hypoplastic left heart syndrome
258
what are the *congenital heart defects* that ***increase*** pulmonary blood flow?
* atrial septal defect * ventricular septal defect * patent ductus arteriosus * atrioventricular canal
259
what are the ***obstructive defects*** of the heart?
* coarctation of the aorta * aortic stenosis * pulmonary stenosis
260
auscultory landmarks of the heart
| *be mindful of* **STERNAL BORDERS** & **MIDCLAVICULAR**
261
what are the conditions that are included under *Tetralogy of Fallot*? | (4)
* pulmonary stenosis * overriding aorta * right ventricular hypertrophy * VSD
262
s/s of *ToF* | (5)
* ***cyanotic spells*** *(Tet spells)* * ***polycythemia*** * systolic murmur * clubbing * tachypnea
263
what is the treatment for **ToF**?
* O2 * Morphine *(induce slower RR)* * squatting *(knees to chest)*
264
what is the nursing action when a child has > 60mg/kg of **iron**?
administer **Deferoxamine**